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## Summary ### Clinical characteristics. Cardiofaciocutaneous (CFC) syndrome is characterized by cardiac abnormalities (pulmonic stenosis and other valve dysplasias, septal defects, hypertrophic cardiomyopathy, rhythm disturbances), distinctive craniofacial appearance, and cutaneous abnormalities (including xerosis...
Cardiofaciocutaneous Syndrome
c1275081
7,100
gene_reviews
https://www.ncbi.nlm.nih.gov/books/NBK1186/
2021-01-18T21:36:27
{"mesh": ["C535579"], "synonyms": ["CFC Syndrome"]}
Lichen sclerosus is a chronic skin disorder that is more common in women, most often affecting the external part of the vagina (vulva) or the area around the anus. In men, it typically affects the tip of the penis. It can occur at any age but is usually seen in women over age 50. Some people have no symptoms, while o...
Lichen sclerosus
c0023652
7,101
gard
https://rarediseases.info.nih.gov/diseases/6905/lichen-sclerosus
2021-01-18T17:59:25
{"mesh": ["D018459"], "omim": ["151590"], "umls": ["C0023652"], "orphanet": ["33409"], "synonyms": ["Lichen sclerosis", "Lichen sclerosis et atrophicus", "Lichen sclerosus et atrophicus"]}
Wilson and Deitrick (1986) found no gallbladder in a 45-year-old mother and 23-year-old daughter. Kobacker (1950) proved agenesis of the gallbladder in 2 members of a family and suspected it from failure of visualization on oral cholecystography in 5 others. Nadeau et al. (1972) reported a family with 2 proved cases ...
GALLBLADDER, AGENESIS OF
c0266251
7,102
omim
https://www.omim.org/entry/137040
2019-09-22T16:40:56
{"mesh": ["C562564"], "omim": ["137040"], "icd-10": ["Q44.0"]}
Subcutaneous panniculitis-like T-cell lymphoma (SPTCL) is a rare type of lymphoma that mainly affects the skin. Lymphomas are cancers that result from a type of white blood cell that grows out of control. In SPTCL, people develop multiple painless nodules in the fat layer under the skin and can these cause swelling. ...
Subcutaneous panniculitis-like T-cell lymphoma
c0522624
7,103
gard
https://rarediseases.info.nih.gov/diseases/10193/subcutaneous-panniculitis-like-t-cell-lymphoma
2021-01-18T17:57:29
{"mesh": ["C537503"], "synonyms": ["SPTCL"]}
## Summary ### Clinical characteristics. Myhre syndrome is a connective tissue disorder with multisystem involvement, progressive and proliferative fibrosis that may occur spontaneously or following trauma or surgery, mild-to-moderate intellectual disability, and in some instances, autistic-like behaviors. Organ sy...
Myhre Syndrome
c0796081
7,104
gene_reviews
https://www.ncbi.nlm.nih.gov/books/NBK425723/
2021-01-18T21:10:03
{"mesh": ["C537620"], "synonyms": ["Laryngotracheal Stenosis", "Arthropathy", "Prognathism", "and Short Stature (LAPS) Syndrome; Myhre-LAPS Syndrome"]}
A number sign (#) is used with this entry because of evidence that susceptibility to microvascular complications of diabetes-5 is associated with variation in the PON1 gene (168820) on chromosome 7q21.3. For a discussion of genetic heterogeneity of susceptibility to microvascular complications of diabetes, see MVCD1...
MICROVASCULAR COMPLICATIONS OF DIABETES, SUSCEPTIBILITY TO, 5
c2674665
7,105
omim
https://www.omim.org/entry/612633
2019-09-22T16:00:57
{"omim": ["612633"], "synonyms": ["Alternative titles", "RETINOPATHY, DIABETIC, SUSCEPTIBILITY TO"]}
A number sign (#) is used with this entry because of evidence that congenital disorder of glycosylation type Iy (CDG1Y) is caused by hemizygous mutation in the SSR4 gene (300090) on chromosome Xq28. For discussion of the classification of CDGs, see CDG1A (212065). Clinical Features Losfeld et al. (2014) reported a...
CONGENITAL DISORDER OF GLYCOSYLATION, TYPE Iy
c4012395
7,106
omim
https://www.omim.org/entry/300934
2019-09-22T16:19:16
{"doid": ["0080574"], "omim": ["300934"], "orphanet": ["370927"], "synonyms": ["CDG syndrome type Iy", "Congenital disorder of glycosylation type Iy", "CDG-Iy", "Congenital disorder of glycosylation type 1y", "CDG1Y", "CDG IY", "Alternative titles", "Carbohydrate deficient glycoprotein syndrome type Iy"], "genereviews"...
Patellar subluxation syndrome Other namesPatellar instability, Onstable kneecap Patellar subluxation syndrome, is an injury that is concerned with the kneecap. Patellar subluxation is more common than patellar dislocation and is just as disabling.[1] In this condition, the patella repetitively subluxates and ...
Patellar subluxation syndrome
c0857276
7,107
wikipedia
https://en.wikipedia.org/wiki/Patellar_subluxation_syndrome
2021-01-18T18:58:41
{"umls": ["C0857276"], "wikidata": ["Q7144432"]}
This article needs additional citations for verification. Please help improve this article by adding citations to reliable sources. Unsourced material may be challenged and removed. Find sources: "Congenital epulis" – news · newspapers · books · scholar · JSTOR (April 2008) (Learn how and when to remove this templa...
Congenital epulis
c0376319
7,108
wikipedia
https://en.wikipedia.org/wiki/Congenital_epulis
2021-01-18T18:27:59
{"mesh": ["D005887"], "umls": ["C0376319"], "orphanet": ["157826"], "wikidata": ["Q5160427"]}
Trichorhinophalangeal syndrome type 3 (TRPS3), also known as Sugio-Kajii syndrome, is an extremely rare inherited multisystem disorder. TRPS3 is characterized by short stature, sparse hair, a bulbous nasal tip and cone-shaped epiphyses (the growing ends of bones), as well as severe generalized shortening of all f...
Trichorhinophalangeal syndrome type 3
c1860823
7,109
gard
https://rarediseases.info.nih.gov/diseases/7802/trichorhinophalangeal-syndrome-type-3
2021-01-18T17:57:18
{"mesh": ["C566033"], "omim": ["190351"], "umls": ["C1860823"], "orphanet": ["77258"], "synonyms": ["TRPS 3", "Sugio-Kajii Syndrome"]}
Voice disorder Hoarse voice Other namesHoarseness, dysphonia The vocal folds (or vocal cords) in the larynx vibrate to produce sound. When this process is disturbed hoarseness may ensue. SpecialtyOtolaryngology A hoarse voice, also known as dysphonia or hoarseness,[1] is when the voice involuntarily sound...
Hoarse voice
c1527344
7,110
wikipedia
https://en.wikipedia.org/wiki/Hoarse_voice
2021-01-18T18:53:39
{"mesh": ["D055154"], "umls": ["C1527344"], "icd-9": ["784.42"], "icd-10": ["R49"], "wikidata": ["Q836379"]}
Laryngoonychocutaneous syndrome SpecialtyDermatology Laryngo-onycho-cutaneous syndrome (also known as Shabbir syndrome) is a rare epithelial disorder inherited in an autosomal recessive fashion.[1][2] It is characterized by abnormalities in the larynx, nails ("onycho-"), and skin ("cutaneous").[3] The diso...
Laryngo-onycho-cutaneous syndrome
c1328355
7,111
wikipedia
https://en.wikipedia.org/wiki/Laryngo-onycho-cutaneous_syndrome
2021-01-18T19:06:59
{"mesh": ["C537032"], "umls": ["C1328355"], "orphanet": ["2407"], "wikidata": ["Q6491971"]}
Aspermia SpecialtyUrology Aspermia is the complete lack of semen with ejaculation (not to be confused with azoospermia, the lack of sperm cells in the semen). It is associated with infertility. One of the causes of aspermia is retrograde ejaculation,[1] which can be brought on by excessive drug use, or as...
Aspermia
c1704202
7,112
wikipedia
https://en.wikipedia.org/wiki/Aspermia
2021-01-18T18:39:27
{"mesh": ["D053714"], "icd-9": ["606.0"], "icd-10": ["N46"], "wikidata": ["Q736599"]}
A number sign (#) is used with this entry because of evidence that susceptibility to sarcoidosis-2 (SS2) is conferred by variation in the BTNL2 gene (606000) on chromosome 6p21. For a general description and a discussion of genetic heterogeneity of sarcoidosis, see 181000. Mapping Valentonyte et al. (2005) not...
SARCOIDOSIS, SUSCEPTIBILITY TO, 2
c0036202
7,113
omim
https://www.omim.org/entry/612387
2019-09-22T16:01:36
{"mesh": ["D012507"], "omim": ["612387"], "orphanet": ["797"]}
A rare genetic multiple congenital anomalies/dysmorphic syndrome characterized by global developmental delay, intellectual disability, short stature, skeletal abnormalities (such as brachydactyly and vertebral anomalies), obesity, cardiac, respiratory, and genitourinary anomalies, and dysmorphic facial features (incl...
Cognitive impairment-coarse facies-heart defects-obesity-pulmonary involvement-short stature-skeletal dysplasia syndrome
c4085597
7,114
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=444077
2021-01-23T17:56:21
{"gard": ["12845"], "omim": ["616368"], "icd-10": ["Q87.8"], "synonyms": ["CHOPS syndrome"]}
A rare autosomal recessive complex spastic paraplegia characterized by mostly adult-onset progressive spasticity and weakness predominantly affecting the lower limbs, axonal motor and sensory neuropathy, and cerebellar symptoms like ataxia, dysarthria, and oculomotor abnormalities. Variable degrees of cognitive impai...
Autosomal recessive spastic paraplegia type 78
c4310662
7,115
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=513436
2021-01-23T17:00:47
{"omim": ["617225"], "synonyms": ["SPG78"]}
A rare inflammatory demyelinating disorder of the spinal cord that can be either idiopathic (IATM) or secondary to a known cause (SATM). ## Epidemiology Annual incidence of IATM is estimated between 1/1,000,000 and 1/250,000. Incidence of SATM is variable and depends of the underlying disease. ## Clinical descript...
Acute transverse myelitis
c0270627
7,116
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=139417
2021-01-23T18:32:21
{"mesh": ["D009188"], "umls": ["C0270627"], "icd-10": ["G37.3"]}
Disorder caused due to injury to the spinal accessory nerve (11th cranial nerve or Cranial Nerve XI) Accessory nerve disorder Other namesSpinal accessory nerve palsy Muscles innervated by the accessory nerve SpecialtyNeurology Accessory nerve disorder is an injury to the spinal accessory nerve which resul...
Accessory nerve disorder
c0152180
7,117
wikipedia
https://en.wikipedia.org/wiki/Accessory_nerve_disorder
2021-01-18T18:43:01
{"mesh": ["D020436"], "umls": ["C0152180"], "icd-10": ["G52.8", "S04.7"], "wikidata": ["Q4672538"]}
Trichorrhexis nodosa Other namesHair shaft fracture[1] Tricho-hepato-enteric syndrome: Microscopic analysis of the hair shaft showing breaks located at nodes in the hair (trichorrhexis nodosa) and longitudinal breaks. SpecialtyDermatology Trichorrhexis nodosa is a defect in the hair shaft characterized...
Trichorrhexis nodosa
c0263485
7,118
wikipedia
https://en.wikipedia.org/wiki/Trichorrhexis_nodosa
2021-01-18T18:36:25
{"umls": ["C0263485"], "icd-9": ["704.2"], "icd-10": ["L67.0"], "wikidata": ["Q7840966"]}
Penile discharge This male presented with a purulent penile discharge due to gonorrhea with an overlying penile pyodermal lesion. Pyoderma involves the formation of a purulent skin lesion, in this case located on the glans penis, and overlying the sexually transmitted disease gonorrhea.[1] SymptomsFluid from ...
Penile discharge
c0232861
7,119
wikipedia
https://en.wikipedia.org/wiki/Penile_discharge
2021-01-18T18:41:15
{"umls": ["C0232861"], "icd-10": ["R36"], "wikidata": ["Q5803863"]}
Leydig cell hypoplasia is a condition that affects male sexual development. It is characterized by underdevelopment (hypoplasia) of Leydig cells in the testes. Leydig cells secrete male sex hormones (androgens) that are important for normal male sexual development before birth and during puberty. In Leydig cell hypo...
Leydig cell hypoplasia
c2673497
7,120
medlineplus
https://medlineplus.gov/genetics/condition/leydig-cell-hypoplasia/
2021-01-27T08:25:14
{"gard": ["3244"], "mesh": ["C562567"], "omim": ["238320"], "synonyms": []}
Functional gastrointestinal disorder Other namesDisorders of gut–brain interaction SpecialtyGastroenterology Functional gastrointestinal disorders (FGID), also known as disorders of gut–brain interaction, include a number of separate idiopathic disorders which affect different parts of the gastrointestinal t...
Functional gastrointestinal disorder
c0017178
7,121
wikipedia
https://en.wikipedia.org/wiki/Functional_gastrointestinal_disorder
2021-01-18T19:04:03
{"mesh": ["D005767"], "wikidata": ["Q5508825"]}
Uterine adenosarcoma Other namesAdenosarcoma of the uterus, Müllerian adenosarcoma of the uterus Micrograph of a uterine adenosarcoma showing a mitotically active malignant stroma and benign glands. H&E stain. SpecialtyGynecology Uterine adenosarcoma is an uncommon form of cancer that arises from mesenchym...
Uterine adenosarcoma
c2103110
7,122
wikipedia
https://en.wikipedia.org/wiki/Uterine_adenosarcoma
2021-01-18T18:55:46
{"gard": ["9636"], "mesh": ["C538232"], "umls": ["C2103110"], "wikidata": ["Q7902645"]}
Proopiomelanocortin (POMC) deficiency is characterized by severe obesity that begins at an early age. Affected infants are usually a normal weight at birth, but they are constantly hungry, which leads to excessive feeding and weight gain during the first year and throughout life. In addition, people with this con...
Proopiomelanocortin deficiency
c1857854
7,123
gard
https://rarediseases.info.nih.gov/diseases/10823/proopiomelanocortin-deficiency
2021-01-18T17:58:07
{"mesh": ["C565726"], "omim": ["609734"], "orphanet": ["71526"], "synonyms": ["Obesity, early-onset, adrenal insufficiency, and red hair", "POMC deficiency", "Obesity due to pro-opiomelanocortin deficiency"]}
A number sign (#) is used with this entry because of evidence that hyperphosphatemic familial tumoral calcinosis-3 (HFTC3) is caused by homozygous mutation in the KL gene (604824) on chromosome 13q13. One such patient has been reported. Description Hyperphosphatemic familial tumoral calcinosis is a rare autosomal r...
TUMORAL CALCINOSIS, HYPERPHOSPHATEMIC, FAMILIAL, 3
c4693864
7,124
omim
https://www.omim.org/entry/617994
2019-09-22T15:44:06
{"omim": ["617994", "211900"], "orphanet": ["306661"], "synonyms": ["Hypercalcemic tumoral calcinosis"]}
Bladder cancer in cats and dogs usually is transitional cell carcinoma,[1] which arises from the epithelial cells that line the bladder. Less often, cancer of the urinary bladder is squamous cell carcinoma, adenocarcinoma, or rhabdomyosarcoma. ## Contents * 1 Signs and symptoms * 2 Diagnosis * 3 Treatment *...
Bladder cancer in cats and dogs
None
7,125
wikipedia
https://en.wikipedia.org/wiki/Bladder_cancer_in_cats_and_dogs
2021-01-18T18:53:22
{"wikidata": ["Q4923664"]}
Familial British dementia SpecialtyPsychiatry Familial British dementia is a form of dementia. It was first reported by Cecil Charles Worster-Drought in 1933 [1] and is therefore also known as Worster-Drought syndrome. It is caused by a mutation in the ITM2B gene (also known as BRI2); a different mutation of t...
Familial British dementia
c1867773
7,126
wikipedia
https://en.wikipedia.org/wiki/Familial_British_dementia
2021-01-18T18:40:10
{"gard": ["8344"], "mesh": ["C538208"], "orphanet": ["97345"], "wikidata": ["Q5432926"]}
A number sign (#) is used with this entry because of evidence that autosomal recessive macrocephaly/megalencephaly syndrome (MGCPH) is caused by homozygous mutation in the TBC1D7 gene (612655) on chromosome 6p24. Description Macrocephaly refers to an abnormally enlarged head inclusive of the scalp, cranial bone...
MACROCEPHALY/MEGALENCEPHALY SYNDROME, AUTOSOMAL RECESSIVE
c0221355
7,127
omim
https://www.omim.org/entry/248000
2019-09-22T16:25:44
{"mesh": ["D058627"], "omim": ["248000"], "orphanet": ["2477"]}
X-linked intellectual disability-acromegaly-hyperactivity syndrome is characterised by severe intellectual deficit, acromegaly and hyperactivity. The syndrome has been described in two half-brothers. Dysarthria, aggressive behaviour, a characteristic facies (an acromegalic and triangular face with a long nose) and ma...
X-linked intellectual disability-acromegaly-hyperactivity syndrome
None
7,128
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=85327
2021-01-23T19:11:45
{"icd-10": ["Q87.8"]}
An X-linked mental retardation (XLMR) syndrome belonging to the group of conditions characterised by the association of intellectual deficit with hypotonic facies (Mental retardation, X-linked-hypotonic facies). ## Epidemiology Prevalence is unknown but the syndrome was originally described in 1988 in six males fro...
Carpenter-Waziri syndrome
c0796003
7,129
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=93973
2021-01-23T18:46:19
{"mesh": ["C537457"], "omim": ["309580"]}
Intraocular melanoma is a cancer of the pigment-producing cells (melanocytes) in the middle layer of the eye, called the uveal tract. The uveal tract has 3 main parts: (1) the choroid (the tissue layer filled with blood vessels); (2) the ciliary body (the ring of muscle tissue that changes the size of the pupil and t...
Intraocular melanoma
c0220633
7,130
gard
https://rarediseases.info.nih.gov/diseases/8621/intraocular-melanoma
2021-01-18T17:59:44
{"mesh": ["C536494"], "omim": ["155720"], "umls": ["C0220633"], "orphanet": ["39044"], "synonyms": ["Melanoma of the Uvea", "Uveal melanoma"]}
See TIM10 (602251) and Koehler et al. (1998). *[v]: View this template *[t]: Discuss this template *[e]: Edit this template *[c.]: circa *[AA]: Adrenergic agonist *[AD]: Acetaldehyde dehydrogenase *[HAART]: highly active antiretroviral therapy *[Ki]: Inhibitor constant *[nM]: nanomolars *[MOR...
MITOCHONDRIAL INTERMEMBRANE SPACE PROTEIN TIM12, YEAST, HOMOLOG OF
c1865698
7,131
omim
https://www.omim.org/entry/602252
2019-09-22T16:13:52
{"omim": ["602252"]}
A form of renal hypoplasia characterized by bilateral small kidneys with a deficit in the number of nephrons present. The condition is typically asymptomatic but may be associated with hypertension, and some excretory functional limitations, as well as eventual chronic renal failure. *[v]: View this template *[t...
Renal hypoplasia, bilateral
c0431692
7,132
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=97362
2021-01-23T17:15:51
{"umls": ["C0431692"], "icd-10": ["Q60.4"]}
Hereditary disease characterized by involuntary painful muscle contractions resulting in uncontrollable distortions Torsion dystonia Other namesDystonia musculorum deformans SpecialtyNeurology Torsion dystonia, also known as dystonia musculorum deformans, is a disease characterized by painful muscle contrac...
Torsion dystonia
c0013423
7,133
wikipedia
https://en.wikipedia.org/wiki/Torsion_dystonia
2021-01-18T19:06:06
{"mesh": ["D004422"], "icd-9": ["333.6"], "icd-10": ["G24.1"], "wikidata": ["Q656199"]}
Primary systemic amyloidosis (PSA) is a form of AL amyloidosis (see this term) caused by the aggregation and deposition of insoluble amyloid fibrils derived from misfolded monoclonal immunoglobulin light chains usually produced by a plasma cell tumor (see this term) and characterized by multiple organ involvement...
Primary systemic amyloidosis
c0268381
7,134
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=314701
2021-01-23T16:56:30
{"mesh": ["D000075363"], "omim": ["254500"], "icd-10": ["E85.0", "E85.1", "E85.2", "E85.3"], "synonyms": ["Systemic AL amyloidosis"]}
## Clinical Features Felman (1969) described a black father and his son and daughter with epiphyseal and vertebral dysplasia producing severe scoliosis and truncal shortening as well as complete destruction of the femoral capital epiphyses and necks. The hands and feet were short and stubby. Clinically and radiolog...
SPONDYLOEPIPHYSEAL DYSPLASIA TARDA, AUTOSOMAL DOMINANT
c1866717
7,135
omim
https://www.omim.org/entry/184100
2019-09-22T16:34:23
{"mesh": ["C566658"], "omim": ["184100"], "orphanet": ["93284"], "synonyms": []}
Cutaneous diphtheria infection SpecialtyInfectious disease Cutaneous diphtheria is an infection of the skin by Corynebacterium diphtheriae.[1]:265 It is also known as "desert sore".[2] ## See also[edit] * Diphtheria * Skin lesion ## References[edit] 1. ^ James, William D.; Berger, Timothy G.; et al. ...
Cutaneous diphtheria infection
c0012555
7,136
wikipedia
https://en.wikipedia.org/wiki/Cutaneous_diphtheria_infection
2021-01-18T18:49:27
{"umls": ["C0012555"], "wikidata": ["Q5196693"]}
Sympathetic uveitis Other namesspared eye injury SpecialtyOphthalmology Symptomsfloaters, photophobia Complicationsuveitis, blindness Sympathetic ophthalmia (SO), also called spared eye injury, is a diffuse granulomatous inflammation of the uveal layer of both eyes following trauma to one eye. It can...
Sympathetic ophthalmia
c0029077
7,137
wikipedia
https://en.wikipedia.org/wiki/Sympathetic_ophthalmia
2021-01-18T18:30:15
{"mesh": ["D009879"], "umls": ["C0029077"], "orphanet": ["79098"], "wikidata": ["Q2037487"]}
## Clinical Features Fitzsimmons et al. (1983) reported mental retardation with spastic paraplegia and palmoplantar hyperkeratosis in 4 brothers whose ages ranged from 16 to 35 years at the time of report. Pes cavus was striking. The mother was of normal intelligence but had plantar hyperkeratosis and a strong ...
MENTAL RETARDATION WITH SPASTIC PARAPLEGIA AND PALMOPLANTAR HYPERKERATOSIS
c2745996
7,138
omim
https://www.omim.org/entry/309560
2019-09-22T16:17:49
{"mesh": ["C537058"], "omim": ["309560"], "orphanet": ["2824"]}
Rare X-linked form of chondrodysplasia punctata Conradi–Hünermann syndrome Other names"Conradi–Hünermann–Happle syndrome",[1]:500 "Happle syndrome,"[2] and "X-linked dominant chondrodysplasia punctata"[2] SpecialtyMedical genetics Conradi–Hünermann syndrome is a rare type of chondrodysplasia punctata. It is...
Conradi–Hünermann syndrome
None
7,139
wikipedia
https://en.wikipedia.org/wiki/Conradi%E2%80%93H%C3%BCnermann_syndrome
2021-01-18T18:58:40
{"icd-9": ["756.59"], "icd-10": ["Q77.3"], "wikidata": ["Q2964437"]}
A rare genetic neuromuscular disease characterized by late onset of mild, progressive, proximal muscle weakness, severe myalgias during and after exercise, and susceptibility to rhabdomyolysis. Intellectual disability is mild or absent. There are no abnormalities of the skin. Muscle biopsy shows focal depletion o...
Proximal myopathy with focal depletion of mitochondria
c1833453
7,140
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=521305
2021-01-23T16:54:56
{"mesh": ["C563453"], "omim": ["600706"]}
Severe early childhood onset retinal dystrophy (SECORD) is an inherited retinal dystrophy characterized by a severe congenital night blindness, progressive retinal dystrophy and nystagmus. Best corrected visual acuity can reach 0.3 in the first decade of life and can pertain well into the second decade of life. Blind...
Severe early-childhood-onset retinal dystrophy
c1858080
7,141
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=364055
2021-01-23T19:03:16
{"mesh": ["C565741"], "umls": ["C1858080"], "icd-10": ["H35.5"], "synonyms": ["EOSRD", "Early-onset severe retinal dystrophy", "SECORD"]}
Granulomatous facial dermatitis is found in patients with persistent facial erythema involving one or more convex surfaces of the face, with lesions that show granulomatous reaction histologically.[1] ## See also[edit] * List of cutaneous conditions ## References[edit] 1. ^ James, William; Berger, Timothy; El...
Granulomatous facial dermatitis
None
7,142
wikipedia
https://en.wikipedia.org/wiki/Granulomatous_facial_dermatitis
2021-01-18T18:52:27
{"wikidata": ["Q5596831"]}
Craniofrontonasal dysplasia is a rare genetic condition with several skeletal defects. Main features of this condition include widely spaced eyes (hypertelorism), bifid tip of the nose, broad head (brachycephaly), prominent forehead (frontal bossing), asymmetry of facial features, abnoral form of the eyebrow, and...
Craniofrontonasal dysplasia
c0220767
7,143
gard
https://rarediseases.info.nih.gov/diseases/1578/craniofrontonasal-dysplasia
2021-01-18T18:01:03
{"mesh": ["C536456"], "omim": ["304110"], "umls": ["C0220767"], "orphanet": ["1520"], "synonyms": ["Craniofrontonasal syndrome", "CFNS", "CFND", "Craniofrontonasal dysostosis"]}
Chronic ulcer of skin where the ulcer is an ulceration of tissue deprived of adequate blood supply by prolonged pressure Pressure ulcer Other namesDecubiti, decubitus, or decubitous ulcers, pressure injuries, pressure sores, bedsores Stage IV decubitus displaying the tuberosity of the ischium protruding through ...
Pressure ulcer
c0011127
7,144
wikipedia
https://en.wikipedia.org/wiki/Pressure_ulcer
2021-01-18T18:29:06
{"mesh": ["D003668"], "umls": ["C0011127"], "wikidata": ["Q308978"]}
Coats disease is an eye disorder characterized by abnormal development of the blood vessels in the retina (retinal telangiectasia). Most people begin showing symptoms in childhood. Early signs and symptoms vary but may include vision loss, "crossed eyes" (strabismus), and a white mass in the pupil behind the lens...
Coats disease
c0154832
7,145
gard
https://rarediseases.info.nih.gov/diseases/6121/coats-disease
2021-01-18T18:01:16
{"mesh": ["D058456"], "omim": ["300216"], "umls": ["C0154832"], "orphanet": ["190"], "synonyms": ["Retinal telangiectasis", "Leber miliary aneurysm"]}
HIV-associated lipodystrophy Other namesLipodystrophy in HIV-infected patients (LD-HIV) SpecialtyImmunology, dermatology, infectious disease, endocrinology HIV-associated lipodystrophy, is a condition characterized by loss of subcutaneous fat associated with infection with HIV.[1]:497 ## Contents * 1 Pre...
HIV-associated lipodystrophy
c1136321
7,146
wikipedia
https://en.wikipedia.org/wiki/HIV-associated_lipodystrophy
2021-01-18T18:28:48
{"mesh": ["D039682"], "wikidata": ["Q5629813"]}
"Pustule" redirects here. It is not to be confused with Boil. See also: List of cutaneous conditions Skin condition Other namesCutaneous condition 3D medical illustration showing major layers of skin SpecialtyDermatology CausesSun exposure, vitamin deficiencies, substance usage, poor hygiene, cancers ...
Skin condition
c0037277
7,147
wikipedia
https://en.wikipedia.org/wiki/Skin_condition
2021-01-18T18:59:27
{"mesh": ["D012871", "D012873"], "umls": ["C0037277", "C0037274", "C0029574"], "icd-10": ["L98.9"], "wikidata": ["Q949302"]}
A number sign (#) is used with this entry because of evidence that orofaciodigital syndrome-5 (OFD5) is caused by homozygous mutation in the DDX59 gene (615464) on chromosome 1q32. Clinical Features Rischbieth (1910) pictured a Hindu patient with postaxial polydactyly and median cleft of the upper lip. His brot...
OROFACIODIGITAL SYNDROME V
c1868118
7,148
omim
https://www.omim.org/entry/174300
2019-09-22T16:36:03
{"doid": ["0060375"], "mesh": ["C557819"], "omim": ["174300"], "orphanet": ["2919"], "synonyms": ["Alternative titles", "OFDS V", "ORAL-FACIAL-DIGITAL SYNDROME, TYPE V", "OROFACIODIGITAL SYNDROME, THURSTON TYPE", "THURSTON SYNDROME", "POLYDACTYLY, POSTAXIAL, WITH MEDIAN CLEFT OF UPPER LIP"]}
Double vision "Double vision" redirects here. For other uses, see Double vision (disambiguation). Diplopia Other namesDouble vision One way a person might experience double vision SpecialtyNeurology, ophthalmology Diplopia is the simultaneous perception of two images of a single object that may be displa...
Diplopia
c0012569
7,149
wikipedia
https://en.wikipedia.org/wiki/Diplopia
2021-01-18T18:41:42
{"mesh": ["D004172"], "umls": ["C0012569"], "icd-9": ["368.2"], "icd-10": ["H53.2"], "wikidata": ["Q775940"]}
Infection that is acquired in a hospital or other health care facility This article has multiple issues. Please help improve it or discuss these issues on the talk page. (Learn how and when to remove these template messages) This article needs additional citations for verification. Please help improve this arti...
Hospital-acquired infection
c0205721
7,150
wikipedia
https://en.wikipedia.org/wiki/Hospital-acquired_infection
2021-01-18T18:41:50
{"mesh": ["D003428"], "umls": ["C0205721"], "icd-10": ["Y95"], "wikidata": ["Q215509"]}
Infective endocarditis Other namesBacterial endocarditis A mitral valve vegetation caused by bacterial endocarditis. SpecialtyCardiology, Infectious disease SymptomsFever, small areas of bleeding into the skin, heart murmur, feeling tired, low red blood cells[1] ComplicationsValvular insufficiency, hear...
Infective endocarditis
c1541923
7,151
wikipedia
https://en.wikipedia.org/wiki/Infective_endocarditis
2021-01-18T18:57:47
{"gard": ["6337"], "mesh": ["D004696"], "umls": ["C1541923", "C0014118"], "icd-9": ["421.1", "421.0"], "icd-10": ["I33"], "wikidata": ["Q2450598"]}
A form of oculocutaneous albinism characterized by variable hypopigmentation of the skin and hair, numerous characteristic ocular changes and misrouting of the optic nerves at the chiasm. ## Epidemiology The prevalence of Oculocutaneous albinism type 2 (OCA2) is estimated at 1/38,000-1/40,000 in most population...
Oculocutaneous albinism type 2
c0268495
7,152
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=79432
2021-01-23T18:27:58
{"gard": ["4038"], "mesh": ["C537730"], "omim": ["203200"], "umls": ["C0268495"], "icd-10": ["E70.3"], "synonyms": ["OCA2"]}
A number sign (#) is used with this entry because of evidence that Shprintzen-Goldberg craniosynostosis syndrome (SGS) is caused by heterozygous mutation in the SKI gene (164780) on chromosome 1p36. Description Shprintzen-Goldberg syndrome is a disorder comprising craniosynostosis, a marfanoid habitus, and skeletal...
SHPRINTZEN-GOLDBERG CRANIOSYNOSTOSIS SYNDROME
c1321551
7,153
omim
https://www.omim.org/entry/182212
2019-09-22T16:34:51
{"doid": ["2340"], "mesh": ["C537328"], "omim": ["182212"], "orphanet": ["2462"], "synonyms": ["Alternative titles", "CRANIOSYNOSTOSIS WITH ARACHNODACTYLY AND ABDOMINAL HERNIAS", "MARFANOID DISORDER WITH CRANIOSYNOSTOSIS, TYPE I", "MARFANOID CRANIOSYNOSTOSIS SYNDROME"], "genereviews": ["NBK1277"]}
A number sign (#) is used with this entry because susceptibility to the development of autosomal dominant Parkinson disease-13 may be conferred by heterozygous mutation in the HTRA2 gene (606441) on chromosome 2p13. For a phenotypic description and a discussion of genetic heterogeneity of Parkinson disease, see PD (...
PARKINSON DISEASE 13, AUTOSOMAL DOMINANT, SUSCEPTIBILITY TO
c1853202
7,154
omim
https://www.omim.org/entry/610297
2019-09-22T16:04:43
{"omim": ["610297"], "orphanet": ["2828"], "synonyms": ["Early-onset Parkinson disease", "YOPD"], "genereviews": ["NBK1223"]}
Serotoninergic syndrome is characterised by an excess of serotonin in the central nervous system, associated with the use of various agents, including selective serotonin reuptake inhibitors (SSRIs). ## Epidemiology Data regarding prevalence in Europe are not available. ## Clinical description Serotoninergic synd...
Serotonin syndrome
c0699828
7,155
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=43116
2021-01-23T17:12:45
{"mesh": ["D020230"], "umls": ["C0699828"], "synonyms": ["Serotonergic syndrome", "Serotonin storm", "Serotonin toxicity", "Serotonin toxidrome"]}
Tuffli and Laxova (1983) observed a 15-year-old boy with aplasia cutis verticis, hypohidrosis, nipple hypoplasia, onychodysplasia and delayed dental eruption with minor tooth anomalies who developed a large left adrenal cyst. The mother had similar changes of ectodermal dysplasia (including breast hypoplasia and lack...
ECTODERMAL DYSPLASIA WITH ADRENAL CYST
c1851850
7,156
omim
https://www.omim.org/entry/129550
2019-09-22T16:41:54
{"mesh": ["C538015"], "omim": ["129550"], "orphanet": ["3391"]}
A - Cabot ring B - Howell-Jolly body Cabot ring Cabot rings are thin, red-violet staining, threadlike strands in the shape of a loop or figure-8 that are found on rare occasions in red blood cells (erythrocytes). They are believed to be microtubules that are remnants from a mitotic spindle, and their presence ind...
Cabot rings
c0333813
7,157
wikipedia
https://en.wikipedia.org/wiki/Cabot_rings
2021-01-18T18:52:23
{"umls": ["C0333813"], "wikidata": ["Q4892104"]}
Daum et al. (1958) described a 6-month-old child with frontal bone protrusion, encephalocele, craniosynostosis, and developmental retardation. Jabbour and Taybi (1964) reported a similarly affected child whose condition they designated craniotelencephalic dysplasia. Hughes et al. (1983) reported 2 affected sister...
CRANIOTELENCEPHALIC DYSPLASIA
c1857471
7,158
omim
https://www.omim.org/entry/218670
2019-09-22T16:29:14
{"mesh": ["C535597"], "omim": ["218670"], "orphanet": ["1528"]}
Muscular dystrophy (MD) refers to a group of more than 30 genetic diseases characterized by progressive weakness and degeneration of the skeletal muscles that control movement. Some forms of MD are seen in newborns, infants or children, while others have late-onset and may not appear until middle age or later. The di...
Muscular dystrophy
c0026850
7,159
gard
https://rarediseases.info.nih.gov/diseases/7922/muscular-dystrophy
2021-01-18T17:58:52
{"mesh": ["D009136"], "umls": ["C0026850"], "synonyms": []}
A number sign (#) is used with this entry because dystonia-25 (DYT25) is caused by heterozygous mutation in the GNAL gene (139312) on chromosome 18p11. Description Dystonia-25 is an autosomal dominant neurologic disorder characterized by adult onset of focal dystonia, usually involving the neck. The dystonia most o...
DYSTONIA 25
c3554447
7,160
omim
https://www.omim.org/entry/615073
2019-09-22T15:53:15
{"doid": ["0090055"], "omim": ["615073"], "orphanet": ["329466"], "synonyms": ["DYT25", "Dystonia 25"], "genereviews": ["NBK535640"]}
Jessner lymphocytic infiltration of the skin (JLIS) is a chronic benign cutaneous disease characterized by asymptomatic non-scaly erythematous papules or plaques on the face and neck. ## Epidemiology The disease is rare, but the exact prevalence is unknown. ## Clinical description Onset usually occurs between 30 ...
Jessner lymphocytic infiltration of the skin
c0580181
7,161
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=33314
2021-01-23T18:29:13
{"gard": ["6940"], "umls": ["C0580181"], "icd-10": ["L98.6"], "synonyms": ["Jessner-Kanof lymphocytic infiltration of the skin"]}
A number sign (#) is used with this entry because of evidence that spermatogenic failure-35 (SPGF35) is caused by homozygous mutation in the QRICH2 gene (618304) on chromosome 17q25. Description Spermatogenic failure-35 is characterized by multiple morphologic abnormalities of the flagella (MMAF), resulting in sper...
SPERMATOGENIC FAILURE 35
None
7,162
omim
https://www.omim.org/entry/618341
2019-09-22T15:42:27
{"omim": ["618341"]}
Leukoencephalopathy with thalamus and brainstem involvement and high lactate (LTBL) is a disorder that affects the brain. LTBL is one of a group of genetic disorders called leukodystrophies, which feature abnormalities of the nervous system's white matter. White matter consists of nerve fibers covered by a fatty subs...
Leukoencephalopathy with thalamus and brainstem involvement and high lactate
c3554079
7,163
medlineplus
https://medlineplus.gov/genetics/condition/leukoencephalopathy-with-thalamus-and-brainstem-involvement-and-high-lactate/
2021-01-27T08:24:53
{"omim": ["614924"], "synonyms": []}
A clinical photograph showing a patient with the flexed posture. It can be abated when lying down.[1] Camptocormia, also known as bent spine syndrome (BSS), is a symptom of a multitude of diseases that is most commonly seen in the elderly. It is identified by an abnormal thoracolumbar spinal flexion, which is a forw...
Camptocormia
c0264162
7,164
wikipedia
https://en.wikipedia.org/wiki/Camptocormia
2021-01-18T18:50:47
{"mesh": ["C537968"], "wikidata": ["Q1723395"]}
A number sign (#) is used with this entry because of evidence that primary ciliary dyskinesia-21 (CILD21) is caused by homozygous mutation in the DRC1 gene (615288) on chromosome 2p23. Description Primary ciliary dyskinesia-21 is an autosomal recessive ciliopathy characterized by infantile onset of chronic sinopulm...
CILIARY DYSKINESIA, PRIMARY, 21
c0022521
7,165
omim
https://www.omim.org/entry/615294
2019-09-22T15:52:36
{"doid": ["0110596"], "mesh": ["D007619"], "omim": ["244400", "615294"], "orphanet": ["244"], "synonyms": ["Alternative titles", "PCD", "CILIARY DYSKINESIA, PRIMARY, 21, WITHOUT SITUS INVERSUS"], "genereviews": ["NBK1122"]}
A red oscar that has died while showing HLLE Head and lateral line erosion, (HLLE) or hole-in-the-head (HITH) is a disease in fish. Chronic ulcerative dermatopathy or chronic erosive dermatopathy are symptoms of similar conditions with different etiology. ## Contents * 1 Symptoms * 2 Causes * 3 Cure * 4 Re...
Head and lateral line erosion
None
7,166
wikipedia
https://en.wikipedia.org/wiki/Head_and_lateral_line_erosion
2021-01-18T18:28:31
{"wikidata": ["Q5689273"]}
Potassium-aggravated myotonia is a disorder that affects muscles used for movement (skeletal muscles). Beginning in childhood or adolescence, people with this condition experience bouts of sustained muscle tensing (myotonia) that prevent muscles from relaxing normally. Myotonia causes muscle stiffness that worsen...
Potassium-aggravated myotonia
c2931826
7,167
medlineplus
https://medlineplus.gov/genetics/condition/potassium-aggravated-myotonia/
2021-01-27T08:25:02
{"gard": ["4459"], "mesh": ["C538353"], "omim": ["608390"], "synonyms": []}
This article includes a list of general references, but it remains largely unverified because it lacks sufficient corresponding inline citations. Please help to improve this article by introducing more precise citations. (April 2009) (Learn how and when to remove this template message) Juvenile dermatomyositis ...
Juvenile dermatomyositis
c0263666
7,168
wikipedia
https://en.wikipedia.org/wiki/Juvenile_dermatomyositis
2021-01-18T18:38:38
{"gard": ["6805"], "mesh": ["D003882"], "umls": ["C0263666"], "orphanet": ["93672"], "wikidata": ["Q6318950"]}
A number sign (#) is used with this entry because glutathione synthetase deficiency, or 5-oxoprolinuria, is caused by homozygous or compound heterozygous mutation in the gene encoding glutathione synthetase (GSS; 601002) on chromosome 20q11. The same gene is mutant in hemolytic anemia due to glutathione synthetas...
GLUTATHIONE SYNTHETASE DEFICIENCY
c0398746
7,169
omim
https://www.omim.org/entry/266130
2019-09-22T16:23:01
{"mesh": ["C536835"], "omim": ["266130"], "orphanet": ["32", "289846"], "synonyms": ["Alternative titles", "5-OXOPROLINURIA", "PYROGLUTAMIC ACIDURIA"]}
A rare variant of mycosis fungoides (MF), a form of cutaneous T-cell lymphoma, characterized by the presence of folliculotropic infiltrates in patch-plaque lesions usually involving the head and neck area. ## Epidemiology The annual incidence of MF and its variants is estimated at between 1/350,000 and 1/110,000, w...
Folliculotropic mycosis fungoides
c1627767
7,170
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=178512
2021-01-23T18:11:13
{"umls": ["C1627767"], "icd-10": ["C84.0"], "synonyms": ["Mycosis fungoides-associated follicular mucinosis"]}
A number sign (#) is used with this entry because of evidence that ichthyosis, leukocyte vacuoles, alopecia, and sclerosing cholangitis (ILVASC) is caused by homozygous mutation in the CLDN1 gene (603718) on chromosome 3q28. Clinical Features Baala et al. (2002) described a novel autosomal recessive ichthyosis synd...
ICHTHYOSIS, LEUKOCYTE VACUOLES, ALOPECIA, AND SCLEROSING CHOLANGITIS
c1843355
7,171
omim
https://www.omim.org/entry/607626
2019-09-22T16:09:00
{"mesh": ["C564365"], "omim": ["607626"], "orphanet": ["59303"], "synonyms": ["Alternative titles", "ICHTHYOSIS-SCLEROSING CHOLANGITIS SYNDROME", "NEONATAL ICHTHYOSIS-SCLEROSING CHOLANGITIS SYNDROME", "NISCH SYNDROME"]}
Aman vibhore SpecialtyHematology and oncology Accelerated phase chronic myelogenous leukemia is a phase of chronic myelogenous leukemia in which the disease is progressing.[1] In this phase, 10 to 19% of the cells in the blood and bone marrow are blast cells (immature blood cells). In the accelerated phase, th...
Accelerated phase chronic myelogenous leukemia
c0023472
7,172
wikipedia
https://en.wikipedia.org/wiki/Accelerated_phase_chronic_myelogenous_leukemia
2021-01-18T18:45:15
{"mesh": ["D015465"], "wikidata": ["Q268832"]}
Mosquito bite allergies (MBA), also termed hypersensitivity to mosquito bites (HMB), are excessive reactions of varying severity to mosquito bites. Circumscribed erythema related to severe mosquito bite allergy. MBA are not caused by any toxin or pathogen in the saliva injected by a female mosquito at the time ...
Mosquito bite allergy
c0277369
7,173
wikipedia
https://en.wikipedia.org/wiki/Mosquito_bite_allergy
2021-01-18T18:58:36
{"umls": ["C0277369"], "wikidata": ["Q4246325"]}
Isolated glycerol kinase deficiency (GKD) is a very rare X-linked disorder of glycerol metabolism characterized biochemically by elevated plasma and urine glycerol levels, and clinically by variable neurometabolic manifestations, depending on the age of onset, and varying from a life-threatening childhood metabolic c...
Isolated glycerol kinase deficiency
c0268418
7,174
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=408
2021-01-23T17:21:40
{"gard": ["2807"], "mesh": ["C538138"], "omim": ["307030"], "umls": ["C0268418", "C0574108"], "icd-10": ["E74.8"], "synonyms": ["Hyperglycerolemia"]}
## Clinical Features Townes et al. (1988) described a sibship in which there were twins with anencephaly and a female infant with aprosencephaly, fused humerus and radius, and oligodactyly. Townes et al. (1988) suggested that the XK aprosencephaly syndrome may be an autosomal recessive disorder. The authors noted t...
APROSENCEPHALY SYNDROME
c0431348
7,175
omim
https://www.omim.org/entry/207770
2019-09-22T16:30:52
{"omim": ["207770"], "orphanet": ["3469"], "synonyms": ["Alternative titles", "XK SYNDROME", "GARCIA-LURIE SYNDROME"]}
Human disease Thyrotoxic periodic paralysis Thyrotoxic periodic paralysis occurs when the thyroid gland releases excessive amounts of thyroxine (thyroid hormone). SpecialtyEndocrinology Thyrotoxic periodic paralysis (TPP) is a condition featuring attacks of muscle weakness in the presence of hyperthyroidism...
Thyrotoxic periodic paralysis
c2749982
7,176
wikipedia
https://en.wikipedia.org/wiki/Thyrotoxic_periodic_paralysis
2021-01-18T18:55:15
{"gard": ["10814"], "umls": ["C2749982", "C0268446"], "icd-9": ["359.3"], "icd-10": ["G72.3"], "orphanet": ["79102"], "wikidata": ["Q2702863"]}
A rare genetic neurological disorder characterized by subacute encephalopathy with confusion, seizures, and movement disorder, often following a history of febrile illness. Imaging may reveal bilateral lesions in the basal ganglia. The disease usually becomes symptomatic in childhood and is life-threatening if le...
Biotin-thiamine-responsive basal ganglia disease
c1843807
7,177
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=65284
2021-01-23T19:07:20
{"gard": ["10237"], "mesh": ["C537658"], "omim": ["607483"], "umls": ["C1843807"], "icd-10": ["G93.8"], "synonyms": ["BBGD", "BTBGD", "Biotin-responsive basal ganglia disease"]}
Complication of pregnancy associated with severe pre-eclampsia HELLP syndrome SpecialtyObstetrics SymptomsFeeling tired, retaining fluid, headache, nausea, upper abdominal pain, blurry vision, seizures[1] ComplicationsDisseminated intravascular coagulation (DIC), placental abruption, kidney failure, pulmonary ...
HELLP syndrome
c0162739
7,178
wikipedia
https://en.wikipedia.org/wiki/HELLP_syndrome
2021-01-18T18:57:40
{"gard": ["8528"], "mesh": ["D017359"], "umls": ["C0162739"], "orphanet": ["244242"], "wikidata": ["Q1563513"]}
Autoimmune progesterone dermatitis SpecialtyDermatology Autoimmune progesterone dermatitis may appear as urticarial papules, deep gyrate lesions, papulovesicular lesions, an eczematous eruption, or as targetoid lesions.[1]:82 Autoimmune progesterone dermatitis initially manifests with eye symptoms, e.g. bu...
Autoimmune progesterone dermatitis
c1260879
7,179
wikipedia
https://en.wikipedia.org/wiki/Autoimmune_progesterone_dermatitis
2021-01-18T19:05:58
{"gard": ["9139"], "mesh": ["C535299"], "umls": ["C1260879"], "wikidata": ["Q4826347"]}
A number sign (#) is used with this entry because of evidence that erythrokeratodermia variabilis et progressiva-5 (EKVP5) is caused by homozygous mutation in the KRT83 gene (602765) on chromosome 12q13. One such family has been reported. For a general phenotypic description and discussion of genetic heterogenei...
ERYTHROKERATODERMIA VARIABILIS ET PROGRESSIVA 5
c4540331
7,180
omim
https://www.omim.org/entry/617756
2019-09-22T15:44:56
{"doid": ["0080251"], "omim": ["617756"], "orphanet": ["316"], "synonyms": ["Darier-Gottron disease", "Erythrokeratodermia progressiva symmetrica", "Progressive symmetric erythrokeratodermia, Gottron type"]}
This article relies largely or entirely on a single source. Relevant discussion may be found on the talk page. Please help improve this article by introducing citations to additional sources. Find sources: "Sexual anhedonia" – news · newspapers · books · scholar · JSTOR (April 2013) Sexual anhedonia, also know...
Sexual anhedonia
c0234019
7,181
wikipedia
https://en.wikipedia.org/wiki/Sexual_anhedonia
2021-01-18T18:28:27
{"umls": ["C0234019"], "icd-10": ["F52.0"], "wikidata": ["Q7458756"]}
A number sign (#) is used with this entry because of evidence that frontotemporal dementia and/or amyotrophic lateral sclerosis-4 (FTDALS4) is caused by heterozygous mutation in the TBK1 gene (604834) on chromosome 12q14. Description Frontotemporal dementia and/or amyotrophic lateral sclerosis-4 is an autosomal...
FRONTOTEMPORAL DEMENTIA AND/OR AMYOTROPHIC LATERAL SCLEROSIS 4
c3888102
7,182
omim
https://www.omim.org/entry/616439
2019-09-22T15:48:54
{"doid": ["0110069"], "mesh": ["C566288"], "omim": ["616439"], "orphanet": ["275872"]}
Enchondromatosis is a rare primary bone dysplasia disorder characterized by the development of multiple mainly unilateral or asymmetrically distributed enchondromas throughout the metaphyses of the long bones. *[v]: View this template *[t]: Discuss this template *[e]: Edit this template *[c.]: circa *[AA]:...
Ollier disease
c0014084
7,183
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=296
2021-01-23T18:12:48
{"gard": ["7251"], "mesh": ["D004687"], "omim": ["166000"], "umls": ["C0013366", "C0014084"], "icd-10": ["Q78.4"], "synonyms": ["Dyschondroplasia"]}
On the basis of a family in which 3 brothers and their maternal grandfather were affected, Middleton et al. (1975) concluded that an X-linked form may exist. None of 3 sisters was affected. See 193000. GU \- Vesicoureteral reflux Inheritance \- X-linked ▲ Close *[v]: View this template *[t]: Discuss this tem...
VESICOURETERAL REFLUX, X-LINKED
c1839114
7,184
omim
https://www.omim.org/entry/314550
2019-09-22T16:17:04
{"mesh": ["C564042"], "omim": ["314550"]}
Fissure of the nipple An irritated nipple, or jogger's nipple, acquired while riding a bike on a warm day. Fissure of the nipple, colloquially referred to as "jogger's nipple", is a condition that is the result of irritation of one or both nipples as the result of chafing, the friction of clothing against the ...
Fissure of the nipple
c0152453
7,185
wikipedia
https://en.wikipedia.org/wiki/Fissure_of_the_nipple
2021-01-18T18:28:44
{"umls": ["C0152453"], "icd-9": ["611.2"], "icd-10": ["N64.0", "O92.1"], "wikidata": ["Q5455245"]}
Cognitive and affective symptoms of cerebellum damage Cerebellar cognitive affective syndrome Other namesSchmahmann's syndrome SpecialtyNeurology Cerebellar cognitive affective syndrome (CCAS), also called Schmahmann's syndrome[1] is a condition that follows from lesions (damage) to the cerebellum of th...
Cerebellar cognitive affective syndrome
c2609040
7,186
wikipedia
https://en.wikipedia.org/wiki/Cerebellar_cognitive_affective_syndrome
2021-01-18T18:56:57
{"wikidata": ["Q2031371"]}
Congenital stenosis of vena cava Superior and inferior vena cava(on left) SpecialtyMedical genetics Congenital stenosis of vena cava is a congenital anomaly in which the superior vena cava or inferior vena cava has an aberrant interruption or coarctation. In some cases, it can be asymptomatic,[1] and in oth...
Congenital stenosis of vena cava
c0265927
7,187
wikipedia
https://en.wikipedia.org/wiki/Congenital_stenosis_of_vena_cava
2021-01-18T18:30:17
{"icd-9": ["747.49"], "icd-10": ["Q26.0"], "wikidata": ["Q5160451"]}
A number sign (#) is used with this entry because of evidence that congenital myasthenic syndrome-4C (CMS4C) associated with acetylcholine receptor (AChR) deficiency is caused by homozygous or compound heterozygous mutation in the CHRNE gene (100725) on chromosome 17p13. Mutation in the CHRNE gene can also cause...
MYASTHENIC SYNDROME, CONGENITAL, 4C, ASSOCIATED WITH ACETYLCHOLINE RECEPTOR DEFICIENCY
c0751882
7,188
omim
https://www.omim.org/entry/608931
2019-09-22T16:06:54
{"doid": ["0110679"], "mesh": ["D020294"], "omim": ["608931"], "orphanet": ["98913", "590"], "synonyms": ["MYASTHENIA, FAMILIAL INFANTILE, 1, FORMERLY", "CMS Id, FORMERLY", "Alternative titles", "MYASTHENIC SYNDROME, CONGENITAL, TYPE Id"], "genereviews": ["NBK1168"]}
Quadrantanopia Other namesQuadrant anopia Right homonymous superior quadrantanopia. The areas of the field lost in each eye are shown as black areas. This visual field defect is characteristic of damage to Meyer's loop on the left side of the brain. SpecialtyOphthalmology Quadrantanopia, quadrantanopsia, r...
Quadrantanopia
c0544680
7,189
wikipedia
https://en.wikipedia.org/wiki/Quadrantanopia
2021-01-18T18:45:08
{"mesh": ["D006423"], "icd-9": ["368.46"], "icd-10": ["H53.4"], "wikidata": ["Q2121869"]}
Body function in humans Vaginal flatulence is an emission or expulsion of air from the vagina. It may occur during or after sexual intercourse or during other sexual acts, stretching or exercise. The sound is somewhat comparable to flatulence from the anus, but does not involve waste gases, and thus often does n...
Vaginal flatulence
c1535974
7,190
wikipedia
https://en.wikipedia.org/wiki/Vaginal_flatulence
2021-01-18T19:05:31
{"wikidata": ["Q558165"]}
Perry syndrome is a progressive brain disease that is characterized by four major features: a pattern of movement abnormalities known as parkinsonism, psychiatric changes, weight loss, and abnormally slow breathing (hypoventilation). These signs and symptoms typically appear in a person's forties or fifties. Par...
Perry syndrome
c1868594
7,191
medlineplus
https://medlineplus.gov/genetics/condition/perry-syndrome/
2021-01-27T08:24:55
{"gard": ["10453"], "mesh": ["C566822"], "omim": ["168605"], "synonyms": []}
Isolated congenital megalocornea affects the cornea, the part of the eye that lets in light. The symptoms of isolated congenital megalocornea include mild nearsightedness, light sensitivity, and/or unusual vibration of the iris. At birth, the corneas are thin and enlarged. Cataracts may develop by 30-50 years of age....
Isolated congenital megalocornea
c0344530
7,192
gard
https://rarediseases.info.nih.gov/diseases/12648/isolated-congenital-megalocornea
2021-01-18T17:59:42
{"mesh": ["C562829"], "omim": ["309300"], "orphanet": ["91489"], "synonyms": ["Megalocornea", "MGCN", "MGC1", "Congenital anterior megalophthalmia"]}
A number sign (#) is used with this entry because of evidence that susceptibility to the development of acquired partial lipodystrophy (APLD) can be conferred in some cases by heterozygous mutation in the gene encoding the nuclear lamina protein lamin B2 (LMNB2; 150341) on chromosome 19p13. Description Acquired par...
LIPODYSTROPHY, PARTIAL, ACQUIRED, SUSCEPTIBILITY TO
c0220989
7,193
omim
https://www.omim.org/entry/608709
2019-09-22T16:07:21
{"mesh": ["C562448"], "omim": ["608709"], "orphanet": ["79087"], "synonyms": ["Alternative titles", "APLD, SUSCEPTIBILITY TO", "BARRAQUER-SIMONS SYNDROME", "LIPODYSTROPHY, CEPHALOTHORACIC TYPE", "LIPODYSTROPHY, PARTIAL, PROGRESSIVE"]}
A rare neuro-ophthalmological disease which is one of the most common forms of hereditary optic neuropathy characterized by progressive bilateral visual loss with an onset during the first decade of life, associated with optic disc pallor, visual acuity loss, visual field deficits and color vision defects. ## Epidem...
Autosomal dominant optic atrophy, classic form
c0338508
7,194
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=98673
2021-01-23T18:29:52
{"gard": ["9890"], "mesh": ["D029241"], "omim": ["165500", "605293", "610708"], "icd-10": ["H47.2"], "synonyms": ["Autosomal dominant optic atrophy, Kjer type", "Kjer optic atrophy", "Optic atrophy type 1"]}
Glomangiosarcoma SpecialtyDermatology Glomangiosarcoma is a low grade[1] tumor of the soft tissue. They rarely metastasize,[2] but metastases are possible.[3] It is also known as "malignant glomus tumor".[4] Positive staining for vimentin has been reported.[5] ## See also[edit] * angiosarcoma * Glomus tu...
Glomangiosarcoma
c1266111
7,195
wikipedia
https://en.wikipedia.org/wiki/Glomangiosarcoma
2021-01-18T18:31:47
{"umls": ["C1266111"], "wikidata": ["Q5571213"]}
medical condition in dogs Ununited anconeal process Elbow dysplasia is a condition involving multiple developmental abnormalities of the elbow-joint in the dog, specifically the growth of cartilage or the structures surrounding it. These abnormalities, known as 'primary lesions', give rise to osteoarthritic pro...
Elbow dysplasia
c3665589
7,196
wikipedia
https://en.wikipedia.org/wiki/Elbow_dysplasia
2021-01-18T18:52:00
{"wikidata": ["Q678183"]}
A rare, congenital, non-syndromic heart malformation characterized by a single fibrous annulus with two orifices opening into the left ventricle. Clinical presentation is variable and related to the degree of resulting mitral insufficiency and/or stenosis, and depending on the associated heart disease, most commonly ...
Double-orifice mitral valve
c0344770
7,197
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=95474
2021-01-23T17:53:56
{"umls": ["C0344770"], "icd-10": ["Q23.8"]}
Liver damage caused by a drug or chemical Hepatotoxicity Other namesToxic liver disease, toxin-induced liver disease, drug-induced liver disease, drug-induced liver damage, drug-induced liver injury, hepatogenous poisoning Drug-induced hepatitis with granulomata. Other causes were excluded with extensive investi...
Hepatotoxicity
c1262760
7,198
wikipedia
https://en.wikipedia.org/wiki/Hepatotoxicity
2021-01-18T18:46:18
{"mesh": ["D056486"], "wikidata": ["Q1349821"]}
Diogenes syndrome Other namesSenile squalor syndrome Room crammed with garbage SpecialtyPsychology, psychiatry Diogenes syndrome, also known as senile squalor syndrome, is a disorder characterized by extreme self-neglect, domestic squalor, social withdrawal, apathy, compulsive hoarding of garbage or animal...
Diogenes syndrome
c0424291
7,199
wikipedia
https://en.wikipedia.org/wiki/Diogenes_syndrome
2021-01-18T19:08:14
{"umls": ["C0424291"], "wikidata": ["Q1226826"]}