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C0000768
has_associated_morphology
C0265933
Congenital Abnormality
Absence of inferior vena cava
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265934
Congenital Abnormality
Congenital stenosis of inferior vena cava
Malformations of organs or body parts during development in utero.
A rare vascular anomaly characterized by congenital narrowing of the inferior vena cava mostly at the diaphragmatic level or hepatic segment, with or without web formation. Patients may present with deep vein thrombosis below the obstructed segment as well as swelling, pain, and varices of the lower extremities, abdomi...
C0000768
has_associated_morphology
C0265935
Congenital Abnormality
Congenital anomaly of artery
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265937
Congenital Abnormality
Congenital atresia of artery
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265938
Congenital Abnormality
Congenital stricture of artery
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265940
Congenital Abnormality
Double artery
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265942
Congenital Abnormality
Peripheral congenital arteriovenous aneurysm
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265943
Congenital Abnormality
Congenital anomaly of cerebral artery
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265945
Congenital Abnormality
Congenital aneurysm of anterior communicating artery
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265947
Congenital Abnormality
Anomalous origin of right subclavian artery
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265948
Congenital Abnormality
Origin of innominate artery from left side of aortic arch
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265949
Congenital Abnormality
Multiple renal arteries
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265950
Congenital Abnormality
Venous malformation
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265952
Congenital Abnormality
Congenital atresia of vein
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265953
Congenital Abnormality
Congenital phlebectasia
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265955
Congenital Abnormality
Persistent left posterior cardinal vein
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265961
Congenital Abnormality
Erythrokeratodermia variabilis
Malformations of organs or body parts during development in utero.
An autosomal dominant skin disease characterized by transient and variable noninflammatory ERYTHEMA and hyperkeratosis. It has been associated with mutations in the genes that code for CONNEXINS. Erythrokeratodermia variabilis inherited in an autosomal recessive fashion has also been reported. Affected individuals ofte...
C0000768
has_associated_morphology
C0265962
Congenital Abnormality
Ichthyosis linearis circumflexa
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265963
Congenital Abnormality
Congenital keratoderma
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265964
Congenital Abnormality
Mutilating keratoderma
Malformations of organs or body parts during development in utero.
Keratoderma hereditarium mutilans is a rare, diffuse, mutilating, hereditary palmoplantar keratoderma disorder characterized by severe, honeycomb-pattern palmoplantar keratosis and pseudoainhum of the digits leading to autoamputation, associated with mild to moderate congenital sensorineural hearing loss. Additional fe...
C0000768
has_associated_morphology
C0265965
Congenital Abnormality
Dyskeratosis Congenita
Malformations of organs or body parts during development in utero.
A predominantly X-linked recessive syndrome characterized by a triad of reticular skin pigmentation, nail dystrophy and leukoplakia of mucous membranes. Oral and dental abnormalities may also be present. Complications are a predisposition to malignancy and bone marrow involvement with pancytopenia. (from Int J Paediatr...
C0000768
has_associated_morphology
C0265966
Congenital Abnormality
Hereditary benign intraepithelial dyskeratosis
Malformations of organs or body parts during development in utero.
A rare, genetic, superficial corneal dystrophy disease characterized by white, elevated, epithelial plaques located on the bulbar conjunctiva (sometimes with encroachment of the cornea) and oral mucosa (in any part of the oral cavity), associated with dilated, hyperemic, conjunctival blood vessels, observed mainly in H...
C0000768
has_associated_morphology
C0265967
Congenital Abnormality
Porokeratosis of Mibelli, plaque type
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265968
Congenital Abnormality
Porokeratosis of Mibelli, superficial disseminated type
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265969
Congenital Abnormality
Porokeratosis of Mibelli, linear unilateral type
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265970
Congenital Abnormality
Porokeratosis, Disseminated Superficial Actinic
Malformations of organs or body parts during development in utero.
A rare skin disease that is the most common form of porokeratosis characterized by the presence of several small annular plaques with a distinctive keratotic rim found most commonly on sun-exposed areas of the skin, particularly the extremities.
C0000768
has_associated_morphology
C0265971
Congenital Abnormality
Acrokeratosis Verruciformis of Hopf
Malformations of organs or body parts during development in utero.
An alleleic variant of Darier's disease.
C0000768
has_associated_morphology
C0265972
Congenital Abnormality
Congenital skin fragility of animals
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265972
Congenital Abnormality
Congenital skin fragility of animals
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265974
Congenital Abnormality
Birthmark
Malformations of organs or body parts during development in utero.
<p>Birthmarks are abnormalities of the skin that are present when a baby is born. There are two types of birthmarks. Vascular birthmarks are made up of blood vessels that haven't formed correctly. They are usually red. Two types of vascular birthmarks are hemangiomas and port-wine stains. <a href="https://medlineplus.g...
C0000768
has_associated_morphology
C0265977
Congenital Abnormality
Congenital cutaneous angiomatosis
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265979
Congenital Abnormality
Fibrous Hamartoma of Infancy
Malformations of organs or body parts during development in utero.
A poorly circumscribed neoplasm arising from the soft tissues in infants. It is characterized by the presence of bland fibroblastic spindle cells, collagenous stroma formation, primitive mesenchymal round cells, and mature fat cells. These components combined form a distinct organoid pattern.
C0000768
has_associated_morphology
C0265982
Congenital Abnormality
Nevus anemicus
Malformations of organs or body parts during development in utero.
A congenital skin lesion characterized by irregular hypopigmented macules that coalesce to form plaques and occur particularly on the chest. It is generally present at birth or develops in the first days of life. It is more common in females. Diagnosis is confirmed by applying gentle friction to the lesion and the surr...
C0000768
has_associated_morphology
C0265985
Congenital Abnormality
Mongolian Spot
Malformations of organs or body parts during development in utero.
A bluish-gray to gray-brown benign, melanocytic nevus found usually in the LUMBOSACRAL REGION of dark-skinned people, especially those of East Asian ancestry. It is usually congenital or appears shortly after birth, and disappears in childhood.
C0000768
has_associated_morphology
C0265987
Congenital Abnormality
Nevus comedonicus
Malformations of organs or body parts during development in utero.
A rare developmental skin condition consisting of abnormal pilosebaceous follicle development. It is characterized by linear or band-like distributions of groups of comedones, usually on the face, neck, upper arm, chest, and abdomen, that appear at birth or in childhood.
C0000768
has_associated_morphology
C0265988
Congenital Abnormality
Congenital accessory skin tag
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265989
Congenital Abnormality
Congenital scar
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265991
Congenital Abnormality
Congenital anomaly of hair
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265994
Congenital Abnormality
Persistent lanugo
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265996
Congenital Abnormality
Bayonet hair
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265997
Congenital Abnormality
Congenital anomaly of nail
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0265999
Congenital Abnormality
Congenital clubnail
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266001
Congenital Abnormality
Congenital leukonychia
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266003
Congenital Abnormality
Subungual fibroma
Malformations of organs or body parts during development in utero.
The presence of fibromata beneath finger or toenails. [https://orcid.org/0000-0002-0736-9199]
C0000768
has_associated_morphology
C0266004
Congenital Abnormality
Knuckle pads, leuconychia and sensorineural deafness
Malformations of organs or body parts during development in utero.
A rare, syndromic genetic deafness disease characterized by symmetric or asymmetric knuckle pads (typically located on the distal and interphalangeal joints), leukonychia, diffuse palmoplantar keratoderma, and congenital, mild to moderate sensorineural deafness.
C0000768
has_associated_morphology
C0266006
Congenital Abnormality
Pili torti-deafness syndrome
Malformations of organs or body parts during development in utero.
Björnstad syndrome is characterized by congenital sensorineural hearing loss and pili torti.
C0000768
has_associated_morphology
C0266007
Congenital Abnormality
Congenital anomaly of subcutaneous tissue
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266008
Congenital Abnormality
Congenital anomaly of breast
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266012
Congenital Abnormality
Ectopic breast tissue
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266013
Congenital Abnormality
Congenital hypoplasia of breast
Malformations of organs or body parts during development in utero.
Underdevelopment of the breast. [https://orcid.org/0000-0002-0736-9199]
C0000768
has_associated_morphology
C0266014
Congenital Abnormality
Congenital inversion of nipple
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266015
Congenital Abnormality
Congenital digestive system anomalies
Malformations of organs or body parts during development in utero.
Congenital structural abnormalities of the DIGESTIVE SYSTEM.
C0000768
has_associated_morphology
C0266017
Congenital Abnormality
Congenital absence of alimentary tract
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266018
Congenital Abnormality
Congenital partial absence of alimentary tract
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266020
Congenital Abnormality
Congenital malposition of digestive organs
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266021
Congenital Abnormality
Other specified congenital malformations of upper alimentary tract
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266073
Congenital Abnormality
Congenital asymmetry of jaw
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266076
Congenital Abnormality
Maxillary prognathism
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266077
Congenital Abnormality
Mandibular retrognathism
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266079
Congenital Abnormality
Congenital macrognathism
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266080
Congenital Abnormality
Congenital mandibular hyperplasia
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266094
Congenital Abnormality
Congenital macrocheilia
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266101
Congenital Abnormality
Primordial cyst
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266103
Congenital Abnormality
Naso-palatine duct cyst
Malformations of organs or body parts during development in utero.
A non-odontogenic cyst of developmental origin that arises in the midline of the anterior maxilla. It is found exclusively in the midline of the anterior hard palate. (WHO 2017)
C0000768
has_associated_morphology
C0266106
Congenital Abnormality
Median mandibular cyst
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266113
Congenital Abnormality
Epitheliogenesis imperfecta lingua bovis
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266115
Congenital Abnormality
Lethal glossopharyngeal defect
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266126
Congenital Abnormality
Congenital anomaly of esophagus
Malformations of organs or body parts during development in utero.
A structural abnormality of the esophagus. [https://orcid.org/0000-0002-0736-9199]
C0000768
has_associated_morphology
C0266132
Congenital Abnormality
Congenital displacement of esophagus
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266133
Congenital Abnormality
Congenital diverticulum of esophagus
Malformations of organs or body parts during development in utero.
A rare, non-syndromic, congenital esophageal malformation characterized by a false diverticulum, most often located in the upper, posterior esophagus (pharyngo-esophageal) but may occur anywhere along the esophagus (mid-thoracic or epiphrenic). Many patients are asymptomatic, but bad breath, chronic cough, respiratory ...
C0000768
has_associated_morphology
C0266135
Congenital Abnormality
Congenital duplication of esophagus
Malformations of organs or body parts during development in utero.
A developmental disorder in which there is a duplication of a portion of the muscle and submucosa of the esophagus without epithelial duplication. [https://orcid.org/0000-0002-0736-9199, PMID:10464795]
C0000768
has_associated_morphology
C0266137
Congenital Abnormality
Congenital esophagobronchial fistula
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266138
Congenital Abnormality
Congenital esophagotracheal fistula
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266139
Congenital Abnormality
H-type congenital tracheoesophageal fistula
Malformations of organs or body parts during development in utero.
Congenital tracheoesophageal fistula without esophageal atresia.
C0000768
has_associated_morphology
C0266140
Congenital Abnormality
Vascular compression of esophagus by aberrant artery
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266141
Congenital Abnormality
Vascular compression of esophagus by aberrant right subclavian artery arising from descending aorta
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266142
Congenital Abnormality
Congenital anomaly of stomach
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266143
Congenital Abnormality
Congenital cardiospasm
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266145
Congenital Abnormality
Congenital hourglass stomach
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266146
Congenital Abnormality
Congenital displacement of stomach
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266147
Congenital Abnormality
Congenital diverticulum of stomach
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266150
Congenital Abnormality
Congenital microgastria
Malformations of organs or body parts during development in utero.
Congenital microgastria is a rare malformation where the embryological development of the stomach is interrupted, leading to an abnormally small foregut in newborns and characterized by extreme feeding intolerance and malnutrition along with growth retardation and death if untreated. It is usually associated with multi...
C0000768
has_associated_morphology
C0266151
Congenital Abnormality
Congenital gastric perforation
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266155
Congenital Abnormality
Brunner's gland adenoma
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266156
Congenital Abnormality
Congenital volvulus of stomach
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266157
Congenital Abnormality
Congenital organoaxial volvulus of stomach
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266159
Congenital Abnormality
Pyloric Atresia
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266160
Congenital Abnormality
Pyloric antral atresia
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266162
Congenital Abnormality
Congenital pyloric membrane
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266166
Congenital Abnormality
Congenital duplication of intestine
Malformations of organs or body parts during development in utero.
A developmental disorder in which there is a duplication the entire intestine or of a portion of the intestine. [https://orcid.org/0000-0002-0736-9199]
C0000768
has_associated_morphology
C0266167
Congenital Abnormality
Long tubular intestinal duplication
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266168
Congenital Abnormality
Ectopic intestinal mucosa
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266169
Congenital Abnormality
Congenital anomaly of small intestine
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266170
Congenital Abnormality
Congenital absence of small intestine
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266172
Congenital Abnormality
Congenital atresia of small intestine
Malformations of organs or body parts during development in utero.
A rare, congenital defect of the small intestine characterized by disruption in the normal small intestine continuity, resulting in intestinal obstruction. The malformation may be classified in four different types of small bowel atresia (SBA) based on the anatomical obstruction.
C0000768
has_associated_morphology
C0266173
Congenital Abnormality
Congenital stenosis of small intestine
Malformations of organs or body parts during development in utero.
null
C0000768
has_associated_morphology
C0266174
Congenital Abnormality
Duodenal atresia
Malformations of organs or body parts during development in utero.
A rare, non-syndromic intestinal malformation characterized by a complete but short segment obliteration of the duodenal lumen.
C0000768
has_associated_morphology
C0266175
Congenital Abnormality
Jejunal Atresia
Malformations of organs or body parts during development in utero.
A developmental defect resulting in abnormal closure, or atresia of the tubular structure of the jejunum. [https://orcid.org/0000-0002-0736-9199]
C0000768
has_associated_morphology
C0266177
Congenital Abnormality
Megaduodenum
Malformations of organs or body parts during development in utero.
Dilation and elongation of the duodenum with hypertrophy of all layers of the duodenum. []
C0000768
has_associated_morphology
C0266179
Congenital Abnormality
Omphalocele with gangrene
Malformations of organs or body parts during development in utero.
null