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C0000768
has_associated_morphology
C0265767
Congenital Abnormality
Congenital stenosis of trachea
Malformations of organs or body parts during development in utero.
A rare malformation characterized by fixed narrowing of the tracheal lumen primarily due to complete tracheal cartilage rings and an absent membranous trachea, which causes breathing difficulty.
C0000768
has_associated_morphology
C0265768
Congenital Abnormality
Congenital dilatation of trachea
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265769
Congenital Abnormality
Congenital diverticulum of trachea
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265770
Congenital Abnormality
Rudimentary tracheal bronchus
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265772
Congenital Abnormality
Accessory trachea
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265773
Congenital Abnormality
Congenital anomaly of tracheal cartilage
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265774
Congenital Abnormality
Congenital anomaly of bronchus
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265776
Congenital Abnormality
Congenital atresia of bronchus
Malformations of organs or body parts during development in utero.
A developmental anomaly characterized by focal obliteration of the proximal segment of a bronchus. The bronchial pattern is entirely normal distal to the site of stenosis. [https://orcid.org/0000-0002-0003-6754]
C0000768
has_associated_morphology
C0265777
Congenital Abnormality
Congenital diverticulum of bronchus
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265778
Congenital Abnormality
Accessory bronchus
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265797
Congenital Abnormality
Congenital emphysema
Malformations of organs or body parts during development in utero.
A respiratory abnormality characterized by respiratory distress due to hyperinflation of one or more affected lobes of the lung.
C0000768
has_associated_morphology
C0265798
Congenital Abnormality
Bronchial atresia with segmental pulmonary emphysema
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265801
Congenital Abnormality
Congenital anomaly of pleural folds
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265802
Congenital Abnormality
Congenital cyst of mediastinum
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265807
Congenital Abnormality
Acyanotic congenital heart disease
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265808
Congenital Abnormality
Cyanotic congenital heart disease
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265809
Congenital Abnormality
Double outlet left ventricle
Malformations of organs or body parts during development in utero.
Double-outlet left ventricle (DOLV) is an extremely rare congenital cardiac malformation in which both the aorta and the pulmonary artery arise, either exclusively or predominantly, from the morphologic left ventricle.
C0000768
has_associated_morphology
C0265812
Congenital Abnormality
Left ventricular-right atrial communication
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265815
Congenital Abnormality
Premature closure of foramen ovale
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265817
Congenital Abnormality
Common arterial trunk and separate origin of pulmonary arteries
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265819
Congenital Abnormality
Truncus arteriosus, Edwards' type IV
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265820
Congenital Abnormality
Congenital anomaly of heart valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265825
Congenital Abnormality
Monocuspid cardiac valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265827
Congenital Abnormality
Quadricuspid cardiac valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265828
Congenital Abnormality
Myxomatosis of cardiac valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265829
Congenital Abnormality
Congenital valvular insufficiency
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265830
Congenital Abnormality
Congenital pulmonary valve abnormality
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265832
Congenital Abnormality
Congenital supravalvular pulmonary stenosis
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265833
Congenital Abnormality
Congenital insufficiency of pulmonary valve
Malformations of organs or body parts during development in utero.
Dysfunction of the pulmonary valve characterized by incomplete valve closure that is present at birth.
C0000768
has_associated_morphology
C0265836
Congenital Abnormality
Congenital stenosis of tricuspid valve
Malformations of organs or body parts during development in utero.
Tricuspid valve stenosis that is present at birth.
C0000768
has_associated_morphology
C0265837
Congenital Abnormality
Congenital hypoplasia of tricuspid valve
Malformations of organs or body parts during development in utero.
Congenital defect characterized by underdevelopment of the tricuspid valve. [HPO_CONTRIBUTOR:DDD_dbrown]
C0000768
has_associated_morphology
C0265839
Congenital Abnormality
Ebstein's anomaly with atrial septal defect
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265840
Congenital Abnormality
Congenital insufficiency of tricuspid valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265841
Congenital Abnormality
Congenital anomaly of aortic valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265843
Congenital Abnormality
Congenital atresia of aortic valve
Malformations of organs or body parts during development in utero.
A congenital disorder of the aortic valve in which the orifice of the valve fails to develop. [https://orcid.org/0000-0002-0736-9199]
C0000768
has_associated_morphology
C0265844
Congenital Abnormality
Double aortic valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265845
Congenital Abnormality
Congenital anomaly of mitral valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265848
Congenital Abnormality
Supernumerary cusps of the mitral valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265849
Congenital Abnormality
Double mitral valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265850
Congenital Abnormality
Fused commissures of mitral valve
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265851
Congenital Abnormality
Congenital supravalvular mitral stenosis
Malformations of organs or body parts during development in utero.
Congenital supravalvular mitral ring is a rare, congenital, mitral valve malformation characterized by an abnormal ridge of the connective tissue on the atrial side of the mitral valve, which can present clinically with signs and symptoms of left ventricle inflow obstruction (dyspnea, tachypnea, pulmonary hypertension,...
C0000768
has_associated_morphology
C0265856
Congenital Abnormality
Hypoplasia of right heart
Malformations of organs or body parts during development in utero.
Underdevelopment of the right-sided structures of the heart. [https://orcid.org/0000-0002-0736-9199]
C0000768
has_associated_morphology
C0265857
Congenital Abnormality
Uhl anomaly
Malformations of organs or body parts during development in utero.
Uhl anomaly is characterized by an almost complete absence of the myocardium in the right ventricle resulting in a thin walled nonfunctional right ventricle manifesting with cardiac arrhythmias and right ventricular failure. Cases of partial absence of right ventricular myocardium which remains asymptomatic or mildly s...
C0000768
has_associated_morphology
C0265866
Congenital Abnormality
Congenital atresia of cardiac vein
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265867
Congenital Abnormality
Hypoplasia of cardiac vein
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265868
Congenital Abnormality
Chiari network
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265870
Congenital Abnormality
Congenital absence of coronary sinus
Malformations of organs or body parts during development in utero.
A developmental defect in which the coronary sinus fails to form. [https://orcid.org/0000-0001-5208-3432, PMID:24551710]
C0000768
has_associated_morphology
C0265871
Congenital Abnormality
Anomalous muscle bands of right ventricle
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265872
Congenital Abnormality
Anomalous muscle bands of left ventricle
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265873
Congenital Abnormality
Congenital cardiomegaly
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265875
Congenital Abnormality
Congenital rhabdomyoma of heart
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265876
Congenital Abnormality
Primary endocardial fibroelastosis
Malformations of organs or body parts during development in utero.
Endocardial fibroelastosis unassociated with other cardiac abnormalities.
C0000768
has_associated_morphology
C0265878
Congenital Abnormality
Preductal coarctation of aorta
Malformations of organs or body parts during development in utero.
Narrowing or constriction of the aorta localized proximal to the ductus arteriosus, i.e., to the preductal region of aortic arch. [HPO_CONTRIBUTOR:DDD_dbrown]
C0000768
has_associated_morphology
C0265879
Congenital Abnormality
Postductal coarctation of aorta
Malformations of organs or body parts during development in utero.
Narrowing or constriction of the aorta localized distal to the ductus arteriosus, i.e., to the postductal region of aortic arch. [HPO_CONTRIBUTOR:DDD_dbrown]
C0000768
has_associated_morphology
C0265881
Congenital Abnormality
Congenital hypoplasia of aortic arch
Malformations of organs or body parts during development in utero.
An underdeveloped aortic arch that is present at birth. This symptom is usually found in association with other cardiac defects that characterize left heart syndrome.
C0000768
has_associated_morphology
C0265882
Congenital Abnormality
Congenital hypoplasia of ascending aorta
Malformations of organs or body parts during development in utero.
Significant luminal narrowing of a long segment of or the entire ascending aorta. [PMID:13938144]
C0000768
has_associated_morphology
C0265883
Congenital Abnormality
Double Aortic Arch
Malformations of organs or body parts during development in utero.
A conenital abnormality of the aortic arch in which the two embryonic aortc arches form a vascular ring that surrounds the trachea or esophagus and then join to form the descending aorta. Double aortic arch can cause symptoms because of compression of the esophagus (dysphagia, cyanosis while eating) or trachea (stridor...
C0000768
has_associated_morphology
C0265885
Congenital Abnormality
Kommerell's diverticulum
Malformations of organs or body parts during development in utero.
Kommerell diverticulum (KD) is a developmental anomaly of the aortic arch characterized by a diverticulum at the proximal descending aorta of left or right arch configuration that gives rise to an aberrant subclavian artery. KD is primarily asymptomatic but may become symptomatic secondary to dilatation of KD, atheroma...
C0000768
has_associated_morphology
C0265886
Congenital Abnormality
Overriding aorta
Malformations of organs or body parts during development in utero.
A congenital anatomic anomaly in which the aorta is positioned directly above a ventricular septal defect, thus receiving blood from both the right and left ventricles, resulting in an overall decrease In oxygenated haemoglobin and tissue cyanosis.
C0000768
has_associated_morphology
C0265887
Congenital Abnormality
Persistent aortic arch convolutions
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265889
Congenital Abnormality
Congenital atresia of aorta
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265890
Congenital Abnormality
Congenital stenosis of aorta
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265891
Congenital Abnormality
Aplasia of aorta
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265892
Congenital Abnormality
Hypoplasia of aorta
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265894
Congenital Abnormality
Congenital aneurysm of aorta
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265895
Congenital Abnormality
Congenital dilatation of aorta
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265897
Congenital Abnormality
Anomalous communication of coronary artery
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265898
Congenital Abnormality
Coronary artery fistula
Malformations of organs or body parts during development in utero.
Coronary arterial fistulas are a connection between one or more of the coronary arteries and a cardiac chamber or great vessel.
C0000768
has_associated_morphology
C0265899
Congenital Abnormality
Congenital absence of coronary artery
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265900
Congenital Abnormality
Anomalous origin of left circumflex artery from right coronary artery
Malformations of organs or body parts during development in utero.
An abnormal origin of the left circumflex artery (LCX) from the right coronary artery. Normally, the left anterior descending (LAD) and the LCX arise from a common stem, the left main coronary artery (LMCA). [PMID:27358682]
C0000768
has_associated_morphology
C0265901
Congenital Abnormality
Coronary artery arising from aorta
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265902
Congenital Abnormality
Anomalous origin of coronary artery from pulmonary arterial tree
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265903
Congenital Abnormality
Single coronary artery
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265905
Congenital Abnormality
Agenesis of pulmonary artery
Malformations of organs or body parts during development in utero.
A rare vascular anomaly characterized by congenital absence of the right or left pulmonary artery, usually ending within 2 cm of its expected origin from the pulmonary trunk. Patients often also have other cardiovascular abnormalities and respective symptoms and are then typically diagnosed in infancy or childhood, whi...
C0000768
has_associated_morphology
C0265906
Congenital Abnormality
Congenital absence of right pulmonary artery
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265907
Congenital Abnormality
Congenital absence of left pulmonary artery
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265908
Congenital Abnormality
Congenital atresia of pulmonary artery
Malformations of organs or body parts during development in utero.
A congenital anomaly with a narrowing or complete absence of the opening between the right ventricle and the pulmonary artery. [https://orcid.org/0000-0002-0736-9199]
C0000768
has_associated_morphology
C0265909
Congenital Abnormality
Coarctation of pulmonary artery
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265910
Congenital Abnormality
Congenital hypoplasia of pulmonary artery
Malformations of organs or body parts during development in utero.
A rare, congenital anomaly of the great arteries characterized by various clinical signs and symptoms, including shortness of breath, recurrent lower respiratory tract infections, lung hypoplasia, pulmonary hypertension, and haemoptysis. The anomaly can be isolated or associated with congenital heart disease, such as t...
C0000768
has_associated_morphology
C0265912
Congenital Abnormality
Anomalous origin of pulmonary artery
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265913
Congenital Abnormality
Pulmonary arteriovenous aneurysm
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265914
Congenital Abnormality
Anomalous pulmonary vein
Malformations of organs or body parts during development in utero.
An abnormality of the pulmonary veins. [https://orcid.org/0000-0002-0736-9199]
C0000768
has_associated_morphology
C0265915
Congenital Abnormality
Congenital stenosis of pulmonary veins
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265916
Congenital Abnormality
Anomalous pulmonary venous drainage
Malformations of organs or body parts during development in utero.
A rare developmental defect during embryogenesis where some or all of the pulmonary veins drain into the right atrium or the systemic veins, with or without the presence of pulmonary venous obstruction, leading to various manifestations such as fatigue, exertional dyspnea, pulmonary arterial hypertension, cyanosis and ...
C0000768
has_associated_morphology
C0265917
Congenital Abnormality
Supradiaphragmatic total anomalous pulmonary venous return
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265918
Congenital Abnormality
Anomalous pulmonary venous drainage to right atrium
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265919
Congenital Abnormality
Anomalous pulmonary venous drainage to coronary sinus
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265920
Congenital Abnormality
Anomalous pulmonary venous drainage to superior vena cava
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265921
Congenital Abnormality
Subdiaphragmatic total anomalous pulmonary venous return
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265922
Congenital Abnormality
Anomalous pulmonary venous drainage to hepatic veins
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265923
Congenital Abnormality
Anomalous pulmonary venous drainage to abdominal portion of inferior vena cava
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265924
Congenital Abnormality
Transposition of pulmonary veins
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265925
Congenital Abnormality
Congenital anomaly of vena cava
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265926
Congenital Abnormality
Congenital absence of vena cava
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265927
Congenital Abnormality
Congenital stenosis of vena cava
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265928
Congenital Abnormality
Congenital anomaly of superior vena cava
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265929
Congenital Abnormality
Absence of superior vena cava
Malformations of organs or body parts during development in utero.
A rare congenital anomaly of the great veins characterized by unilateral or bilateral complete absence of the superior vena cava (SVC). Unilateral agenesis is mainly asymptomatic (most of the time diagnosed incidentally) and patients usually have otherwise normal heart structure. Bilateral agenesis, however, is frequen...
C0000768
has_associated_morphology
C0265930
Congenital Abnormality
Congenital stenosis of superior vena cava
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265931
Congenital Abnormality
Persistent Left Superior Vena Cava
Malformations of organs or body parts during development in utero.
Finding of the SUPERIOR VENA CAVA on the left instead of the usual right side of the ASCENDING AORTA. In bilateral superior vena cava it is found on both sides.
C0000768
has_associated_morphology
C0265932
Congenital Abnormality
Congenital anomaly of inferior vena cava
Malformations of organs or body parts during development in utero.
null