icd10Code
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Disease
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228
E79.2
Myoadenylate deaminase deficiency
E79.8
Other disorders of purine and pyrimidine metabolism
E79.9
Disorder of purine and pyrimidine metabolism unspecified
E80.0
Hereditary erythropoietic porphyria
E80.1
Porphyria cutanea tarda
E80.2
Other and unspecified porphyria
E80.20
Unspecified porphyria
E80.21
Acute intermittent (hepatic) porphyria
E80.29
Other porphyria
E80.3
Defects of catalase and peroxidase
E80.4
Gilbert syndrome
E80.5
Crigler-Najjar syndrome
E80.6
Other disorders of bilirubin metabolism
E80.7
Disorder of bilirubin metabolism unspecified
E83.0
Disorders of copper metabolism
E83.00
Disorder of copper metabolism unspecified
E83.01
Wilson's disease
E83.09
Other disorders of copper metabolism
E83.1
Disorders of iron metabolism
E83.10
Disorder of iron metabolism unspecified
E83.11
Hemochromatosis
E83.110
Hereditary hemochromatosis
E83.111
Hemochromatosis due to repeated red blood cell transfusions
E83.118
Other hemochromatosis
E83.119
Hemochromatosis unspecified
E83.19
Other disorders of iron metabolism
E83.2
Disorders of zinc metabolism
E83.3
Disorders of phosphorus metabolism and phosphatases
E83.30
Disorder of phosphorus metabolism unspecified
E83.31
Familial hypophosphatemia
E83.32
Hereditary vitamin D-dependent rickets (type 1) (type 2)
E83.39
Other disorders of phosphorus metabolism
E83.4
Disorders of magnesium metabolism
E83.40
Disorders of magnesium metabolism unspecified
E83.41
Hypermagnesemia
E83.42
Hypomagnesemia
E83.49
Other disorders of magnesium metabolism
E83.5
Disorders of calcium metabolism
E83.50
Unspecified disorder of calcium metabolism
E83.51
Hypocalcemia
E83.52
Hypercalcemia
E83.59
Other disorders of calcium metabolism
E83.8
Other disorders of mineral metabolism
E83.81
Hungry bone syndrome
E83.89
Other disorders of mineral metabolism
E83.9
Disorder of mineral metabolism unspecified
E84.0
Cystic fibrosis with pulmonary manifestations
E84.1
Cystic fibrosis with intestinal manifestations
E84.11
Meconium ileus in cystic fibrosis
E84.19
Cystic fibrosis with other intestinal manifestations
E84.8
Cystic fibrosis with other manifestations
E84.9
Cystic fibrosis unspecified
E85.0
Non-neuropathic heredofamilial amyloidosis
E85.1
Neuropathic heredofamilial amyloidosis
E85.2
Heredofamilial amyloidosis unspecified
E85.3
Secondary systemic amyloidosis
E85.4
Organ-limited amyloidosis
E85.8
Other amyloidosis
E85.81
Light chain (AL) amyloidosis
E85.82
Wild-type transthyretin-related (ATTR) amyloidosis
E85.89
Other amyloidosis
E85.9
Amyloidosis unspecified
E86.0
Dehydration
E86.1
Hypovolemia
E86.9
Volume depletion unspecified
E87.0
Hyperosmolality and hypernatremia
E87.1
Hypo-osmolality and hyponatremia
E87.2
Acidosis
E87.3
Alkalosis
E87.4
Mixed disorder of acid-base balance
E87.5
Hyperkalemia
E87.6
Hypokalemia
E87.7
Fluid overload
E87.70
Fluid overload unspecified
E87.71
Transfusion associated circulatory overload
E87.79
Other fluid overload
E87.8
Other disorders of electrolyte and fluid balance not elsewhere classified
E88.0
Disorders of plasma-protein metabolism not elsewhere classified
E88.01
Alpha-1-antitrypsin deficiency
E88.09
Other disorders of plasma-protein metabolism not elsewhere classified
E88.1
Lipodystrophy not elsewhere classified
E88.2
Lipomatosis not elsewhere classified
E88.3
Tumor lysis syndrome
E88.4
Mitochondrial metabolism disorders
E88.40
Mitochondrial metabolism disorder unspecified
E88.41
MELAS syndrome
E88.42
MERRF syndrome
E88.49
Other mitochondrial metabolism disorders
E88.8
Other specified metabolic disorders
E88.81
Metabolic syndrome
E88.89
Other specified metabolic disorders
E88.9
Metabolic disorder unspecified
E89.0
Postprocedural hypothyroidism
E89.1
Postprocedural hypoinsulinemia
E89.2
Postprocedural hypoparathyroidism
E89.3
Postprocedural hypopituitarism
E89.4
Postprocedural ovarian failure
E89.40
Asymptomatic postprocedural ovarian failure
E89.41
Symptomatic postprocedural ovarian failure
E89.5
Postprocedural testicular hypofunction