CUI1
stringlengths
8
8
RELA
stringlengths
3
54
CUI2
stringlengths
8
8
Name1
stringlengths
1
2.86k
Name2
stringlengths
1
2.86k
Def1
stringlengths
1
8.95k
Def2
stringlengths
1
8.95k
C0000768
has_associated_morphology
C0344665
Congenital Abnormality
Inferior vena cava interruption with left sided hemiazygos continuation
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344666
Congenital Abnormality
Inferior vena cava interruption with right sided azygos continuation
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344667
Congenital Abnormality
Inferior vena cava interruption with bilateral azygos continuation
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344668
Congenital Abnormality
Abnormal inferior vena caval connection
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344669
Congenital Abnormality
Inferior vena cava connecting to morphological left atrium
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344670
Congenital Abnormality
Inferior vena cava connecting to coronary sinus
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344671
Congenital Abnormality
Inferior vena cava to left of spine
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344672
Congenital Abnormality
Inferior cava to left of spine with right descending aorta
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344674
Congenital Abnormality
Anomalous portal vein termination
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344675
Congenital Abnormality
Anomalous termination of right pulmonary vein
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344678
Congenital Abnormality
Obstructed pulmonary venous connection
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344679
Congenital Abnormality
Pulmonary vein atresia
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344680
Congenital Abnormality
Coronary sinus abnormality
Malformations of organs or body parts during development in utero.
An abnormality of the coronary sinus, which is formed by the union of the great cardiac vein and the left marginal vein and terminates in the right atrium. The coronary sinus functions to o collect deoxygenated blood from the myocardium of the heart and drain it into the right atrium. [HPO_CONTRIBUTOR:DDD_dbrown, https...
C0000768
has_associated_morphology
C0344681
Congenital Abnormality
Coronary sinus defect in left atrium
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344683
Congenital Abnormality
Coronary sinus orifice atresia
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344684
Congenital Abnormality
Congenital coronary sinus stenosis
Malformations of organs or body parts during development in utero.
A rare congenital anomaly of the coronary sinus characterized by its stenosis at the ostium, lumen, or origin, typically leading to dilation of the vessel. Symptoms are variable and can include palpitations, tachypnea, dyspnea, chest pain, fatigue, and cyanosis. The malformation may be associated with other cardiac ano...
C0000768
has_associated_morphology
C0344685
Congenital Abnormality
Coronary sinus to left ventricle fistula
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344686
Congenital Abnormality
Congenital enlargement of coronary sinus
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344687
Congenital Abnormality
Ductus venosus abnormality
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344688
Congenital Abnormality
Patent Ductus Venosus
Malformations of organs or body parts during development in utero.
A congenital defect of the vasculature such that there is a shunt (by-pass) of blood directly from the portal vein to the vena cava (i.e., the blood from the portal vein is not filtered through the liver). [https://orcid.org/0000-0002-0736-9199]
C0000768
has_associated_morphology
C0344689
Congenital Abnormality
Closed ductus venosus
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344690
Congenital Abnormality
Abnormal connection of hepatic vein to atrium
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344691
Congenital Abnormality
Congenital abnormality of atria and atrial septum
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344692
Congenital Abnormality
Isomerism of atrial appendages
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344694
Congenital Abnormality
Isomerism of left atrial appendage
Malformations of organs or body parts during development in utero.
A rare cardiac malformation characterized by both atrial appendages having the morphology of the left atrial appendage. It is associated with other anomalies of the heart, systemic and pulmonary veins, and other organ systems, including the gastrointestinal, respiratory, and genitourinary tract, as well as the spleen a...
C0000768
has_associated_morphology
C0344695
Congenital Abnormality
Mirror imaged atria
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344696
Congenital Abnormality
Right atrial abnormality
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344697
Congenital Abnormality
Divided right atrium
Malformations of organs or body parts during development in utero.
A rare, congenital, non-syndromic, heart malformation characterized by the persistence of the embryonic right valve of the sinus venosus which results in a subdivision of right atrium into two chambers. Clinical manifestations depend on the degree of right atrial septation and the size of sinoatrial orifice and vary fr...
C0000768
has_associated_morphology
C0344698
Congenital Abnormality
Prominent valve of inferior vena cava
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344699
Congenital Abnormality
Obstructive Eustachian valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344700
Congenital Abnormality
Prolapse of Eustachian valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344701
Congenital Abnormality
Anomalous valve of coronary sinus
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344703
Congenital Abnormality
Abnormality of right atrial appendage
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344704
Congenital Abnormality
Right atrial appendage absent
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344705
Congenital Abnormality
Right atrial appendage - left - juxtaposition
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344706
Congenital Abnormality
Right atrial appendage aneurysm
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344707
Congenital Abnormality
Endocardial fibroelastosis of right atrium
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344708
Congenital Abnormality
Right atrial hypoplasia
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344710
Congenital Abnormality
Giant right atrium
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344711
Congenital Abnormality
Left atrial abnormality
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344712
Congenital Abnormality
Divided left atrium
Malformations of organs or body parts during development in utero.
A rare, congenital, non-syndromic, heart malformation characterized by the presence of a thin, fibromuscular membrane subdividing the left atrium into an upper and lower chamber. The upper chamber receives blood from the pulmonary veins and the lower chamber is attached to the left atrial appendage. Therefore, the memb...
C0000768
has_associated_morphology
C0344713
Congenital Abnormality
Supramitral left atrial ring
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344714
Congenital Abnormality
Abnormality of left atrial appendage
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344715
Congenital Abnormality
Left atrial appendage absent
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344716
Congenital Abnormality
Left atrial appendage - right - juxtaposition
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344717
Congenital Abnormality
Left atrial appendage aneurysm
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344718
Congenital Abnormality
Endocardial fibroelastosis of left atrium
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344719
Congenital Abnormality
Left atrial hypoplasia
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344720
Congenital Abnormality
Left atrial dilatation
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344721
Congenital Abnormality
Giant left atrium
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344722
Congenital Abnormality
Abnormality of atrial septum
Malformations of organs or body parts during development in utero.
An abnormality of the interatrial septum. [https://orcid.org/0000-0002-0736-9199]
C0000768
has_associated_morphology
C0344723
Congenital Abnormality
Foramen ovale valvar aneurysm
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344733
Congenital Abnormality
Atrial septal defect through coronary sinus orifice
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344735
Congenital Abnormality
Atrioventricular septal defect - isolated atrial component
Malformations of organs or body parts during development in utero.
An ostium primum atrial septal defect is located in the most anterior and inferior aspect of the atrial septum. The ostium primum refers to an anterior and inferior opening (ostium) within the septum primum, which divides the rudimentary atrium during fetal development. The ostium primum is normally sealed by fusion of...
C0000768
has_associated_morphology
C0344736
Congenital Abnormality
Congenital abnormality of atrioventricular valves in atrioventricular septal defect
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344737
Congenital Abnormality
Myxoid transformation of tricuspid valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344738
Congenital Abnormality
Tricuspid leaflet dysplasia
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344739
Congenital Abnormality
Tricuspid annulus hypoplasia
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344740
Congenital Abnormality
Dilatation of tricuspid annulus
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344741
Congenital Abnormality
Congenital tricuspid atresia or stenosis NOS
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344742
Congenital Abnormality
Overriding tricuspid valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344743
Congenital Abnormality
Straddling tricuspid valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344744
Congenital Abnormality
Tricuspid leaflet abnormality
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344745
Congenital Abnormality
Absent tricuspid leaflet
Malformations of organs or body parts during development in utero.
A form of agenesis of the tricuspid valve in which (although the normal orifice between the right atrium and right ventricle exists) there is no tricuspid valvular tissue. [https://orcid.org/0000-0002-0003-6754, PMID:14246338]
C0000768
has_associated_morphology
C0344746
Congenital Abnormality
Double orifice of tricuspid valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344747
Congenital Abnormality
Cleft leaflet of tricuspid valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344748
Congenital Abnormality
Accessory tissue on tricuspid leaflet
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344755
Congenital Abnormality
Parachute malformation of tricuspid valve
Malformations of organs or body parts during development in utero.
Parachute tricuspid valve is a rare congenital heart malformation defined as an insertion of the chordal apparatus into a single papillary muscle or a muscle group, making a pathognomonic 'pear' shape sign in the four-chamber echocardiographic view with the atrium forming the larger base of the pear and the leaflets th...
C0000768
has_associated_morphology
C0344760
Congenital Abnormality
Congenital atresia of mitral valve
Malformations of organs or body parts during development in utero.
A rare congenital non-syndromic heart malformation characterized by an imperforate or absent mitral valve. In most cases, there is a univentricular atrioventricular connection to a dominant right ventricle via a tricuspid valve, and a hypoplastic left ventricle. Morphologic heterogeneity is considerable, and hemodynami...
C0000768
has_associated_morphology
C0344762
Congenital Abnormality
Mitral leaflet dysplasia
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344763
Congenital Abnormality
Congenital hypoplasia of mitral valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344764
Congenital Abnormality
Overriding mitral valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344765
Congenital Abnormality
Congenital dilatation of the mitral annulus
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344767
Congenital Abnormality
Straddling mitral valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344771
Congenital Abnormality
Ebstein-like downward displacement of mitral valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344772
Congenital Abnormality
Cleft leaflet of mitral valve
Malformations of organs or body parts during development in utero.
A rare, congenital, non-syndromic heart malformation characterized by a slit-like hole or defect in one of the mitral valve leaflets, which is usually thickened and distorted. It usually affects the anterior leaflet, but the cleft of posterior leaflet has also been described. Cleft mitral valve can be isolated or assoc...
C0000768
has_associated_morphology
C0344773
Congenital Abnormality
Anterior leaflet of mitral valve attached to septum
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344774
Congenital Abnormality
Accessory tissue on mitral leaflet
Malformations of organs or body parts during development in utero.
A rare congenital non-syndromic heart malformation characterized by an accessory mitral valve leaflet or various accessory mitral valve structures. It may be asymptomatic or present at various ages with symptoms of left ventricular outflow tract obstruction, low cardiac output due to subaortic obstruction or congestive...
C0000768
has_associated_morphology
C0344779
Congenital Abnormality
Mitral papillary muscle abnormality
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344780
Congenital Abnormality
Absent mitral papillary muscle
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344781
Congenital Abnormality
Fused mitral papillary muscles
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344782
Congenital Abnormality
Hypoplastic mitral papillary muscle
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344783
Congenital Abnormality
Atrioventricular septal defect and common atrioventricular junction
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344784
Congenital Abnormality
Other specified endocardial cushion defects
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344786
Congenital Abnormality
Atrioventricular septal defect - isolated ventricular component
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344787
Congenital Abnormality
Atrioventricular septal defect: atrial and ventricular components
Malformations of organs or body parts during development in utero.
A rare, congenital cardiac anomaly characterized by a common atrioventricular junction with a common AV valve, an interatrial communication just above the common AV valve (ostium primum defect), a posterior interventricular communication (inlet VSD), that results in shunting at both the atrial and ventricular level. Mo...
C0000768
has_associated_morphology
C0344788
Congenital Abnormality
Atrioventricular septal defect - ventricular component
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344789
Congenital Abnormality
Atrioventricular septal defect - ventricular component under superior bridging leaflet
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344790
Congenital Abnormality
Atrioventricular septal defect with ventricular component under superior bridging leaflet with chords at crest ventricular septum
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344791
Congenital Abnormality
Atrioventricular septal defect with ventricular component under superior bridging leaflet with chords to papillary muscle on right ventricular side septum
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344792
Congenital Abnormality
Atrioventricular septal defect with ventricular component under free floating superior bridging leaflet and chords to papillary muscle at right ventricular free wall
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344793
Congenital Abnormality
Atrioventricular septal defect - ventricular component under inferior bridging leaflet
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344797
Congenital Abnormality
Abnormality of atrioventricular (non-mitral, non-tricuspid) valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344798
Congenital Abnormality
Abnormality of common atrioventricular valve in atrioventricular septal defect
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344799
Congenital Abnormality
Atresia of common atrioventricular valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344800
Congenital Abnormality
Imperforate common atrioventricular valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344801
Congenital Abnormality
Hypoplasia of common atrioventricular valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344802
Congenital Abnormality
Dysplasia of common atrioventricular valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344803
Congenital Abnormality
Regurgitation of common atrioventricular valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0344804
Congenital Abnormality
Common atrioventricular valve limited to one ventricle
Malformations of organs or body parts during development in utero.
null