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C0000754
inverse_isa
C0000768
Congenital abnormal fusion
Congenital Abnormality
null
Malformations of organs or body parts during development in utero.
C0000754
inverse_isa
C0332466
Congenital abnormal fusion
Fused structure
null
null
C0000754
has_associated_morphology
C0001193
Congenital abnormal fusion
Apert syndrome
null
An autosomal dominant inherited type of acrocephalosyndactyly caused by mutations in the FGFR2 gene. It is characterized by early closure of the sutures between the skull bones, bulging eyes, low-set ears, fusion of the second, third, and forth fingers, and fusion of the toes.
C0000754
has_associated_morphology
C0016873
Congenital abnormal fusion
Fused Teeth
null
Two teeth united during development by the union of their tooth germs; the teeth may be joined by the enamel of their crowns, by their root dentin, or by both.
C0000754
has_associated_morphology
C0022738
Congenital abnormal fusion
Klippel-Feil Syndrome
null
A syndrome characterised by a low hairline and a shortened neck resulting from a reduced number of vertebrae or the fusion of multiple hemivertebrae into one osseous mass.
C0000754
has_associated_morphology
C0032357
Congenital abnormal fusion
Poland Syndrome
null
A syndrome which is characterized by symbrachydactyly and aplasia of the sternal head of pectoralis major.
C0000754
has_associated_morphology
C0037205
Congenital abnormal fusion
Sirenomelia
null
A rare, lethal, congenital anomaly that may represent the most severe form of caudal dysgenesia and characterized by fusion of the lower limbs (mermaid-like) always associated with severe genitourinary and gastrointestinal anomalies. Furthermore, there is wide phenotipical variability in the musculoskeletal, central ne...
C0000754
has_associated_morphology
C0039075
Congenital abnormal fusion
Syndactyly
null
A congenital anomaly of the hand or foot, marked by the webbing between adjacent fingers or toes. Syndactylies are classified as complete or incomplete by the degree of joining. Syndactylies can also be simple or complex. Simple syndactyly indicates joining of only skin or soft tissue; complex syndactyly marks joining ...
C0000754
has_associated_morphology
C0041428
Congenital abnormal fusion
Twins, Conjoined
null
MONOZYGOTIC TWINS who are joined in utero. They may be well developed and share only a superficial connection, often in the frontal, transverse or sagittal body plane, or they may share a partial duplication of a body structure. Alternatively, there may be a small and incompletely developed twin conjoined to a larger, ...
C0000754
has_associated_morphology
C0152436
Congenital abnormal fusion
Hymen, Imperforate
null
A congenital disorder where the hymen (a membrane that surrounds or partially covers the external vaginal opening) does not have an opening and completely obstructs the vagina. [PMID:24822139]
C0000754
has_associated_morphology
C0158736
Congenital abnormal fusion
Syndactyly of fingers with fusion of bones
null
Webbing or fusion of the fingers, involving soft parts and including fusion of individual finger bones. [https://orcid.org/0009-0006-4530-3154]
C0000754
has_associated_morphology
C0158738
Congenital abnormal fusion
Syndactyly of toes with fusion of bones
null
Webbing or fusion of the toes, involving soft parts and including fusion of individual bones of the toes. Bony fusions are referred to as bony" Syndactyly if the fusion occurs in a tibial-fibular axis. Fusions of bones of the toes in a proximo-distal axis are referred to as "Symphalangism"." [https://orcid.org/0009-000...
C0000754
has_associated_morphology
C0158761
Congenital abnormal fusion
Radioulnar Synostosis
null
An abnormal osseous union (fusion) between the radius and the ulna. [https://orcid.org/0000-0002-0736-9199]
C0000754
has_associated_morphology
C0175699
Congenital abnormal fusion
Saethre-Chotzen Syndrome
null
A syndrome characterized by unilateral or bilateral coronal synostosis, facial asymmetry, ptosis, strabismus and small ears with prominent superior and/or inferior crus, among other less common manifestations.
C0000754
has_direct_morphology
C0191427
Congenital abnormal fusion
Repair of syndactyly
null
null
C0000754
has_associated_morphology
C0220658
Congenital abnormal fusion
Pfeiffer Syndrome
null
An acrocephalosyndactyly associated with craniosynostosis, midfacial hypoplasia, hand and foot malformation with a wide range of clinical expression and severity. Most of the affected patients show various other associated manifestations.
C0000754
has_associated_morphology
C0221352
Congenital abnormal fusion
Syndactyly of fingers
null
Webbing or fusion of the fingers, involving soft parts only or including bone structure. Bony fusions are referred to as bony" Syndactyly if the fusion occurs in a radio-ulnar axis. Fusions of bones of the fingers in a proximo-distal axis are referred to as "Symphalangism"." [https://orcid.org/0000-0002-0736-9199]
C0000754
has_associated_morphology
C0221353
Congenital abnormal fusion
Horseshoe Kidney
null
Congenital fusion of two kidneys in the lower midline.
C0000754
has_associated_morphology
C0239054
Congenital abnormal fusion
Coloboma of choroid
null
null
C0000754
has_associated_morphology
C0240896
Congenital abnormal fusion
Fundus coloboma
null
Absence of a region of the retina, retinal pigment epithelium, and choroid. [https://orcid.org/0000-0002-0736-9199]
C0000754
has_associated_morphology
C0265239
Congenital abnormal fusion
Wildervanck's syndrome
null
Wildervanck syndrome is characterized by the triad of cervical vertebral fusion (Klippel-Feil anomaly, see this term), bilateral abducens palsy with retracted eyes (Duane syndrome, see this term) and congenital perceptive deafness.
C0000754
has_associated_morphology
C0265303
Congenital abnormal fusion
ACROCEPHALOPOLYSYNDACTYLY TYPE IV
null
Goodman syndrome is an extremely rare genetic disorder with characteristics of marked malformations of the head and face (essentially acrocephaly), abnormalities of the hands and feet (polydactyly, syndactyly, clinodactyly, camptodactyly, ulnar deviation), and congenital heart disease. There have been no further descri...
C0000754
has_associated_morphology
C0265536
Congenital abnormal fusion
Imperfect fusion of skull
null
null
C0000754
has_associated_morphology
C0265553
Congenital abnormal fusion
Polysyndactyly
null
A rare anatomical malformation characterized by polydactyly (extra fingers or toes) and syndactyly (webbed fingers or toes).
C0000754
has_associated_morphology
C0265651
Congenital abnormal fusion
Astragaloscaphoid synostosis
null
null
C0000754
has_associated_morphology
C0265652
Congenital abnormal fusion
Calcaneonavicular bar
null
null
C0000754
has_associated_morphology
C0265653
Congenital abnormal fusion
Coalition of calcaneus
null
null
C0000754
has_associated_morphology
C0265654
Congenital abnormal fusion
Tarsal Coalition
null
Congenital, complete or partial fusion of the TARSAL BONES of the foot. PES PLANUS is usually a feature.
C0000754
has_associated_morphology
C0265660
Congenital abnormal fusion
Syndactyly of the toes
null
Webbing or fusion of the toes, involving soft parts only or including bone structure. Bony fusions are referred to as bony" Syndactyly if the fusion occurs in a radio-ulnar axis. Fusions of bones of the toes in a proximo-distal axis are referred to as "Symphalangism"." [https://orcid.org/0000-0002-0736-9199]
C0000754
has_associated_morphology
C0265678
Congenital abnormal fusion
Congenital fusion of spine
null
null
C0000754
has_associated_morphology
C0265682
Congenital abnormal fusion
Sacralization of lumbar vertebra
null
null
C0000754
has_associated_morphology
C0265685
Congenital abnormal fusion
Congenital fusion of sacroiliac joint
null
null
C0000754
has_associated_morphology
C0265695
Congenital abnormal fusion
Congenital fusion of ribs
null
Complete or partial merging of adjacent ribs. [https://orcid.org/0000-0002-0736-9199]
C0000754
has_associated_morphology
C0265709
Congenital abnormal fusion
Assimilation pelvis
null
null
C0000754
has_associated_morphology
C0265710
Congenital abnormal fusion
High assimilation pelvis
null
null
C0000754
has_associated_morphology
C0265711
Congenital abnormal fusion
Low assimilation pelvis
null
null
C0000754
has_associated_morphology
C0265782
Congenital abnormal fusion
Unilobar lung
null
null
C0000754
has_associated_morphology
C0265826
Congenital abnormal fusion
Bicuspid cardiac valve
null
null
C0000754
has_associated_morphology
C0265850
Congenital abnormal fusion
Fused commissures of mitral valve
null
null
C0000754
has_associated_morphology
C0266033
Congenital abnormal fusion
Gemination of teeth
null
The development of two teeth from a single tooth bud, leading to a larger fused tooth. [PMID:18167487]
C0000754
has_associated_morphology
C0266096
Congenital abnormal fusion
Synchilia
null
null
C0000754
has_associated_morphology
C0266305
Congenital abnormal fusion
Fused Kidney
null
Congenital fusion of two kidneys.
C0000754
has_associated_morphology
C0266361
Congenital abnormal fusion
Hermaphroditism, True
null
An historical term for conditions of sexual ambiguity in which the individual possesses gonadal tissues of both sexes.
C0000754
has_associated_morphology
C0266419
Congenital abnormal fusion
Synechia vulvae
null
Synechia vulvae (adhesions of the labia minora) are characterized by a complete or partial fusion of the labia minora in the midline. [PMID:17364294, PMID:29262197]
C0000754
has_associated_morphology
C0266428
Congenital abnormal fusion
Congenital fusion of testis
null
null
C0000754
has_associated_morphology
C0266602
Congenital abnormal fusion
Congenital fusion of ossicles of ear
null
null
C0000754
has_associated_morphology
C0266636
Congenital abnormal fusion
Splenogonadal fusion
null
A rare, non-syndromic visceral malformation characterized by an abnormal, continuous or discontinuous attachment of the spleen to the gonad, epididymis or vas. Continuous type has a direct connection between spleen and the gonad, whereas discontinuous type indicates gonadal tissue fused with an accessory spleen or ecto...
C0000754
has_associated_morphology
C0266658
Congenital abnormal fusion
Autositic twin of asymmetrical conjoined twins
null
null
C0000754
has_associated_morphology
C0266659
Congenital abnormal fusion
Parasitic twin of asymmetrical conjoined twins
null
null
C0000754
has_associated_morphology
C0266674
Congenital abnormal fusion
Cranial duplication
null
null
C0000754
has_associated_morphology
C0266684
Congenital abnormal fusion
Fetus in fetu
null
Rare abnormality where a fetal part of an identical twin that stopped developing during gestation is found within a normally developing fetus. It is considered a TWIN PREGNANCY complication.
C0000754
has_associated_morphology
C0266685
Congenital abnormal fusion
double; monster
null
null
C0000754
has_associated_morphology
C0266686
Congenital abnormal fusion
Anadidymus
null
null
C0000754
has_associated_morphology
C0266687
Congenital abnormal fusion
Cephalodymus
null
null
C0000754
has_associated_morphology
C0266689
Congenital abnormal fusion
Cephalothoracopagus
null
null
C0000754
has_associated_morphology
C0266690
Congenital abnormal fusion
Thoracodelphus
null
null
C0000754
has_associated_morphology
C0266691
Congenital abnormal fusion
Pygodidymus
null
null
C0000754
has_associated_morphology
C0266692
Congenital abnormal fusion
Craniopagus
null
null
C0000754
has_associated_morphology
C0266693
Congenital abnormal fusion
Craniopagus occipitalis
null
null
C0000754
has_associated_morphology
C0266694
Congenital abnormal fusion
Craniopagus parietalis
null
null
C0000754
has_associated_morphology
C0266695
Congenital abnormal fusion
Monocephalus (disorder)
null
null
C0000754
has_associated_morphology
C0266696
Congenital abnormal fusion
Monocephalus tetrapus dibrachius
null
null
C0000754
has_associated_morphology
C0266697
Congenital abnormal fusion
Monocephalus tripus dibrachius
null
null
C0000754
has_associated_morphology
C0266698
Congenital abnormal fusion
Syncephalus
null
null
C0000754
has_associated_morphology
C0266699
Congenital abnormal fusion
Deradelphus
null
null
C0000754
has_associated_morphology
C0266700
Congenital abnormal fusion
Janiceps (disorder)
null
null
C0000754
has_associated_morphology
C0266701
Congenital abnormal fusion
Anakatadidymus
null
null
C0000754
has_associated_morphology
C0266702
Congenital abnormal fusion
Gastrothoracopagus
null
null
C0000754
has_associated_morphology
C0266703
Congenital abnormal fusion
Thoracodidymus
null
null
C0000754
has_associated_morphology
C0266704
Congenital abnormal fusion
Thoracopagus
null
null
C0000754
has_associated_morphology
C0266705
Congenital abnormal fusion
Thoracopagus parasiticus
null
null
C0000754
has_associated_morphology
C0266706
Congenital abnormal fusion
Thoracopagus epigastricus
null
null
C0000754
has_associated_morphology
C0266707
Congenital abnormal fusion
Thoracoparacephalus
null
null
C0000754
has_associated_morphology
C0266709
Congenital abnormal fusion
Omphaloangiopagus
null
null
C0000754
has_associated_morphology
C0266711
Congenital abnormal fusion
Pygopagus
null
null
C0000754
has_associated_morphology
C0266712
Congenital abnormal fusion
Katadidymus
null
null
C0000754
has_associated_morphology
C0266713
Congenital abnormal fusion
Heterodymus
null
null
C0000754
has_associated_morphology
C0266714
Congenital abnormal fusion
Dicephalus dipus tetrabrachius
null
null
C0000754
has_associated_morphology
C0266715
Congenital abnormal fusion
Dicephalus dipus tribrachius
null
null
C0000754
has_associated_morphology
C0266716
Congenital abnormal fusion
Dicephalus tripus tribrachius
null
null
C0000754
has_associated_morphology
C0266717
Congenital abnormal fusion
Acardius
null
A severe form of twin-twin transfusion syndrome that occurs in monochorionic pregnancies. The normal twin (pump twin) supplies the blood flow to its sibling that lacks heart or brain or both (acardiac/acephalic twin). Untreated, it may lead to the demise of the pump twin in some cases.
C0000754
has_associated_morphology
C0266720
Congenital abnormal fusion
Acardiacus anceps
null
null
C0000754
has_associated_morphology
C0266723
Congenital abnormal fusion
Compound monster, NOS
null
null
C0000754
has_associated_morphology
C0266724
Congenital abnormal fusion
Desmiognathus
null
null
C0000754
has_associated_morphology
C0266725
Congenital abnormal fusion
Epignathus
null
Epignathus is a very rare and life threatening intraoral teratoma, usually arising from the maxilla, mandible, palate or base of skull and invading the cranium, nasopharynx or oral cavity. Epignathus is more commonly seen in females, and presents with various manifestations (depending on the tumor size) including obstr...
C0000754
has_associated_morphology
C0266726
Congenital abnormal fusion
Thoracomelus
null
null
C0000754
has_associated_morphology
C0266727
Congenital abnormal fusion
Ischiomelus
null
null
C0000754
has_associated_morphology
C0266728
Congenital abnormal fusion
Pygomelus
null
null
C0000754
has_associated_morphology
C0266729
Congenital abnormal fusion
Gastrothoracopagus dipygus
null
null
C0000754
has_associated_morphology
C0266735
Congenital abnormal fusion
Derodidymis
null
null
C0000754
has_associated_morphology
C0266736
Congenital abnormal fusion
Dicephalus dipus dibrachius
null
null
C0000754
has_associated_morphology
C0266739
Congenital abnormal fusion
Pygoamorphus
null
null
C0000754
has_associated_morphology
C0266740
Congenital abnormal fusion
Symmetrical conjoined twins
null
null
C0000754
has_associated_morphology
C0266741
Congenital abnormal fusion
Xiphopagus
null
null
C0000754
has_associated_morphology
C0266742
Congenital abnormal fusion
Asymmetrical conjoined twins
null
null
C0000754
has_associated_morphology
C0269719
Congenital abnormal fusion
disproportion at birth due to conjoined twins
null
null
C0000754
has_associated_morphology
C0344757
Congenital abnormal fusion
Fused tricuspid papillary muscle
null
null
C0000754
has_associated_morphology
C0344781
Congenital abnormal fusion
Fused mitral papillary muscles
null
null
C0000754
has_associated_morphology
C0344822
Congenital abnormal fusion
Fused common atrioventricular valve papillary muscle
null
null
C0000754
has_associated_morphology
C0344850
Congenital abnormal fusion
Congenital fusion of right atrioventricular valve papillary muscles
null
null