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C0000768
has_associated_morphology
C0032897
Congenital Abnormality
Prader-Willi Syndrome
Malformations of organs or body parts during development in utero.
An autosomal dominant disorder caused by deletion of the proximal long arm of the paternal chromosome 15 (15q11-q13) or by inheritance of both of the pair of chromosomes 15 from the mother (UNIPARENTAL DISOMY) which are imprinted (GENETIC IMPRINTING) and hence silenced. Clinical manifestations include MENTAL RETARDATIO...
C0000768
has_associated_morphology
C0033770
Congenital Abnormality
Prune Belly Syndrome
Malformations of organs or body parts during development in utero.
A syndrome characterized by abdominal wall musculature deficiency, cryptorchism, and urinary tract abnormalities. The syndrome derives its name from its characteristic distended abdomen with wrinkled skin.
C0000768
has_associated_morphology
C0033804
Congenital Abnormality
Pseudohermaphroditism
Malformations of organs or body parts during development in utero.
An historical term for a variety of abnormalities in sex development that lead to anomalies in the reproductive tract and/or external genitalia.
C0000768
has_associated_morphology
C0035238
Congenital Abnormality
Congenital abnormality of respiratory system
Malformations of organs or body parts during development in utero.
Congenital structural abnormalities of the respiratory system.
C0000768
has_associated_morphology
C0035934
Congenital Abnormality
Rubinstein-Taybi Syndrome
Malformations of organs or body parts during development in utero.
A chromosomal disorder characterized by MENTAL RETARDATION, broad thumbs, webbing of fingers and toes, beaked nose, short upper lip, pouting lower lip, agenesis of corpus callosum, large foramen magnum, keloid formation, pulmonary stenosis, vertebral anomalies, chest wall anomalies, sleep apnea, and megacolon. The dise...
C0000768
has_associated_morphology
C0036391
Congenital Abnormality
Schwartz-Jampel Syndrome
Malformations of organs or body parts during development in utero.
A syndrome of short stature; generalized myotonia with contractures of major joints, microstomia, and muscle rigidity; ocular anomalies, mainly blepharophimosis; and characteristic facies marked by pinched or frozen smile puckered lips. Some degree of mental retardation occurs in about 25% of patients. The affected chi...
C0000768
has_associated_morphology
C0037205
Congenital Abnormality
Sirenomelia
Malformations of organs or body parts during development in utero.
A rare, lethal, congenital anomaly that may represent the most severe form of caudal dysgenesia and characterized by fusion of the lower limbs (mermaid-like) always associated with severe genitourinary and gastrointestinal anomalies. Furthermore, there is wide phenotipical variability in the musculoskeletal, central ne...
C0000768
has_associated_morphology
C0037231
Congenital Abnormality
Sjogren-Larsson Syndrome
Malformations of organs or body parts during development in utero.
An autosomal recessive neurocutaneous disorder characterized by severe ichthyosis MENTAL RETARDATION; SPASTIC PARAPLEGIA; and congenital ICHTHYOSIS. It is caused by mutation of gene encoding microsomal fatty ALDEHYDE DEHYDROGENASE leading to defect in fatty alcohol metabolism.
C0000768
has_associated_morphology
C0038505
Congenital Abnormality
Sturge-Weber Syndrome
Malformations of organs or body parts during development in utero.
A non-inherited congenital condition with vascular and neurological abnormalities. It is characterized by facial vascular nevi (PORT-WINE STAIN), and capillary angiomatosis of intracranial membranes (MENINGES; CHOROID). Neurological features include EPILEPSY; cognitive deficits; GLAUCOMA; and visual defects.
C0000768
has_associated_morphology
C0039685
Congenital Abnormality
Tetralogy of Fallot
Malformations of organs or body parts during development in utero.
A combination of congenital heart defects consisting of four key features including VENTRICULAR SEPTAL DEFECTS; PULMONARY STENOSIS; RIGHT VENTRICULAR HYPERTROPHY; and a dextro-positioned AORTA. In this condition, blood from both ventricles (oxygen-rich and oxygen-poor) is pumped into the body often causing CYANOSIS.
C0000768
has_associated_morphology
C0039743
Congenital Abnormality
Thanatophoric Dysplasia
Malformations of organs or body parts during development in utero.
A severe form of neonatal dwarfism with very short limbs. All cases have died at birth or later in the neonatal period.
C0000768
has_associated_morphology
C0040427
Congenital Abnormality
Tooth Abnormalities
Malformations of organs or body parts during development in utero.
Congenital absence of or defects in structures of the teeth.
C0000768
has_associated_morphology
C0040433
Congenital Abnormality
Tooth Crowding
Malformations of organs or body parts during development in utero.
Changes in alignment of teeth in the dental arch [PMID:19125428, PMID:31468724]
C0000768
has_associated_morphology
C0040456
Congenital Abnormality
Impacted tooth
Malformations of organs or body parts during development in utero.
A tooth that is prevented from erupting by a physical barrier, usually other teeth. Impaction may also result from orientation of the tooth in an other than vertical position in the periodontal structures.
C0000768
has_associated_morphology
C0040457
Congenital Abnormality
Tooth, Supernumerary
Malformations of organs or body parts during development in utero.
An extra tooth, erupted or unerupted, resembling or unlike the other teeth in the group to which it belongs. Its presence may cause malposition of adjacent teeth or prevent their eruption.
C0000768
has_associated_morphology
C0043119
Congenital Abnormality
Werner Syndrome
Malformations of organs or body parts during development in utero.
An autosomal recessive disorder that causes premature aging in adults, characterized by sclerodermal skin changes, cataracts, subcutaneous calcification, muscular atrophy, a tendency to diabetes mellitus, aged appearance of the face, baldness, and a high incidence of neoplastic disease.
C0000768
has_associated_morphology
C0043152
Congenital Abnormality
White Heifer Disease
Malformations of organs or body parts during development in utero.
A congenital reproductive abnormality in white female offspring (heifers) in certain breeds of CATTLE, such as Belgian Blue and Shorthorn. The white color is inherited as a recessive trait which is associated with defects in the female reproductive tract (Muellerian system). These heifers are usually sterile.
C0000768
has_associated_morphology
C0043459
Congenital Abnormality
Zellweger Syndrome
Malformations of organs or body parts during development in utero.
An autosomal recessive disorder due to defects in PEROXISOME biogenesis which involves more than 13 genes encoding peroxin proteins of the peroxisomal membrane and matrix. Zellweger syndrome is typically seen in the neonatal period with features such as dysmorphic skull; MUSCLE HYPOTONIA; SENSORINEURAL HEARING LOSS; vi...
C0000768
has_associated_morphology
C0079541
Congenital Abnormality
Holoprosencephaly
Malformations of organs or body parts during development in utero.
Anterior midline brain, cranial, and facial malformations resulting from the failure of the embryonic prosencephalon to undergo segmentation and cleavage. Alobar prosencephaly is the most severe form and features anophthalmia; cyclopia; severe INTELLECTUAL DISABILITY; CLEFT LIP; CLEFT PALATE; SEIZURES; and microcephaly...
C0000768
has_associated_morphology
C0079661
Congenital Abnormality
Klein's Syndrome
Malformations of organs or body parts during development in utero.
A very rare subtype of Waardenburg syndrome (WS) with characteristics of limb anomalies in association with congenital hearing loss, minor defects in structures arising from neural crest, resulting in pigmentation anomalies of eyes, hair, and skin. Caused by heterozygous or homozygous mutations in the PAX3 (2q36.1) gen...
C0000768
has_associated_morphology
C0085280
Congenital Abnormality
Alagille Syndrome
Malformations of organs or body parts during development in utero.
A multisystem disorder that is characterized by aplasia of intrahepatic bile ducts (BILE DUCTS, INTRAHEPATIC), and malformations in the cardiovascular system, the eyes, the vertebral column, and the facies. Major clinical features include JAUNDICE, and congenital heart disease with peripheral PULMONARY STENOSIS. Alagil...
C0000768
has_associated_morphology
C0149955
Congenital Abnormality
Annular pancreas
Malformations of organs or body parts during development in utero.
A distinct form of duodenal atresia in which the head of the pancreas forms a ring around the second portion of the duodenum.
C0000768
has_associated_morphology
C0151489
Congenital Abnormality
Arterial malformation
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0152234
Congenital Abnormality
Iniencephaly
Malformations of organs or body parts during development in utero.
Iniencephaly is a rare form of neural tube defect in which a malformation of the cervico-occipital junction is associated with a malformation of the central nervous system.
C0000768
has_associated_morphology
C0152240
Congenital Abnormality
Uterus bilocularis
Malformations of organs or body parts during development in utero.
A congenital duplication of the UTERUS in which a septum is formed separating the uterus. The partitioning septum can also separate the CERVIX and VAGINA.
C0000768
has_associated_morphology
C0152415
Congenital Abnormality
Ankyloglossia
Malformations of organs or body parts during development in utero.
A severe congenital restriction of TONGUE movement, resulting from fusion or adherence of the tongue to the floor of the mouth. In partial ankyloglossia (tongue-tie) the LINGUAL FRENUM is abnormally short, or is attached too close to the tip of the tongue. OMIM: 106280
C0000768
has_associated_morphology
C0152429
Congenital Abnormality
Accessory salivary gland
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0152436
Congenital Abnormality
Hymen, Imperforate
Malformations of organs or body parts during development in utero.
A congenital disorder where the hymen (a membrane that surrounds or partially covers the external vaginal opening) does not have an opening and completely obstructs the vagina. [PMID:24822139]
C0000768
has_associated_morphology
C0155940
Congenital Abnormality
Displaced tooth
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0155963
Congenital Abnormality
Persistent tuberculum impar
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0158553
Congenital Abnormality
Congenital anomaly of lens shape
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0158635
Congenital Abnormality
Congenital absence and hypoplasia of umbilical artery
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0158638
Congenital Abnormality
Congenital anomaly of cerebrovascular system
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0158646
Congenital Abnormality
Cleft palate with cleft lip
Malformations of organs or body parts during development in utero.
<p>Cleft lip and cleft palate are <a href="https://medlineplus.gov/birthdefects.html">birth defects</a> that occur when a baby's lip or mouth do not form properly. They happen early during pregnancy. A baby can have a cleft lip, a cleft palate, or both.</p> <p>A cleft lip happens if the tissue that makes up the lip doe...
C0000768
has_associated_morphology
C0158647
Congenital Abnormality
Cleft palate, unilateral, complete
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0158648
Congenital Abnormality
Cleft palate, unilateral, incomplete
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0158649
Congenital Abnormality
Complete bilateral cleft palate
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0158650
Congenital Abnormality
Incomplete bilateral cleft palate
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0158651
Congenital Abnormality
Complete unilateral cleft lip
Malformations of organs or body parts during development in utero.
Unilateral cleft lip cleft that starts from the bottom of the upper lip and reaches the nasal cavity. [PMID:21331089, PMID:26171570]
C0000768
has_associated_morphology
C0158652
Congenital Abnormality
Incomplete unilateral cleft lip
Malformations of organs or body parts during development in utero.
Unilateral cleft lip cleft that starts from the bottom of the upper lip but does not reach the nasal cavity. [PMID:21331089, PMID:26171570]
C0000768
has_associated_morphology
C0158653
Congenital Abnormality
Complete bilateral cleft lip
Malformations of organs or body parts during development in utero.
Bilateral cleft lip in which the cleft lip on both sides is complete, i.e. start from the bottom of the upper lip and reach the nasal cavity. [PMID:19884685]
C0000768
has_associated_morphology
C0158654
Congenital Abnormality
Incomplete bilateral cleft lip
Malformations of organs or body parts during development in utero.
Bilateral cleft lip in which the cleft lip on both sides are incomplete (i.e. start from the bottom of the upper lip but do not reach the nasal cavity), or the cleft lip on one is incomplete and a microform on the other side. [PMID:19884685]
C0000768
has_associated_morphology
C0158655
Congenital Abnormality
Cleft palate with cleft lip, unilateral, complete
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0158656
Congenital Abnormality
Cleft palate with cleft lip, unilateral, incomplete
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0158657
Congenital Abnormality
Bilateral complete cleft palate with cleft lip
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0158658
Congenital Abnormality
Cleft palate with cleft lip, bilateral, incomplete
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0158662
Congenital Abnormality
Congenital anomaly of tongue
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0158663
Congenital Abnormality
Tongue absent
Malformations of organs or body parts during development in utero.
Absence of the tongue owing to a developmental abnormality. [https://orcid.org/0000-0002-0736-9199]
C0000768
has_associated_morphology
C0158664
Congenital Abnormality
Congenital adhesions of tongue
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0158667
Congenital Abnormality
Aplasia of Lacrimal and Salivary Glands
Malformations of organs or body parts during development in utero.
A rare autosomal dominant disorder with features of aplasia, atresia or hypoplasia of the lacrimal and salivary glands leading to varying manifestations from infancy such as recurrent eye infections, irritable eyes, epiphora, xerostomia, dental caries, dental erosion and oral inflammation.
C0000768
has_associated_morphology
C0158669
Congenital Abnormality
Congenital salivary gland fistula
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0158670
Congenital Abnormality
Congenital fistula of lip
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0158684
Congenital Abnormality
Anomalies of pancreas
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0158687
Congenital Abnormality
Congenital malformation of genital organs
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0158689
Congenital Abnormality
Fallopian tube and broad ligament anomalies
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0158695
Congenital Abnormality
Embryonic cyst of cervix, vagina, and external female genitalia
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0158698
Congenital Abnormality
Congenital malformation of the urinary system
Malformations of organs or body parts during development in utero.
An abnormality of the kidney, ureter, bladder, or urethra that is present at birth. Representative examples include renal hypoplasia, renal agenesis, accessory kidney, absence of ureter, atresia of bladder neck, and atresia of urethra.
C0000768
has_associated_morphology
C0158795
Congenital Abnormality
Other and unspecified congenital anomalies
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0162635
Congenital Abnormality
Angelman Syndrome
Malformations of organs or body parts during development in utero.
A syndrome characterized by multiple abnormalities, MENTAL RETARDATION, and movement disorders. Present usually are skull and other abnormalities, frequent infantile spasms (SPASMS, INFANTILE); easily provoked and prolonged paroxysms of laughter (hence happy); jerky puppetlike movements (hence puppet); continuous tongu...
C0000768
has_associated_morphology
C0175691
Congenital Abnormality
Dubowitz syndrome
Malformations of organs or body parts during development in utero.
Dubowitz syndrome (DS) is a rare multiple congenital syndrome characterized primarly by growth retardation, microcephaly, distinctive facial dysmorphism, cutaneous eczema, a mild to severe intellectual deficit and genital abnormalities.
C0000768
has_associated_morphology
C0175692
Congenital Abnormality
Johanson-Blizzard syndrome
Malformations of organs or body parts during development in utero.
An extremely rare autosomal recessive condition caused by mutation(s) in the UBR1 gene, encoding E3 ubiquitin-protein ligase UBR1. It is characterized by failure to thrive, often due to pancreatic insufficiency, craniofacial abnormalities, and intellectual disability.
C0000768
has_associated_morphology
C0175693
Congenital Abnormality
Russell-Silver syndrome
Malformations of organs or body parts during development in utero.
Genetically and clinically heterogeneous disorder characterized by low birth weight, postnatal growth retardation, facial dysmorphism, bilateral body asymmetry, and clinodactyly of the fifth fingers. Alterations in GENETIC IMPRINTING are involved. Hypomethylation of IGF2/H19 locus near an imprinting center region of ch...
C0000768
has_associated_morphology
C0175694
Congenital Abnormality
Smith-Lemli-Opitz Syndrome
Malformations of organs or body parts during development in utero.
An autosomal recessive disorder of CHOLESTEROL metabolism. It is caused by a deficiency of 7-dehydrocholesterol reductase, the enzyme that converts 7-dehydrocholesterol to cholesterol, leading to an abnormally low plasma cholesterol. This syndrome is characterized by multiple CONGENITAL ABNORMALITIES, growth deficiency...
C0000768
has_associated_morphology
C0175695
Congenital Abnormality
Sotos' syndrome
Malformations of organs or body parts during development in utero.
Congenital or postnatal overgrowth syndrome most often in height and occipitofrontal circumference with variable delayed motor and cognitive development. Other associated features include advanced bone age, seizures, NEONATAL JAUNDICE; HYPOTONIA; and SCOLIOSIS. It is also associated with increased risk of developing ne...
C0000768
has_associated_morphology
C0175697
Congenital Abnormality
Van der Woude syndrome
Malformations of organs or body parts during development in utero.
Van der Woude syndrome (VWS) is a rare congenital genetic dysmorphic syndrome characterized by paramedian lower-lip fistulae, cleft lip with or without cleft palate, or isolated cleft palate.
C0000768
has_associated_morphology
C0175701
Congenital Abnormality
Aarskog syndrome
Malformations of organs or body parts during development in utero.
A rare developmental disorder characterized by facial, limbs and genital features, and a disproportionate acromelic short stature.
C0000768
has_associated_morphology
C0175702
Congenital Abnormality
Williams Syndrome
Malformations of organs or body parts during development in utero.
A disorder caused by hemizygous microdeletion of about 28 genes on chromosome 7q11.23, including the ELASTIN gene. Clinical manifestations include SUPRAVALVULAR AORTIC STENOSIS; MENTAL RETARDATION; elfin facies; impaired visuospatial constructive abilities; and transient HYPERCALCEMIA in infancy. The condition affects ...
C0000768
has_associated_morphology
C0175703
Congenital Abnormality
Thrombocytopenia-Absent Radius Syndrome
Malformations of organs or body parts during development in utero.
A rare congenital malformation syndrome characterized by bilateral absence/hypoplasia of the radii with presence of both thumbs, and thrombocytopenia. Additional manifestations can include cow's milk allergy, anomalies of the lower limbs, heart and genitourinary system.
C0000768
has_associated_morphology
C0175778
Congenital Abnormality
Larsen syndrome
Malformations of organs or body parts during development in utero.
An orofacial clefting syndrome characterized by congenital dislocation of large joints, foot deformities, cervical spine dysplasia, scoliosis, spatula-shaped distal phalanges and distinctive craniofacial abnormalities, including cleft palate.
C0000768
has_direct_morphology
C0192091
Congenital Abnormality
Grafting of palate for cleft palate repair
Malformations of organs or body parts during development in utero.
null
C0000768
has_direct_morphology
C0193034
Congenital Abnormality
Decompression of imperforate anus
Malformations of organs or body parts during development in utero.
null
C0000768
has_direct_morphology
C0193077
Congenital Abnormality
Duhamel operation, abdominoperineal pull-through
Malformations of organs or body parts during development in utero.
null
C0000768
has_direct_morphology
C0193198
Congenital Abnormality
Repair of congenital anovaginal fistula
Malformations of organs or body parts during development in utero.
null
C0000768
has_direct_morphology
C0193199
Congenital Abnormality
Repair of congenital anovaginal fistula with cut-back type procedure
Malformations of organs or body parts during development in utero.
null
C0000768
has_direct_morphology
C0193205
Congenital Abnormality
Construction of anus for congenital absence with repair of urinary fistula
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0206554
Congenital Abnormality
Odontodysplasia
Malformations of organs or body parts during development in utero.
A localized arrested tooth development which appears to involve most commonly the anterior teeth, usually on one side of the midline, most often the maxillary central and lateral incisors. Roentgenographically, the teeth have a ghostlike appearance. Calcification and bits of prismatic enamel may be found in the pulp an...
C0000768
has_associated_morphology
C0220658
Congenital Abnormality
Pfeiffer Syndrome
Malformations of organs or body parts during development in utero.
An acrocephalosyndactyly associated with craniosynostosis, midfacial hypoplasia, hand and foot malformation with a wide range of clinical expression and severity. Most of the affected patients show various other associated manifestations.
C0000768
has_associated_morphology
C0220663
Congenital Abnormality
Blepharophimosis, Ptosis, and Epicanthus Inversus
Malformations of organs or body parts during development in utero.
A rare ophthalmic disorder characterised by blepharophimosis, ptosis, epicanthus inversus, and telecanthus, that can appear associated with (type 1) or without primary ovarian insufficiency (POI; type 2).
C0000768
has_associated_morphology
C0220704
Congenital Abnormality
Shprintzen syndrome
Malformations of organs or body parts during development in utero.
caused by microdeletion on chromosome 22q11.2; associated with multiple congenital anomalies, learning disabilities, behavioral phenotypes including ADHD and anxiety, with schizophrenic risk in adulthood.
C0000768
has_associated_morphology
C0220708
Congenital Abnormality
VATER Association
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0220726
Congenital Abnormality
Diastrophic dysplasia
Malformations of organs or body parts during development in utero.
A rare disorder marked by short stature with short extremities (final adult height is 120cm +/- 10cm), and joint malformations leading to multiple joint contractures (principally involving the shoulders, elbows, interphalangeal joints and hips).
C0000768
has_associated_morphology
C0220769
Congenital Abnormality
FG syndrome
Malformations of organs or body parts during development in utero.
A multiple congenital anomaly/mental retardation syndrome characterized by a short stature, large head, hypotonia with or without joint contractures, seizures, imperforate anus, agenesis of the corpus callosum, and characteristic facies. "FG" stands for the surnames of patients in whom the syndrome was first reported.
C0000768
has_associated_morphology
C0221060
Congenital Abnormality
Mobius Syndrome
Malformations of organs or body parts during development in utero.
A syndrome of congenital facial paralysis, frequently associated with abducens palsy and other congenital abnormalities including lingual palsy, clubfeet, brachial disorders, cognitive deficits, and pectoral muscle defects. Pathologic findings are variable and include brain stem nuclear aplasia, facial nerve aplasia, a...
C0000768
has_associated_morphology
C0221219
Congenital Abnormality
Ectopic pancreas
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0221366
Congenital Abnormality
Embryonic cyst of Gartner's duct
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0227918
Congenital Abnormality
Epoophoron (disorder)
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0227919
Congenital Abnormality
Paroophoron
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0232511
Congenital Abnormality
Disto-occlusion of teeth
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0232512
Congenital Abnormality
Mesio-occlusion of teeth
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0235752
Congenital Abnormality
Port-Wine Stain
Malformations of organs or body parts during development in utero.
A vascular malformation of developmental origin characterized pathologically by ectasia of superficial dermal capillaries, and clinically by persistent macular erythema. In the past, port wine stains have frequently been termed capillary hemangiomas, which they are not; unfortunately this confusing practice persists: H...
C0000768
has_associated_morphology
C0236026
Congenital Abnormality
Fetal valproate syndrome
Malformations of organs or body parts during development in utero.
A rare teratogenic disease due to embryo/fetal exposure to valproic acid (VPA) and subsequently characterized by a distinct facial dysmorphism, congenital anomalies and developmental delay (especially in language and communication).
C0000768
has_associated_morphology
C0238394
Congenital Abnormality
Female Pseudohermaphroditism
Malformations of organs or body parts during development in utero.
Hermaphroditism refers to a discrepancy between the morphology of the gonads and that of the external genitalia. In female pseudohermaphroditism, the genotype is female (XX) and the gonads are ovaries, but the external genitalia are virilized. [https://orcid.org/0000-0002-0736-9199]
C0000768
has_associated_morphology
C0238395
Congenital Abnormality
Male Pseudohermaphroditism
Malformations of organs or body parts during development in utero.
Hermaphroditism refers to a discrepancy between the morphology of the gonads and that of the external genitalia. In male pseudohermaphroditism, the genotype is male (XY) and the external genitalia are imcompletely virilized, ambiguous, or complete female. If gonads are present, they are testes. [https://orcid.org/0000-...
C0000768
has_associated_morphology
C0238402
Congenital Abnormality
Pycnodysostosis
Malformations of organs or body parts during development in utero.
Rare autosomal recessive syndrome characterized by delayed closing of CRANIAL SUTURES, short stature, ACRO-OSTEOLYSIS of distal phalanges, dental and MAXILLOFACIAL ABNORMALITIES and an increase in bone density that results in frequent BONE FRACTURES. It is associated with BONE RESORPTION defect due to mutations in the ...
C0000768
has_associated_morphology
C0239119
Congenital Abnormality
Lenticonus
Malformations of organs or body parts during development in utero.
A conical projection of the anterior or posterior surface of the lens, occurring as a developmental anomaly. [HPO_CONTRIBUTOR:DDD_ncarter]
C0000768
has_associated_morphology
C0240340
Congenital Abnormality
Microdontia (disorder)
Malformations of organs or body parts during development in utero.
Decreased size of the teeth, which can be defined as a mesiodistal tooth diameter (width) more than 2 SD below mean. Alternatively, an apparently decreased maximum width of tooth. [https://orcid.org/0000-0002-9338-3017, PMID:19125428]
C0000768
has_associated_morphology
C0240635
Congenital Abnormality
Byzanthine arch palate
Malformations of organs or body parts during development in utero.
Height of the palate more than 2 SD above the mean (objective) or palatal height at the level of the first permanent molar more than twice the height of the teeth (subjective). [PMID:19125428]
C0000768
has_associated_morphology
C0241799
Congenital Abnormality
Ruptured cerebral arteriovenous malformation
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0241925
Congenital Abnormality
Hutchinson's triad
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0242385
Congenital Abnormality
Crossbite
Malformations of organs or body parts during development in utero.
Lingual occlusion of buccal cusps and/or incisal edge of maxillary teeth to the buccal cusps and/or incisal edge of mandibular teeth. [PMID:31468724]