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Cervical spine disorder Cervical vertebrate Cervical spine disorders are illnesses that affect the cervical spine, which is made up of the upper first seven vertebrae, encasing and shielding the spinal cord. This fragment of the spine starts from the region above the shoulder blades and ends by supporting and ...
Cervical spine disorder
c1290145
8,300
wikipedia
https://en.wikipedia.org/wiki/Cervical_spine_disorder
2021-01-18T18:55:05
{"umls": ["C1290145"], "wikidata": ["Q5065358"]}
A cosmopolitan zoonotic disease caused in humans by the accidental ingestion of eggs or larvae of the ascarids Toxocara canis or Toxocara cati, the common round worm of dogs and cats respectively. The infestation can be asymptomatic or can present as visceral larva migrans caused by larval migration through major...
Toxocariasis
c0040553
8,301
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=3343
2021-01-23T17:29:01
{"mesh": ["D014120"], "umls": ["C0040553"], "icd-10": ["B83.0"]}
This article needs additional citations for verification. Please help improve this article by adding citations to reliable sources. Unsourced material may be challenged and removed. Find sources: "Allergic reactions to anesthesia" – news · newspapers · books · scholar · JSTOR (January 2009) (Learn how and when to r...
Allergic reactions to anesthesia
None
8,302
wikipedia
https://en.wikipedia.org/wiki/Allergic_reactions_to_anesthesia
2021-01-18T18:45:00
{"wikidata": ["Q4732120"]}
A number sign (#) is used with this entry because of evidence that autosomal recessive spinocerebellar ataxia-15 (SCAR15) is caused by homozygous mutation in the KIAA0226 gene (RUBCN; 613516) on chromosome 3q29. One such family has been reported. Clinical Features Assoum et al. (2010) reported a consanguineous ...
SPINOCEREBELLAR ATAXIA, AUTOSOMAL RECESSIVE 15
c3810326
8,303
omim
https://www.omim.org/entry/615705
2019-09-22T15:51:14
{"doid": ["0080057"], "omim": ["615705"], "orphanet": ["404499"], "synonyms": ["Salih ataxia", "SCAR15", "Autosomal recessive spinocerebellar ataxia type 15", "Alternative titles", "SALIH ATAXIA"]}
Rosselli–Gulienetti syndrome Other namesZlotogora–Ogur syndrome This condition is inherited in an autosomal recessive manner[1] Rosselli–Gulienetti syndrome,[2] also known as Zlotogora–Ogur syndrome[3] and Bowen–Armstrong syndrome,[4] is a type of congenital ectodermal dysplasia syndrome. The syndrome is rel...
Rosselli–Gulienetti syndrome
c0796139
8,304
wikipedia
https://en.wikipedia.org/wiki/Rosselli%E2%80%93Gulienetti_syndrome
2021-01-18T19:00:15
{"mesh": ["C563117"], "umls": ["C0796139"], "orphanet": ["90339"], "wikidata": ["Q7369769"]}
Food intolerances SpecialtyGastroenterology, immunology Food intolerance is a detrimental reaction, often delayed, to a food, beverage, food additive, or compound found in foods that produces symptoms in one or more body organs and systems, but generally refers to reactions other than food allergy. Food hy...
Food intolerance
c0149696
8,305
wikipedia
https://en.wikipedia.org/wiki/Food_intolerance
2021-01-18T18:45:10
{"mesh": ["D000073923"], "icd-9": ["V69.1"], "icd-10": ["K90.4", "Z71.3"], "wikidata": ["Q1727229"]}
A number sign (#) is used with this entry because of evidence that Seckel syndrome-8 (SCKL8) is caused by homozygous mutation in the DNA2 gene (601810) on chromosome 10q21. One such family has been reported. Description Seckel syndrome is a rare autosomal recessive disorder characterized by intrauterine growth reta...
SECKEL SYNDROME 8
c0265202
8,306
omim
https://www.omim.org/entry/615807
2019-09-22T15:51:03
{"doid": ["0070009"], "omim": ["615807"], "orphanet": ["808"]}
A number sign (#) is used with this entry because UV-sensitive syndrome-3 (UVSS3) can be caused by homozygous mutation in the UVSSA gene (614632) on chromosome 4p16. Description UV-sensitive syndrome-3 is an autosomal recessive disorder characterized by cutaneous photosensitivity and slight dyspigmentation, without...
UV-SENSITIVE SYNDROME 3
c1833561
8,307
omim
https://www.omim.org/entry/614640
2019-09-22T15:54:38
{"doid": ["0060240"], "mesh": ["C563466"], "omim": ["614640"], "orphanet": ["178338"]}
Torlontano et al. (1979) suggested that hereditary elliptocytosis (HE) falls into four categories: (1) HE without clinical hemolysis; (2) HE with hemolysis and sometimes anemia; (3) hereditary hemolytic ovalocytosis (166900); and (4) defective erythropoiesis and incomplete response to splenectomy. They studied 4 fami...
OVALOCYTOSIS, HEREDITARY HEMOLYTIC, WITH DEFECTIVE ERYTHROPOIESIS
c1833689
8,308
omim
https://www.omim.org/entry/166910
2019-09-22T16:36:49
{"mesh": ["C563479"], "omim": ["166910"]}
Poikiloderma with neutropenia (PN) is a disorder that mainly affects the skin and the immune system. This condition begins with a bumpy rash that usually appears between the ages of 6 and 12 months, gradually spreading from the arms and legs to the torso and face. At about age 2, the rash fades, and the affected chil...
Poikiloderma with neutropenia
c1858723
8,309
medlineplus
https://medlineplus.gov/genetics/condition/poikiloderma-with-neutropenia/
2021-01-27T08:25:14
{"gard": ["4085"], "mesh": ["C565820"], "omim": ["604173"], "synonyms": []}
Cytomegalovirus colitis Other namesCMV colitis Micrograph of CMV colitis. H&E stain. SpecialtyInfectious disease Cytomegalovirus colitis, also known as CMV colitis, is an inflammation of the colon. ## Contents * 1 Causes * 1.1 Risk factors * 2 Diagnosis * 3 Treatment * 4 See also * 5 Refere...
Cytomegalovirus colitis
c0341335
8,310
wikipedia
https://en.wikipedia.org/wiki/Cytomegalovirus_colitis
2021-01-18T18:56:05
{"wikidata": ["Q5201361"]}
Thymus hyperplasia Other namesThymic hyperplasia SpecialtyImmunology Thymus hyperplasia refers to an enlargement ("hyperplasia") of the thymus.[1] It is not always a disease state. The size of the thymus usually peaks during adolescence and atrophies in the following decades. Before the immune function ...
Thymus hyperplasia
c0040115
8,311
wikipedia
https://en.wikipedia.org/wiki/Thymus_hyperplasia
2021-01-18T18:46:04
{"mesh": ["D013952"], "umls": ["C0040115"], "icd-9": ["254.0"], "icd-10": ["E32.0"], "wikidata": ["Q7799652"]}
A number sign (#) is used with this entry because of evidence that craniofrontonasal syndrome (CFNS) is caused by mutation in the EFNB1 gene (300035) on chromosome Xq13. Description Craniofrontonasal syndrome is an X-linked developmental disorder that shows paradoxically greater severity in heterozygous females...
CRANIOFRONTONASAL SYNDROME
c0220767
8,312
omim
https://www.omim.org/entry/304110
2019-09-22T16:18:28
{"doid": ["14737"], "mesh": ["C536456"], "omim": ["304110"], "orphanet": ["1520"], "synonyms": ["Alternative titles", "CRANIOFRONTONASAL DYSPLASIA", "CRANIOFRONTONASAL DYSOSTOSIS"]}
Birth at less than a specified gestational age Preterm birth Other namesPremature birth, preemies, premmies Intubated preterm baby in an incubator SpecialtyNeonatology, Pediatrics, Obstetrics SymptomsBirth of a baby at younger than 37 weeks' gestational age[1] ComplicationsCerebral palsy, delays in develop...
Preterm birth
c0151526
8,313
wikipedia
https://en.wikipedia.org/wiki/Preterm_birth
2021-01-18T19:08:33
{"mesh": ["D047928"], "icd-9": ["765", "644"], "icd-10": ["O60.1"], "wikidata": ["Q625506"]}
Ogden syndrome Other namesPremature aging appearance-developmental delay-cardiac arrhythmia syndrome, N-terminal acetyltransferase deficiency Ogden Syndrome, also known as N-terminal acetyltransferase deficiency (NATD),[1] is an X-linked disorder of infancy comprising a distinct combination of distinctive ...
Ogden syndrome
c3275447
8,314
wikipedia
https://en.wikipedia.org/wiki/Ogden_syndrome
2021-01-18T18:46:36
{"umls": ["C3275447"], "orphanet": ["276432"], "wikidata": ["Q17144188"]}
Poisoning caused by mercury chemicals For the song by Graham Parker, see Mercury Poisoning. Mercury poisoning Other namesMercury toxicity, mercury overdose, mercury intoxication, hydrargyria, mercurialism The bulb of a mercury-in-glass thermometer SpecialtyToxicology SymptomsMuscle weakness, poor coordi...
Mercury poisoning
c0025427
8,315
wikipedia
https://en.wikipedia.org/wiki/Mercury_poisoning
2021-01-18T18:37:38
{"gard": ["7021"], "mesh": ["D008630"], "umls": ["C0025427"], "icd-9": ["985.0"], "icd-10": ["T56.1"], "orphanet": ["330021"], "wikidata": ["Q408089"]}
A rare, syndromic intellectual disability characterized by severe intellectual deficit, brachycephaly, plagiocephaly, and prominent forehead in male patients. Females may display moderate intellectual deficit without craniofacial dysmorphism. There have been no further descriptions in the literature since 1992. ...
X-linked intellectual disability-plagiocephaly syndrome
c2931516
8,316
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=2898
2021-01-23T17:23:56
{"gard": ["2765"], "mesh": ["C537512"], "omim": ["300064"], "umls": ["C2931516"], "icd-10": ["Q87.0"], "synonyms": ["Hyde Forster-McCarthy-Berry syndrome"]}
Patent ductus arteriosus - bicuspid aortic valve - hand anomalies syndrome is a very rare heart-hand syndrome (see this term) that is characterized by a variety of cardiovascular anomalies including patent arterial duct, bicuspid aortic valve and pseudocoarctation of the aorta in conjunction with hand anomalies such ...
Patent ductus arteriosus-bicuspid aortic valve-hand anomalies syndrome
c1858420
8,317
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=228190
2021-01-23T17:22:46
{"mesh": ["C565782"], "omim": ["604381"], "umls": ["C1858420"], "icd-10": ["Q87.2"], "synonyms": ["Patent arterial duct-bicuspid aortic valve-hand anomalies syndrome"]}
A number sign (#) is used with this entry because selective complement component C1s deficiency can be caused by homozygous mutation in the C1S gene (120580) on chromosome 12p13. Clinical Features Inoue et al. (1998) reported a patient with a systemic lupus erythematosus-like syndrome and chronic glomerulonephritis...
COMPLEMENT COMPONENT C1s DEFICIENCY
c3151078
8,318
omim
https://www.omim.org/entry/613783
2019-09-22T15:57:32
{"mesh": ["C565170"], "omim": ["613783"], "orphanet": ["169147"], "synonyms": ["Immunodeficiency due to C1, C4, or C2 component complement deficiency", "Alternative titles", "Immunodeficiency due to an early component of complement deficiency", "C1s DEFICIENCY"]}
A number sign (#) is used with this entry because of evidence that Shukla-Vernon syndrome (SHUVER) is caused by hemizygous mutation in the BCORL1 gene (300688) on chromosome Xq25. Description Shukla-Vernon syndrome (SHUVER) is an X-linked recessive neurodevelopmental disorder characterized by global developmental d...
SHUKLA-VERNON SYNDROME
None
8,319
omim
https://www.omim.org/entry/301029
2019-09-22T16:18:52
{"omim": ["301029"]}
Fear or disgust of objects with irregular patterns of holes or bumps The holes in lotus seedheads elicit feelings of discomfort or repulsion in some people.[1][2] Trypophobia is an aversion to the sight of irregular patterns or clusters of small holes or bumps.[3][4] It is not officially recognized as a mental diso...
Trypophobia
None
8,320
wikipedia
https://en.wikipedia.org/wiki/Trypophobia
2021-01-18T18:51:16
{"wikidata": ["Q560107"]}
A number sign (#) is used with this entry because of evidence that retinitis pigmentosa-55 (RP55) is caused by homozygous mutation in the ARL6 gene (608845) on chromosome 3q11. One such family has been reported. Mutation in the ARL6 gene can also cause a form of Bardet-Biedl syndrome (BBS3; see 209900), in which...
RETINITIS PIGMENTOSA 55
c0035334
8,321
omim
https://www.omim.org/entry/613575
2019-09-22T15:58:16
{"doid": ["0110370"], "mesh": ["D012174"], "omim": ["613575"], "orphanet": ["791"], "genereviews": ["NBK1417"]}
In medicine, a stinger,[1][2] also called a burner or nerve pinch injury, is a neurological injury suffered by athletes, mostly in high-contact sports such as ice hockey, rugby, American football, and wrestling. The spine injury is characterized by a shooting or stinging pain that travels down one arm, followed by nu...
Stinger (medicine)
None
8,322
wikipedia
https://en.wikipedia.org/wiki/Stinger_(medicine)
2021-01-18T18:55:05
{"icd-10": ["S14.3"], "wikidata": ["Q7617424"]}
A number sign (#) is used with this entry because of evidence that microvillus inclusion disease is caused by homozygous or compound heterozygous mutation in the MYO5B (606540) gene on chromosome 18q21. Description Microvillus inclusion disease (MVID) is characterized by onset of intractable life-threatening watery...
DIARRHEA 2, WITH MICROVILLUS ATROPHY
c0341306
8,323
omim
https://www.omim.org/entry/251850
2019-09-22T16:25:12
{"doid": ["0060775"], "mesh": ["C537470"], "omim": ["251850"], "orphanet": ["2290"], "synonyms": ["Alternative titles", "MICROVILLUS INCLUSION DISEASE", "MICROVILLUS ATROPHY, CONGENITAL", "DAVIDSON DISEASE", "CONGENITAL FAMILIAL PROTRACTED DIARRHEA WITH ENTEROCYTE BRUSH-BORDER ABNORMALITIES", "INTRACTABLE DIARRHEA OF I...
Spinocerebellar ataxia type 1 (SCA1) is a subtype of type I autosomal dominant cerebellar ataxia (ADCA type I; see this term) characterized by dysarthria, writing difficulties, limb ataxia, and commonly nystagmus and saccadic abnormalities. ## Epidemiology Prevalence is estimated to be 1-2 in 100,000 with significa...
Spinocerebellar ataxia type 1
c0752120
8,324
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=98755
2021-01-23T17:31:54
{"gard": ["4071"], "mesh": ["D020754"], "omim": ["164400"], "umls": ["C0752120"], "icd-10": ["G11.8"], "synonyms": ["SCA1"]}
A number sign (#) is used with this entry because of evidence that autosomal dominant spastic paraplegia-73 (SPG73) is caused by heterozygous mutation in the CPT1C gene (608846) on chromosome 19q13. One such family has been reported. For a general phenotypic description and a discussion of genetic heterogeneity of a...
SPASTIC PARAPLEGIA 73, AUTOSOMAL DOMINANT
c4225387
8,325
omim
https://www.omim.org/entry/616282
2019-09-22T15:49:25
{"doid": ["0110818"], "omim": ["616282"], "orphanet": ["444099"], "synonyms": ["SPG73"]}
This article needs to be updated. Please update this article to reflect recent events or newly available information. (March 2019) Primary immunodeficiencies are disorders in which part of the body's immune system is missing or does not function normally. To be considered a primary immunodeficiency (PID), the ca...
Primary immunodeficiency
c0021051
8,326
wikipedia
https://en.wikipedia.org/wiki/Primary_immunodeficiency
2021-01-18T18:28:15
{"mesh": ["D007153", "D000081207"], "umls": ["C0021051"], "orphanet": ["101997"], "wikidata": ["Q3043160"]}
Familial adenomatous polyposis (FAP) is characterized by the development of hundreds to thousands of adenomas in the rectum and colon during the second decade of life. ## Epidemiology FAP has a birth incidence of about 1/8,300, manifests equally in both sexes, and accounts for less than 1% of colorectal cancer ...
Familial adenomatous polyposis
c0032580
8,327
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=733
2021-01-23T19:05:07
{"gard": ["6408"], "mesh": ["D011125"], "omim": ["175100"], "umls": ["C0032580"], "icd-10": ["D12.6"], "synonyms": ["Colorectal adenomatous polyposis", "FAP", "Familial polyposis coli"]}
Mitochondrial DNA depletion syndrome, hepatocerebrorenal form is a rare, genetic, mitochondrial DNA depletion syndrome characterized by neonatal or early-infantile onset hepatopathy (manifesting with hepatomegaly, cholestasis, increased transaminases, coagulopathy, hypoalbuminemia, ascites, and/or liver failure), ass...
Mitochondrial DNA depletion syndrome, hepatocerebrorenal form
c1849096
8,328
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=363534
2021-01-23T17:19:13
{"mesh": ["C535523"], "omim": ["271245"], "icd-10": ["E88.8"], "synonyms": ["mtDNA depletion syndrome, hepatocerebrorenal form"]}
Foster Kennedy syndrome Other namesGowers–Paton–Kennedy syndrome, Kennedy's phenomenon, Kennedy's syndrome Frontal lobe (on the right) SpecialtyNeurology Foster Kennedy syndrome is a constellation of findings associated with tumors of the frontal lobe.[1] Although Foster Kennedy syndrome is sometimes call...
Foster Kennedy syndrome
c0152112
8,329
wikipedia
https://en.wikipedia.org/wiki/Foster_Kennedy_syndrome
2021-01-18T18:54:43
{"mesh": ["D009901"], "umls": ["C0152112"], "wikidata": ["Q751261"]}
A number sign (#) is used with this entry because it represents a contiguous gene deletion syndrome on chromosome 6q. Description The cardinal features of chromosome 6q11-q14 interstitial deletions include hypotonia, short stature, skeletal/limb anomalies, umbilical hernia, and urinary tract anomalies, as well ...
CHROMOSOME 6q11-q14 DELETION SYNDROME
c3150790
8,330
omim
https://www.omim.org/entry/613544
2019-09-22T15:58:20
{"omim": ["613544"]}
A number sign (#) is used with this entry because of evidence that fast-channel congenital myasthenic syndrome-3B (CMS3B) is caused by homozygous or compound heterozygous mutation in the CHRND gene (100720) on chromosome 2q37. Mutation in the CHRND gene can also cause slow-channel congenital myasthenic syndrome (CMS...
MYASTHENIC SYNDROME, CONGENITAL, 3B, FAST-CHANNEL
c0751882
8,331
omim
https://www.omim.org/entry/616322
2019-09-22T15:49:13
{"doid": ["0110665"], "mesh": ["D020294"], "omim": ["616322"], "orphanet": ["98913", "590"], "synonyms": [], "genereviews": ["NBK1168"]}
Mastocytosis Other namesClonal bone marrow disorder Micrograph of mastocytosis. Skin biopsy. H&E stain. SpecialtyOncology, allergology, hematology Mastocytosis, a type of mast cell disease, is a rare disorder affecting both children and adults caused by the accumulation of functionally defective mast cells...
Mastocytosis
c0024899
8,332
wikipedia
https://en.wikipedia.org/wiki/Mastocytosis
2021-01-18T18:55:03
{"gard": ["6987"], "mesh": ["D008415"], "umls": ["C0024899"], "icd-9": ["202.6", "757.33"], "orphanet": ["98292"], "wikidata": ["Q112670"]}
High myopia-sensorineural deafness syndrome is a rare genetic disease characterized by high myopia, typically ranging from -6.0 to -11.0 diopters, and moderate to profound, bilateral, progressive sensorineural hearing loss with prelingual-onset. Affected individuals do not present other systemic, ocular or connec...
High myopia-sensorineural deafness syndrome
c3806275
8,333
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=363396
2021-01-23T17:40:27
{"gard": ["12844"], "omim": ["221200"], "icd-10": ["H90.5"], "synonyms": ["High myopia-sensorineural hearing loss syndrome"]}
Congenital autosomal recessive sideroblastic anemia (ARSA) is a non-syndromic, microcytic/hypochromic sideroblastic anemia, present from early infancy and characterized by severe microcytic anemia, which is not pyridoxine responsive, and increased serum ferritin. ## Epidemiology To date, fewer than 30 unrelated gen...
Autosomal recessive sideroblastic anemia
c4225428
8,334
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=260305
2021-01-23T17:18:15
{"omim": ["182170", "205950"], "icd-10": ["D64.0"], "synonyms": ["ARSA", "Congenital sideroblastic anemia"]}
Dobrow syndrome is a rare multiple congenital defects/dysmorphic syndrome characterized by variable degrees of bony syngnathia associated with variable additional abnormalities, including growth retardation, intellectual disability, microcephaly, iris coloboma, nystagmus, deafness, and vertebral segmentation defects,...
Dobrow syndrome
None
8,335
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=3262
2021-01-23T17:58:17
{"gard": ["5092"], "synonyms": ["Syngnathia-multiple anomalies syndrome"]}
A number sign (#) is used with this entry because myoclonic epilepsy of Unverricht and Lundborg (ULD), also known as progressive myoclonic epilepsy-1A (EPM1A), is caused by mutation in the cystatin B gene (CSTB; 601145) on chromosome 21q22. Description Myoclonic epilepsy of Unverricht and Lundborg is an autosomal r...
MYOCLONIC EPILEPSY OF UNVERRICHT AND LUNDBORG
c0751785
8,336
omim
https://www.omim.org/entry/254800
2019-09-22T16:24:39
{"doid": ["3535"], "mesh": ["D020194"], "omim": ["254800"], "orphanet": ["308"], "synonyms": ["Alternative titles", "ULD", "EPILEPSY, PROGRESSIVE MYOCLONIC, 1A", "EPILEPSY, PROGRESSIVE MYOCLONIC, 1", "PROGRESSIVE MYOCLONIC EPILEPSY", "BALTIC MYOCLONIC EPILEPSY"], "genereviews": ["NBK1142"]}
natural fear typical of most mammals For other uses, see Fear of falling (disambiguation). 530 feet above the streets of Calgary The fear of falling (FOF), also referred to as basophobia (or basiphobia), is a natural fear and is typical of most humans and mammals, in varying degrees of extremity. It differs from a...
Fear of falling
c0877040
8,337
wikipedia
https://en.wikipedia.org/wiki/Fear_of_falling
2021-01-18T18:36:08
{"umls": ["C0877040"], "wikidata": ["Q5439393"]}
Florida keratopathy, also known as Florida spots, is an eye condition characterized by the presence of multiple spots within both corneas.[1] It is most commonly seen in dogs and cats, but is also rarely seen in horses and birds.[2] The disease is found in the southeastern parts of the United States.[2] In other part...
Florida keratopathy
c4523781
8,338
wikipedia
https://en.wikipedia.org/wiki/Florida_keratopathy
2021-01-18T18:36:04
{"wikidata": ["Q3201122"]}
Heart-hand syndrome refers to a group of congenital disorders characterized by malformations of the upper limbs and heart. To date, heart-hand syndrome comprises the following rare syndromes; Holt-Oram syndrome; heart-hand syndrome type 2; heart-hand syndrome type 3; heart hand syndrome, Slovenian type, brachydactyly...
Heart-hand syndrome
c0265264
8,339
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=228184
2021-01-23T18:24:29
{"mesh": ["C535326"], "umls": ["C0265264"], "icd-10": ["Q87.2"], "synonyms": ["Atriodigital dysplasia"]}
A number sign (#) is used with this entry because of evidence that leukoencephalopathy with ataxia (LKPAT) is caused by homozygous or compound heterozygous mutation in the CLCN2 gene (600570) on chromosome 3q27. Description Leukoencephalopathy with ataxia is an autosomal recessive neurologic disorder with a charact...
LEUKOENCEPHALOPATHY WITH ATAXIA
c3810242
8,340
omim
https://www.omim.org/entry/615651
2019-09-22T15:51:21
{"omim": ["615651"], "orphanet": ["363540"], "synonyms": [], "genereviews": ["NBK326661"]}
A number sign (#) is used with this entry because of evidence that premature ovarian failure-10 (POF10) is caused by homozygous mutation in the MCM8 gene (608187) on chromosome 20p. Description Premature ovarian failure-10 (POF10) represents a syndrome characterized by primary amenorrhea, hypergonadotropic ovarian ...
PREMATURE OVARIAN FAILURE 10
c2752067
8,341
omim
https://www.omim.org/entry/612885
2019-09-22T16:00:24
{"omim": ["612885"]}
A number sign (#) is used with this entry because Farber lipogranulomatosis (FRBRL) is caused by homozygous or compound heterozygous mutation in the gene encoding acid ceramidase (ASAH1; 613468) on chromosome 8p. Description Farber lipogranulomatosis is an autosomal recessive lysosomal storage disorder characterize...
FARBER LIPOGRANULOMATOSIS
c0268255
8,342
omim
https://www.omim.org/entry/228000
2019-09-22T16:27:57
{"doid": ["0050464"], "mesh": ["D055577"], "omim": ["228000"], "orphanet": ["333"], "synonyms": ["Alternative titles", "FARBER DISEASE", "CERAMIDASE DEFICIENCY", "ACID CERAMIDASE DEFICIENCY", "AC DEFICIENCY", "N-LAURYLSPHINGOSINE DEACYLASE DEFICIENCY"], "genereviews": ["NBK488189"]}
Lysinuric protein intolerance is a disorder caused by the body's inability to digest and use certain protein building blocks (amino acids), namely lysine, arginine, and ornithine. Because the body cannot effectively break down these amino acids, which are found in many protein-rich foods, nausea and vomiting are typi...
Lysinuric protein intolerance
c0268647
8,343
medlineplus
https://medlineplus.gov/genetics/condition/lysinuric-protein-intolerance/
2021-01-27T08:24:45
{"gard": ["3335"], "mesh": ["C562687"], "omim": ["222700"], "synonyms": []}
Not to be confused with Allergies to cats. See also: Cat health § Food allergy A cat showing extreme signs of pruritus. Cats exposed to allergens may develop allergies or allergic reactions. Allergies tend to become evident and intensify over extended periods of time and can take years to develop.[1] Some allergic...
Allergies in cats
None
8,344
wikipedia
https://en.wikipedia.org/wiki/Allergies_in_cats
2021-01-18T18:57:44
{"wikidata": ["Q48801082"]}
Mitochondrial membrane protein-associated neurodegeneration (MPAN) is a disorder of the nervous system. The condition typically begins in childhood or early adulthood and worsens (progresses) over time. MPAN commonly begins with difficulty walking. As the condition progresses, affected individuals usually develop ot...
Mitochondrial membrane protein-associated neurodegeneration
c3280371
8,345
medlineplus
https://medlineplus.gov/genetics/condition/mitochondrial-membrane-protein-associated-neurodegeneration/
2021-01-27T08:25:08
{"gard": ["12569"], "omim": ["614298"], "synonyms": []}
Amobarbital normally undergoes two hydroxylations, leading to 3-prime-hydroxyamobarbital (C-OH) and N-hydroxyamobarbital (N-OH). Kalow et al. (1977) described a kindred in which 2 mothers who were identical twins showed a gross deficiency of N-OH in the urine. Family data suggested that the twins were homozygous for ...
AMOBARBITAL, DEFICIENT N-HYDROXYLATION OF
c1859816
8,346
omim
https://www.omim.org/entry/204800
2019-09-22T16:31:08
{"mesh": ["C565959"], "omim": ["204800"]}
This condition must be distinguished from myotonia congenita and from the Debre-Semelaigne syndrome of congenital hypothyroidism. Poch et al. (1971) described a well-documented family with male-to-male transmission. Striking hypertrophy of the calf muscles and less constantly of the masseter muscles was found. Mu...
HYPERTROPHIA MUSCULORUM VERA
c1840361
8,347
omim
https://www.omim.org/entry/145800
2019-09-22T16:39:46
{"mesh": ["C564152"], "omim": ["145800"]}
Degloving A Morel-Lavallée lesion is a closed traumatic soft-tissue degloving injury, caused by separation of the hypodermis from the underlying fascia.[1] It most frequently occurs in the peritrochanteric region along the proximal lateral thigh,[1] such as in this CT scan. A degloving injury is a type of avul...
Degloving
c0433122
8,348
wikipedia
https://en.wikipedia.org/wiki/Degloving
2021-01-18T19:03:11
{"mesh": ["D000069836"], "umls": ["C0433122"], "wikidata": ["Q786854"]}
Variant Creutzfeldt-Jakob disease (vCJD) is a type of Creutzfeldt-Jakob disease (CJD) characterized by early psychiatric symptoms and cognitive decline. All forms of CJD belong to a rare family of progressive neurodegenerative disorders that affect both humans and animals, called prion diseases. The term "prion" ...
Variant Creutzfeldt-Jakob disease
c0376329
8,349
gard
https://rarediseases.info.nih.gov/diseases/9550/variant-creutzfeldt-jakob-disease
2021-01-18T17:57:11
{"mesh": ["D007562"], "umls": ["C0376329"], "synonyms": ["Variant Creutzfeldt-Jacob disease", "VCJD", "Variant CJD", "New variant of CJD", "Nv-CJD"]}
A rare disorder of plasmalogen biosynthesis characterized by syndromic severe intellectual disability with congenital cataracts, early-onset epilepsy, microcephaly, global developmental delay, growth retardation and short stature, and spastic quadriparesis. Dysmorphic facial features may be present, including high-ar...
Fatty acyl-CoA reductase 1 deficiency
c4015344
8,350
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=438178
2021-01-23T18:39:16
{"omim": ["616154"], "icd-10": ["E71.3"], "synonyms": ["FAR1 deficiency", "PFCRD", "Peroxisomal fatty acyl-CoA reductase 1 disorder"]}
Pacman dysplasia Other namesEpiphyseal stippling with osteoclastic hyperplasia Pacman dysplasia is inherited in an autosomal recessive manner Pacman dysplasia is a lethal autosomal recessive skeletal dysplasia. The dysplasia is present during fetal development.[1] ## References[edit] 1. ^ http://www.omim...
Pacman dysplasia
c1833676
8,351
wikipedia
https://en.wikipedia.org/wiki/Pacman_dysplasia
2021-01-18T19:04:12
{"gard": ["4189"], "mesh": ["C538095"], "umls": ["C1833676"], "orphanet": ["1952"], "wikidata": ["Q7123066"]}
Manganese poisoning Manganism SpecialtyOccupational medicine Manganism or manganese poisoning is a toxic condition resulting from chronic exposure to manganese.[1] It was first identified in 1837 by James Couper.[2] ## Contents * 1 Signs and symptoms * 2 Causes * 3 Pathophysiology * 4 Diagnosis ...
Manganism
c0677050
8,352
wikipedia
https://en.wikipedia.org/wiki/Manganism
2021-01-18T18:39:50
{"mesh": ["D020149"], "umls": ["C0677050"], "icd-9": ["985.2"], "icd-10": ["T57.2"], "orphanet": ["306682"], "wikidata": ["Q2480013"]}
A number sign (#) is used with this entry because of evidence that central precocious puberty-2 (CPPB2) is caused by heterozygous mutation on the paternal allele of the MKRN3 gene (603856) on chromosome 15q11. Description Early activation of the hypothalamic-pituitary-gonadal axis results in gonadotropin-depend...
PRECOCIOUS PUBERTY, CENTRAL, 2
c0342543
8,353
omim
https://www.omim.org/entry/615346
2019-09-22T15:52:29
{"mesh": ["D011629"], "omim": ["615346"], "orphanet": ["759"]}
Benign hyperplasia of fibrous connective tissue Epulis fissuratum Other namesInflammatory fibrous hyperplasia,[1] Denture-induced fibrous inflammatory hyperplasia,[2] Denture injury tumor,[1] Denture epulis,[1] Denture induced granuloma,[3] and Granuloma fissuratum[4]:808) Epulis fissuratum is a benign hyperp...
Epulis fissuratum
c0399495
8,354
wikipedia
https://en.wikipedia.org/wiki/Epulis_fissuratum
2021-01-18T18:43:14
{"umls": ["C0399495"], "wikidata": ["Q5384044"]}
Prevalence of HIV/AIDS in Africa, total (% of population ages 15–49), in 2011 (World Bank) over 15% 5-15% 2-5% 1-2% 0.5-1% 0.1-0.5% not available HIV/AIDS originated in Africa in the early 20th century and is a major public health concern and cause of death in many African countries. AIDS rates vary d...
HIV/AIDS in Africa
None
8,355
wikipedia
https://en.wikipedia.org/wiki/HIV/AIDS_in_Africa
2021-01-18T19:02:58
{"wikidata": ["Q1358589"]}
A very rare form of botulism, a rare acquired neuromuscular junction disease with descending flaccid paralysis caused by botulinum neurotoxins (BoNTs), and is due to intestinal colonization by Clostridium botulinum leading to toxin-mediated infection with toxemia. ## Epidemiology Exact prevalence is unknown. To...
Adult intestinal botulism
c4289991
8,356
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=178487
2021-01-23T18:16:50
{"icd-10": ["A05.1"], "synonyms": ["Adult intestinal colonization botulism", "Adult intestinal toxemia botulism", "Adult intestinal toxin-mediated botulism", "Infant-like botulism"]}
A number sign (#) is used with this entry because of evidence that hypomyelinating leukodystrophy-8 (HLD8) is caused by compound heterozygous mutation in the POLR3B gene (614366) on chromosome 12q23. Description Hypomyelinating leukodystrophy-8 is an autosomal recessive neurologic disorder characterized by early ch...
LEUKODYSTROPHY, HYPOMYELINATING, 8, WITH OR WITHOUT OLIGODONTIA AND/OR HYPOGONADOTROPIC HYPOGONADISM
c2676243
8,357
omim
https://www.omim.org/entry/614381
2019-09-22T15:55:27
{"doid": ["0060797"], "mesh": ["C567313"], "omim": ["614381"], "orphanet": ["88637"], "genereviews": ["NBK99167", "NBK1334"]}
PIK3CA-related overgrowth spectrum (PROS) is a group of rare disorders that cause overgrowth of parts of the body, due to mutations in the PIK3CA gene. Specific disorders in this spectrum include: * Fibroadipose hyperplasia (also called fibroadipose overgrowth) * CLOVES syndrome * Megalencephaly-capillary ma...
PIK3CA-related overgrowth spectrum
None
8,358
gard
https://rarediseases.info.nih.gov/diseases/12182/pik3ca-related-overgrowth-spectrum
2021-01-18T17:58:19
{"synonyms": ["PIK3CA-associated segmental overgrowth"]}
Good syndrome is a rare, adult-onset primary immunodeficiency suspected in patients who exhibit hypogammaglobulinemia and low levels of B cells along with a benign thymic tumor (thymoma) on chest X-ray. Symptoms include frequent opportunistic infections involving the sinuses and lungs, including severe CMV disease, P...
Immunodeficiency with thymoma
c0221027
8,359
gard
https://rarediseases.info.nih.gov/diseases/8622/immunodeficiency-with-thymoma
2021-01-18T17:59:49
{"umls": ["C0221027"], "orphanet": ["169105"], "synonyms": ["Thymoma-immunodeficiency syndrome", "Good syndrome"]}
A number sign (#) is used with this entry because of evidence that early infantile epileptic encephalopathy-39 (EIEE39) is caused by homozygous mutation in the SLC25A12 gene (603667) on chromosome 2q31. For a general phenotypic description and a discussion of genetic heterogeneity of EIEE, see EIEE1 (308350). Clini...
EPILEPTIC ENCEPHALOPATHY, EARLY INFANTILE, 39
c2751855
8,360
omim
https://www.omim.org/entry/612949
2019-09-22T16:00:12
{"doid": ["0080349"], "mesh": ["C567847"], "omim": ["612949"], "orphanet": ["353217"], "synonyms": ["AGC1 deficiency", "HYPOMYELINATION, GLOBAL CEREBRAL", "ASPARTATE-GLUTAMATE CARRIER 1 DEFICIENCY", "Alternative titles", "Mitochondrial aspartate-glutamate carrier 1 deficiency", "AGC1 DEFICIENCY"]}
Goblet cell carcinoid (GCC) is a rare tumor normally occurring in the appendix which displays features of both a neuroendocrine tumor and a more aggressive form of cancer known as an adenocarcinoma. It is usually diagnosed in people over the age of 50. People with this tumor may develop acute appendicitis, abdominal ...
Goblet cell carcinoid
c0205695
8,361
gard
https://rarediseases.info.nih.gov/diseases/10414/goblet-cell-carcinoid
2021-01-18T18:00:14
{"mesh": ["D002276"], "orphanet": ["329984"], "synonyms": ["Goblet cell carcinoma", "Mucinous carcinoid", "GCC", "Goblet cell adenocarcinoid", "Goblet cell tumor"]}
A rare urogenital disease characterized by otherwise unexplained chronic urinary retention of more than 1 liter of sterile urine on catheterization, an asensitive bladder with loss of urge to void, and no help of straining. Poor tolerance of self-catheterization is typically reported. The condition occurs in women be...
Fowler urethral sphincter dysfunction syndrome
c2931462
8,362
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=2795
2021-01-23T18:04:49
{"gard": ["2365"], "mesh": ["C537271"], "umls": ["C2931462"], "synonyms": ["Fowler syndrome", "Fowler-Christmas-Chapple syndrome"]}
An extremely rare developmental defect during embryogenesis malformation syndrome characterized by bands of extensile tissue connecting the margins of the upper and lower eyelids, in association with anal atresia. Patients may additionally present cleft palate, hydrocephalus and meningomyelocele. There have been no f...
Ankyloblepharon filiforme adnatum-imperforate anus syndrome
None
8,363
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=1074
2021-01-23T17:33:07
{"gard": ["697"], "icd-10": ["Q87.8"], "synonyms": ["Aughton-Hufnagle syndrome"]}
Not to be confused with Ectropion. Cervical Ectropion Other namesCervical eversion Cervical ectropion SpecialtyGynecology Cervical ectropion is a condition in which the cells from the 'inside' of the cervical canal, known as glandular cells (or columnar epithelium), are present on the 'outside' of the vag...
Cervical ectropion
c0269189
8,364
wikipedia
https://en.wikipedia.org/wiki/Cervical_ectropion
2021-01-18T18:40:02
{"mesh": ["D002579"], "umls": ["C0269189", "C0007869"], "icd-10": ["N86"], "wikidata": ["Q720523"]}
Stratton-Parker Syndrome Other namesMullerian aplasia with hypoplastic thumbs SpecialtyOrthopedic Michels Caskey syndrome is a rare disorder that combines spinal and skeletal abnormalities, especially of the thumbs, with abnormal or absent female reproductive organs. Examples include the absence of a cer...
Michels Caskey syndrome
c2931537
8,365
wikipedia
https://en.wikipedia.org/wiki/Michels_Caskey_syndrome
2021-01-18T18:33:25
{"gard": ["3590"], "mesh": ["C537576"], "umls": ["C2931537"], "icd-9": [], "icd-10": [], "wikidata": ["Q6837318"]}
L-Arginine:glycine amidinotransferase (AGAT) deficiency is a very rare type of creatine deficiency sydrome characterized by global developmental delay, intellectual disability, and myopathy. ## Epidemiology Less than 20 patients have been described with AGAT deficiency to date. ## Clinical description AGAT de...
L-Arginine:glycine amidinotransferase deficiency
c2675179
8,366
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=35704
2021-01-23T18:20:02
{"gard": ["10323"], "mesh": ["C567192"], "omim": ["612718"], "umls": ["C2675179"], "icd-10": ["E72.8"], "synonyms": ["AGAT deficiency"]}
Macrozoospermia is a condition that affects only males. It is characterized by abnormal sperm and leads to an inability to father biological children (infertility). In affected males, almost all sperm cells have abnormally large and misshapen heads. The head of the sperm cell contains the male's genetic information ...
Macrozoospermia
c0403812
8,367
medlineplus
https://medlineplus.gov/genetics/condition/macrozoospermia/
2021-01-27T08:25:09
{"gard": ["12385"], "mesh": ["C562903"], "omim": ["243060"], "synonyms": []}
A number sign (#) is used with this entry because Bloom syndrome (BLM), also referred to here as microcephaly, growth restriction, and increased sister chromatid exchange-1 (MGRISCE1), is caused by homozygous or compound heterozygous mutation in the gene encoding DNA helicase RecQ protein-like-3 (RECQL3; 604610) on c...
BLOOM SYNDROME
c0005859
8,368
omim
https://www.omim.org/entry/210900
2019-09-22T16:30:22
{"doid": ["2717"], "mesh": ["D001816"], "omim": ["210900"], "orphanet": ["125"], "synonyms": ["Alternative titles", "BS", "MICROCEPHALY, GROWTH RESTRICTION, AND INCREASED SISTER CHROMATID EXCHANGE 1"], "genereviews": ["NBK1294", "NBK1398"]}
A number sign (#) is used with this entry because of evidence that Heimler syndrome-1 (HMLR1) is caused by homozygous or compound heterozygous mutations in the PEX1 gene (602136) on chromosome 7q21. Description Heimler syndrome-1 (HMLR1), which represents the mildest end of the peroxisomal biogenesis disorder spect...
HEIMLER SYNDROME 1
c1856186
8,369
omim
https://www.omim.org/entry/234580
2019-09-22T16:27:22
{"mesh": ["C535994"], "omim": ["234580"], "orphanet": ["3220"], "synonyms": ["Alternative titles", "HEARING LOSS, SENSORINEURAL, WITH ENAMEL HYPOPLASIA AND NAIL DEFECTS", "PEROXISOME BIOGENESIS DISORDER 1C"]}
A number sign (#) is used with this entry because of evidence that familial adenomatous polyposis-4 (FAP4) is caused by compound heterozygous mutation in the MSH3 gene (600887) on chromosome 5q11. Description Familial adenomatous polyposis-4 is an autosomal recessive tumor predisposition syndrome characterized by t...
FAMILIAL ADENOMATOUS POLYPOSIS 4
c4310719
8,370
omim
https://www.omim.org/entry/617100
2019-09-22T15:46:55
{"doid": ["0080412"], "omim": ["617100"], "orphanet": ["480536"], "synonyms": ["MSH3-related AFAP", "MSH3-related attenuated FAP", "MSH3-related attenuated familial polyposis coli"]}
Hyper IgM syndrome is a type of primary immunodeficiency syndrome. Primary immunodeficiency occurs when part of a person’s immune system is missing or does not work correctly. The bodies of people with primary immunodeficiency can’t get rid of germs or protect themselves from new germs as well as they should. Primary...
Immunodeficiency with hyper IgM type 1
c0398689
8,371
gard
https://rarediseases.info.nih.gov/diseases/73/immunodeficiency-with-hyper-igm-type-1
2021-01-18T17:59:49
{"mesh": ["D053307"], "omim": ["308230", "605258", "606843", "608106", "608184"], "orphanet": ["101088"], "synonyms": ["X-linked hyper IgM syndrome", "Hyper IgM immunodeficiency, x-linked", "Hyper IgM syndrome", "Hyper IgM syndrome 1", "XHIM", "HIGM", "IHIS", "HIGM1"]}
For the medical journal, see Childhood Obesity (journal). Childhood obesity Children with varying degrees of body fat SpecialtyEndocrinology, pediatrics, bariatrics Part of a series on Human body weight General concepts * Obesity (Epidemiology) * Overweight * Underweight * Body shape * Weight...
Childhood obesity
c2362324
8,372
wikipedia
https://en.wikipedia.org/wiki/Childhood_obesity
2021-01-18T18:51:39
{"mesh": ["D063766"], "icd-9": ["278"], "icd-10": ["E66"], "wikidata": ["Q3241451"]}
Type of hemorrhage Cephalhematoma Other namesCephalhematoma Newborn scalp haematomata SpecialtyPediatrics A cephalohaematoma is a hemorrhage of blood between the skull and the periosteum of any age human, including a newborn baby secondary to rupture of blood vessels crossing the periosteum. Because t...
Cephalohematoma
c0007722
8,373
wikipedia
https://en.wikipedia.org/wiki/Cephalohematoma
2021-01-18T18:48:48
{"umls": ["C0007722"], "icd-9": ["767.19"], "icd-10": ["P12"], "wikidata": ["Q419938"]}
Chronic intestinal pseudo-obstruction (CIPO) is a rare disease characterized by repetitive episodes or continuous symptoms of bowel obstruction when no blockage exists. Problems with nerves, muscles, or interstitial cells of Cajal (the cells that set the pace of intestinal contractions) prevent normal contraction...
Chronic intestinal pseudoobstruction
c0238062
8,374
gard
https://rarediseases.info.nih.gov/diseases/12744/chronic-intestinal-pseudoobstruction
2021-01-18T18:01:18
{"orphanet": ["2978"], "synonyms": ["CIPO"]}
A number sign (#) is used with this entry because the slow and fast acetylation phenotypes are due to polymorphisms in the gene encoding N-acetyltransferase-2 (NAT2; 612182). Clinical Features The antituberculosis agent isoniazid (INH) is rendered therapeutically inactive by acetylation. Most or perhaps all populat...
ACETYLATION, SLOW
c2673470
8,375
omim
https://www.omim.org/entry/243400
2019-09-22T16:26:16
{"omim": ["243400"], "synonyms": ["Alternative titles", "SLOW ACETYLATOR PHENOTYPE", "ISONIAZID INACTIVATION, SLOW", "INH INACTIVATION, SLOW"]}
Poikiloderma People with varying manifestations of poikiloderma SpecialtyDermatology Poikiloderma is a skin condition that consists of areas of hypopigmentation, hyperpigmentation, telangiectasias and atrophy. Poikiloderma of Civatte is most frequently seen on the chest or the neck, characterized by red colo...
Poikiloderma
c0392777
8,376
wikipedia
https://en.wikipedia.org/wiki/Poikiloderma
2021-01-18T18:59:17
{"wikidata": ["Q1307866"]}
Central neurocytoma Axial T1-weighted gadolinium-enhanced MRI image showing an enhancing mass with cystic changes consistent with central neurocytoma in the right lateral ventricle. SpecialtyOncology, neurosurgery Central neurocytoma (CNC) is an extremely rare, ordinarily benign intraventricular brain tu...
Central neurocytoma
c0206719
8,377
wikipedia
https://en.wikipedia.org/wiki/Central_neurocytoma
2021-01-18T18:28:56
{"gard": ["10641"], "mesh": ["D018306"], "umls": ["C0206719"], "orphanet": ["73256"], "wikidata": ["Q5062123"]}
Sebaceoma Sebaceous epithelioma SpecialtyDermatology Sebaceoma (also known as a "sebaceous epithelioma") is a cutaneous condition that appears as a yellow or orange papule.[1]:662 ## See also[edit] * Sebaceous carcinoma * Sebaceous adenoma * Skin lesion ## References[edit] 1. ^ James, William...
Sebaceoma
c2939441
8,378
wikipedia
https://en.wikipedia.org/wiki/Sebaceoma
2021-01-18T18:34:35
{"umls": ["C2939441", "C1275210"], "wikidata": ["Q7442318"]}
For a discussion of the genetic heterogeneity in age at menarche, see MENAQ1 (610873). Mapping Perry et al. (2009) conducted a metaanalysis of 17,510 females from 8 different population-based cohorts and found significant association with rs7759938 on chromosome 6q21, within a recombination interval that includ...
MENARCHE, AGE AT, QUANTITATIVE TRAIT LOCUS 2
c2752070
8,379
omim
https://www.omim.org/entry/612882
2019-09-22T16:00:25
{"omim": ["612882"]}
A number sign (#) is used with this entry because of evidence that autosomal recessive primary microcephaly-23 (MCPH23) is caused by homozygous mutation in the NCAPH gene (602332) on chromosome 2q11. One such patient has been reported. For a general phenotypic description and a discussion of genetic heterogeneity of...
MICROCEPHALY 23, PRIMARY, AUTOSOMAL RECESSIVE
c4693843
8,380
omim
https://www.omim.org/entry/617985
2019-09-22T15:44:08
{"omim": ["617985"]}
Choroid plexus carcinoma is a rare and highly aggressive malignant type of choroid plexus tumor (see this term) occurring almost exclusively in children, presenting with cerebrospinal fluid obstruction in the lateral ventricles (most common), the fourth and third ventricles or in multiple ventricles, leading to hydro...
Choroid plexus carcinoma
c0431109
8,381
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=251899
2021-01-23T17:56:28
{"gard": ["8238"], "mesh": ["C562943"], "omim": ["260500"], "umls": ["C0431109"], "icd-10": ["C71.7"]}
Microcystic adnexal carcinoma A microscopic view of microcystic adnexal carcinoma SpecialtyDermatology/oncology Microcystic adnexal carcinoma (MAC) is a rare sweat gland cancer,[1] which often appears as a yellow spot or bump in the skin. It usually occurs in the neck or head, although cases have been docume...
Microcystic adnexal carcinoma
c0346027
8,382
wikipedia
https://en.wikipedia.org/wiki/Microcystic_adnexal_carcinoma
2021-01-18T18:29:18
{"gard": ["10438"], "umls": ["C0346027"], "wikidata": ["Q6839434"]}
A number sign (#) is used with this entry because autosomal dominant bone marrow failure syndrome-1 (BMFS1) is caused by heterozygous mutation in the SRP72 gene (602122) on chromosome 4q12. ### Genetic Heterogeneity of Bone Marrow Failure Syndrome See also BMFS2 (615715), caused by mutation in the ERCC6L2 gene ...
BONE MARROW FAILURE SYNDROME 1
c3808553
8,383
omim
https://www.omim.org/entry/614675
2019-09-22T15:54:33
{"mesh": ["C536572"], "omim": ["614675"], "orphanet": ["314399"], "synonyms": ["Autosomal dominant aplastic anemia and myelodysplasia"]}
Isolated bilateral hemispheric cerebellar hypoplasia is a rare cerebellar malformation characterized by hypoplasia of both cerebellar hemispheres with no other cerebellar/cerebral anomaly or other associated clinical feature. Affected patients present with mild hypotonia with motor delay, mild cognitive impairment, l...
Isolated bilateral hemispheric cerebellar hypoplasia
None
8,384
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=269221
2021-01-23T17:27:38
{"icd-10": ["Q04.3"]}
A number sign (#) is used with this entry because of evidence that autosomal dominant hypercarotenemia and vitamin A deficiency (HCVAD) is caused by heterozygous mutation in the BCMO1 gene (BCO1; 605748) on chromosome 16q23. One such patient has been reported. See also 277350 for possible autosomal recessive inherit...
HYPERCAROTENEMIA AND VITAMIN A DEFICIENCY, AUTOSOMAL DOMINANT
c2676023
8,385
omim
https://www.omim.org/entry/115300
2019-09-22T16:43:41
{"mesh": ["C567296"], "omim": ["115300"], "orphanet": ["199285"], "synonyms": []}
Persistent aura without infarction SpecialtyNeurology, Neuro-ophthalmology Differential diagnosisVisual snow Persistent aura without infarction (PAWOI) is a little-known condition, first described under the designation prolonged migraine aura status,[1] that is not yet fully understood. PAWOI is said to be a...
Persistent aura without infarction
c2349465
8,386
wikipedia
https://en.wikipedia.org/wiki/Persistent_aura_without_infarction
2021-01-18T18:56:55
{"umls": ["C2349465"], "icd-9": ["346.5"], "icd-10": ["G43.5"], "wikidata": ["Q7170403"]}
A number sign (#) is used with this entry because of evidence that susceptibility to dilated cardiomyopathy is associated with variation in the desmoglein-2 gene (DSG2; 125671). For a phenotypic description and discussion of genetic heterogeneity in dilated cardiomyopathy, see CMD1A (115200). Molecular Genetics...
CARDIOMYOPATHY, DILATED, 1BB
c0340427
8,387
omim
https://www.omim.org/entry/612877
2019-09-22T16:00:26
{"doid": ["0110458"], "mesh": ["C536231"], "omim": ["612877"], "orphanet": ["154"], "genereviews": ["NBK1309"]}
This article may require cleanup to meet Wikipedia's quality standards. The specific problem is: Writing style needs fixing Please help improve this article if you can. (October 2012) (Learn how and when to remove this template message) Brain delivery trauma Position of the child is important for normal birthi...
Birth trauma (physical)
c0005604
8,388
wikipedia
https://en.wikipedia.org/wiki/Birth_trauma_(physical)
2021-01-18T18:31:37
{"mesh": ["D001720"], "icd-9": ["767"], "icd-10": ["P10-P15"], "wikidata": ["Q1235888"]}
For a phenotypic description and a discussion of genetic heterogeneity of Alzheimer disease (AD), see 104300. Mapping In an extended multiplex family, ascertained in a population-based study of early-onset AD in the northern Netherlands, Rademakers et al. (2005) obtained conclusive evidence of linkage of AD wit...
ALZHEIMER DISEASE 10
c0276496
8,389
omim
https://www.omim.org/entry/609636
2019-09-22T16:05:45
{"doid": ["0110043"], "mesh": ["D000544"], "omim": ["609636"], "orphanet": ["1020"], "synonyms": ["Alternative titles", "ALZHEIMER DISEASE, FAMILIAL, 10", "AD10"]}
A rare diving disorder caused by inhaling a mist of seawater This article needs editing for compliance with Wikipedia's Manual of Style. In particular, it has problems with not using MEDMOS. Please help improve it if you can. (August 2017) (Learn how and when to remove this template message) Salt water aspirati...
Salt water aspiration syndrome
None
8,390
wikipedia
https://en.wikipedia.org/wiki/Salt_water_aspiration_syndrome
2021-01-18T18:36:47
{"wikidata": ["Q7406013"]}
## Description Intracranial berry aneurysms are saccular outpouchings of the intracranial arteries, most commonly at arterial bifurcations, characterized by arterial wall remodeling. Most cases of ruptured intracranial berry aneurysms result in a subarachnoid hemorrhage, associated with high morbidity and morta...
ANEURYSM, INTRACRANIAL BERRY, 2
c1837894
8,391
omim
https://www.omim.org/entry/608542
2019-09-22T16:07:40
{"doid": ["0060228"], "mesh": ["C536360"], "omim": ["608542", "105800"], "orphanet": ["231160"], "synonyms": ["Familial berry aneurysm", "Familial intracranial saccular aneurysm"]}
## Description Limb-girdle muscular dystrophy type 1H (LGMD1H) is an autosomal dominant disorder characterized by adult onset of progressive proximal muscle weakness affecting both the upper and lower limbs (Bisceglia et al., 2010). For a phenotypic description and a discussion of genetic heterogeneity of autosoma...
MUSCULAR DYSTROPHY, LIMB-GIRDLE, TYPE 1H
c3150786
8,392
omim
https://www.omim.org/entry/613530
2019-09-22T15:58:21
{"doid": ["0110303"], "omim": ["613530"], "orphanet": ["238755"], "synonyms": ["LGMD1H"]}
Ameloblastoma Micrograph of an ameloblastoma showing the characteristic palisading and stellate reticulum. H&E stain. SpecialtyOncology, oral and maxillofacial surgery Ameloblastoma is a rare, benign tumor of odontogenic epithelium (ameloblasts, or outside portion, of the teeth during development) much more ...
Ameloblastoma
c0002448
8,393
wikipedia
https://en.wikipedia.org/wiki/Ameloblastoma
2021-01-18T18:32:49
{"gard": ["5747"], "mesh": ["D000564"], "umls": ["C0002448"], "icd-9": ["213.1"], "icd-10": ["D16.5"], "orphanet": ["314419"], "wikidata": ["Q461857"]}
Subacromial bursitis Shoulder joint SpecialtyRheumatology Subacromial bursitis is a condition caused by inflammation of the bursa that separates the superior surface of the supraspinatus tendon (one of the four tendons of the rotator cuff) from the overlying coraco-acromial ligament, acromion, and coraco...
Subacromial bursitis
c0546953
8,394
wikipedia
https://en.wikipedia.org/wiki/Subacromial_bursitis
2021-01-18T18:39:44
{"icd-9": ["726.19"], "icd-10": ["M75.5"], "wikidata": ["Q7630699"]}
The newly described 2q23.1 microdeletion syndrome includes severe intellectual deficit with pronounced speech delay, behavioral abnormalities including hyperactivity and inappropriate laughter, short stature and seizures. ## Epidemiology To date, fifteen patients have been reported. ## Clinical description Dy...
2q23.1 microdeletion syndrome
c1969562
8,395
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=228402
2021-01-23T19:09:42
{"gard": ["10998"], "mesh": ["C566947"], "omim": ["156200"], "icd-10": ["Q93.5"], "synonyms": ["Del(2)(q23.1)", "Monosomy 2q23.1", "Pseudo-Angelman syndrome"]}
A number sign (#) is used with this entry because of evidence that X-linked deafness-7 (DFNX7) is caused by hemizygous mutation in the GPRASP2 gene (300969) on chromosome Xq26. One such family has been reported. Description DFNX7 is a congenital form of bilateral mixed or conductive hearing loss, which may be progr...
DEAFNESS, X-LINKED 7
None
8,396
omim
https://www.omim.org/entry/301018
2019-09-22T16:19:00
{"omim": ["301018"], "orphanet": ["500188"], "synonyms": []}
This syndrome is characterised by severe hypotonia, lactic academia and congenital hyperammonaemia. ## Epidemiology It has been described in three newborns born to consanguineous parents. ## Clinical description Ultrasound examination during the 36th week of pregnancy revealed generalised oedema. Hypertrophic car...
Hypotonia with lactic acidemia and hyperammonemia
c2673642
8,397
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=137908
2021-01-23T17:16:41
{"mesh": ["C567126"], "omim": ["611719"], "umls": ["C2673642"], "icd-10": ["E88.8"], "synonyms": ["COXPD5", "Combined oxidative phosphorylation defect type 5"]}
Complete androgen insensitivity syndrome (CAIS) is a form of androgen insensitivity syndrome (AIS; see this term), a disorder of sex development (DSD), characterized by the presence of female external genitalia in a 46,XY individual with normal testis development but undescended testes and unresponsiveness to age-app...
Complete androgen insensitivity syndrome
c0039585
8,398
orphanet
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=99429
2021-01-23T19:00:45
{"gard": ["10597"], "mesh": ["D013734"], "omim": ["300068", "300274"], "icd-10": ["E34.5"], "synonyms": ["CAIS", "Complete androgen resistance syndrome"]}
Fregoli delusion SpecialtyNeuropsychiatry The Fregoli delusion is a rare disorder in which a person holds a delusional belief that different people are in fact a single person who changes appearance or is in disguise. The syndrome may be related to a brain lesion[1][2] and is often of a paranoid nature, with t...
Fregoli delusion
None
8,399
wikipedia
https://en.wikipedia.org/wiki/Fregoli_delusion
2021-01-18T18:59:37
{"icd-9": ["297.8"], "icd-10": ["F22"], "wikidata": ["Q1453767"]}