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211 values
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206
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of sphingolipid metabolism and other lipid storage disorders
E75
E75.19
Other gangliosidosis
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of sphingolipid metabolism and other lipid storage disorders
E75
E75.2
Other sphingolipidosis
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of sphingolipid metabolism and other lipid storage disorders
E75
E75.21
Fabry (-Anderson) disease
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of sphingolipid metabolism and other lipid storage disorders
E75
E75.22
Gaucher disease
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of sphingolipid metabolism and other lipid storage disorders
E75
E75.23
Krabbe disease
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of sphingolipid metabolism and other lipid storage disorders
E75
E75.24
Niemann-Pick disease
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of sphingolipid metabolism and other lipid storage disorders
E75
E75.240
Niemann-Pick disease type A
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of sphingolipid metabolism and other lipid storage disorders
E75
E75.241
Niemann-Pick disease type B
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of sphingolipid metabolism and other lipid storage disorders
E75
E75.242
Niemann-Pick disease type C
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of sphingolipid metabolism and other lipid storage disorders
E75
E75.243
Niemann-Pick disease type D
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of sphingolipid metabolism and other lipid storage disorders
E75
E75.248
Other Niemann-Pick disease
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of sphingolipid metabolism and other lipid storage disorders
E75
E75.249
Niemann-Pick disease, unspecified
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of sphingolipid metabolism and other lipid storage disorders
E75
E75.25
Metachromatic leukodystrophy
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of sphingolipid metabolism and other lipid storage disorders
E75
E75.26
Sulfatase deficiency
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of sphingolipid metabolism and other lipid storage disorders
E75
E75.29
Other sphingolipidosis
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of sphingolipid metabolism and other lipid storage disorders
E75
E75.3
Sphingolipidosis, unspecified
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of sphingolipid metabolism and other lipid storage disorders
E75
E75.4
Neuronal ceroid lipofuscinosis
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of sphingolipid metabolism and other lipid storage disorders
E75
E75.5
Other lipid storage disorders
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of sphingolipid metabolism and other lipid storage disorders
E75
E75.6
Lipid storage disorder, unspecified
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of glycosaminoglycan metabolism
E76
E76.0
Mucopolysaccharidosis, type I
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of glycosaminoglycan metabolism
E76
E76.01
Hurler's syndrome
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of glycosaminoglycan metabolism
E76
E76.02
Hurler-Scheie syndrome
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of glycosaminoglycan metabolism
E76
E76.03
Scheie's syndrome
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of glycosaminoglycan metabolism
E76
E76.1
Mucopolysaccharidosis, type II
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of glycosaminoglycan metabolism
E76
E76.2
Other mucopolysaccharidoses
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of glycosaminoglycan metabolism
E76
E76.21
Morquio mucopolysaccharidoses
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of glycosaminoglycan metabolism
E76
E76.210
Morquio A mucopolysaccharidoses
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of glycosaminoglycan metabolism
E76
E76.211
Morquio B mucopolysaccharidoses
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of glycosaminoglycan metabolism
E76
E76.219
Morquio mucopolysaccharidoses, unspecified
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of glycosaminoglycan metabolism
E76
E76.22
Sanfilippo mucopolysaccharidoses
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of glycosaminoglycan metabolism
E76
E76.29
Other mucopolysaccharidoses
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of glycosaminoglycan metabolism
E76
E76.3
Mucopolysaccharidosis, unspecified
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of glycosaminoglycan metabolism
E76
E76.8
Other disorders of glucosaminoglycan metabolism
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of glycosaminoglycan metabolism
E76
E76.9
Glucosaminoglycan metabolism disorder, unspecified
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of glycoprotein metabolism
E77
E77.0
Defects in post-translational modification of lysosomal enzymes
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of glycoprotein metabolism
E77
E77.1
Defects in glycoprotein degradation
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of glycoprotein metabolism
E77
E77.8
Other disorders of glycoprotein metabolism
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of glycoprotein metabolism
E77
E77.9
Disorder of glycoprotein metabolism, unspecified
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of lipoprotein metabolism and other lipidemias
E78
E78.0
Pure hypercholesterolemia
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of lipoprotein metabolism and other lipidemias
E78
E78.00
Pure hypercholesterolemia, unspecified
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of lipoprotein metabolism and other lipidemias
E78
E78.01
Familial hypercholesterolemia
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of lipoprotein metabolism and other lipidemias
E78
E78.1
Pure hyperglyceridemia
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of lipoprotein metabolism and other lipidemias
E78
E78.2
Mixed hyperlipidemia
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of lipoprotein metabolism and other lipidemias
E78
E78.3
Hyperchylomicronemia
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of lipoprotein metabolism and other lipidemias
E78
E78.4
Other hyperlipidemia
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of lipoprotein metabolism and other lipidemias
E78
E78.41
Elevated Lipoprotein(a)
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of lipoprotein metabolism and other lipidemias
E78
E78.49
Other hyperlipidemia
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of lipoprotein metabolism and other lipidemias
E78
E78.5
Hyperlipidemia, unspecified
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of lipoprotein metabolism and other lipidemias
E78
E78.6
Lipoprotein deficiency
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of lipoprotein metabolism and other lipidemias
E78
E78.7
Disorders of bile acid and cholesterol metabolism
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of lipoprotein metabolism and other lipidemias
E78
E78.70
Disorder of bile acid and cholesterol metabolism, unspecified
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of lipoprotein metabolism and other lipidemias
E78
E78.71
Barth syndrome
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of lipoprotein metabolism and other lipidemias
E78
E78.72
Smith-Lemli-Opitz syndrome
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of lipoprotein metabolism and other lipidemias
E78
E78.79
Other disorders of bile acid and cholesterol metabolism
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of lipoprotein metabolism and other lipidemias
E78
E78.8
Other disorders of lipoprotein metabolism
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of lipoprotein metabolism and other lipidemias
E78
E78.81
Lipoid dermatoarthritis
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of lipoprotein metabolism and other lipidemias
E78
E78.89
Other lipoprotein metabolism disorders
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of lipoprotein metabolism and other lipidemias
E78
E78.9
Disorder of lipoprotein metabolism, unspecified
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of purine and pyrimidine metabolism
E79
E79.0
Hyperuricemia without signs of inflammatory arthritis and tophaceous disease
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of purine and pyrimidine metabolism
E79
E79.1
Lesch-Nyhan syndrome
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of purine and pyrimidine metabolism
E79
E79.2
Myoadenylate deaminase deficiency
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of purine and pyrimidine metabolism
E79
E79.8
Other disorders of purine and pyrimidine metabolism
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of purine and pyrimidine metabolism
E79
E79.9
Disorder of purine and pyrimidine metabolism, unspecified
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of porphyrin and bilirubin metabolism
E80
E80.0
Hereditary erythropoietic porphyria
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of porphyrin and bilirubin metabolism
E80
E80.1
Porphyria cutanea tarda
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of porphyrin and bilirubin metabolism
E80
E80.2
Other and unspecified porphyria
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of porphyrin and bilirubin metabolism
E80
E80.20
Unspecified porphyria
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of porphyrin and bilirubin metabolism
E80
E80.21
Acute intermittent (hepatic) porphyria
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of porphyrin and bilirubin metabolism
E80
E80.29
Other porphyria
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of porphyrin and bilirubin metabolism
E80
E80.3
Defects of catalase and peroxidase
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of porphyrin and bilirubin metabolism
E80
E80.4
Gilbert syndrome
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of porphyrin and bilirubin metabolism
E80
E80.5
Crigler-Najjar syndrome
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of porphyrin and bilirubin metabolism
E80
E80.6
Other disorders of bilirubin metabolism
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of porphyrin and bilirubin metabolism
E80
E80.7
Disorder of bilirubin metabolism, unspecified
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.0
Disorders of copper metabolism
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.00
Disorder of copper metabolism, unspecified
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.01
Wilson's disease
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.09
Other disorders of copper metabolism
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.1
Disorders of iron metabolism
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.10
Disorder of iron metabolism, unspecified
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.11
Hemochromatosis
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.110
Hereditary hemochromatosis
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.111
Hemochromatosis due to repeated red blood cell transfusions
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.118
Other hemochromatosis
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.119
Hemochromatosis, unspecified
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.19
Other disorders of iron metabolism
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.2
Disorders of zinc metabolism
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.3
Disorders of phosphorus metabolism and phosphatases
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.30
Disorder of phosphorus metabolism, unspecified
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.31
Familial hypophosphatemia
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.32
Hereditary vitamin D-dependent rickets (type 1) (type 2)
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.39
Other disorders of phosphorus metabolism
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.4
Disorders of magnesium metabolism
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.40
Disorders of magnesium metabolism, unspecified
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.41
Hypermagnesemia
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.42
Hypomagnesemia
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.49
Other disorders of magnesium metabolism
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.5
Disorders of calcium metabolism
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.50
Unspecified disorder of calcium metabolism
Endocrine. nutritional and metabolic diseases (E00-E89)
Metabolic disorders
Disorders of mineral metabolism
E83
E83.51
Hypocalcemia